{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,3,11]],"date-time":"2026-03-11T20:08:05Z","timestamp":1773259685087,"version":"3.50.1"},"reference-count":28,"publisher":"Wiley","issue":"5","license":[{"start":{"date-parts":[[2014,5,6]],"date-time":"2014-05-06T00:00:00Z","timestamp":1399334400000},"content-version":"vor","delay-in-days":5,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["The Journal of Dermatology"],"published-print":{"date-parts":[[2014,5]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:p>Keratosis pilaris and ulerythema ophryogenes (keratosis pilaris atrophicans faciei) are part of a group of hereditary disorders of hair follicle keratinization involving follicular inflammation and subsequent atrophy. Monosomy 18p refers to a chromosomal disorder resulting from the deletion of all or part of the short arm of chromosome 18. This trias was first described in a patient by Zouboulis <jats:italic>et al<\/jats:italic>. (1994) and has been reported by different authors in four additional patients since then. We have reviewed the five almost identical cases that have been reported in 20\u00a0years and we suggest the existence of a new rare syndrome characterized by the trias keratosis pilaris, ulerythema ophryogenes and monosomy 18p. Recognition of the syndrome could assist in early diagnosis of monosomy 18p in these patients.<\/jats:p>","DOI":"10.1111\/1346-8138.12442","type":"journal-article","created":{"date-parts":[[2014,5,7]],"date-time":"2014-05-07T02:42:25Z","timestamp":1399430545000},"page":"371-376","source":"Crossref","is-referenced-by-count":14,"title":["Trias of keratosis pilaris, ulerythema ophryogenes and 18p monosomy: Zouboulis syndrome"],"prefix":"10.1111","volume":"41","author":[{"given":"Aikaterini I.","family":"Liakou","sequence":"first","affiliation":[{"name":"Departments of Dermatology, Venereology, Allergology and Immunology Dessau Medical Center Dessau Germany"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Andr\u00e9 V.","family":"Esteves de Carvalho","sequence":"additional","affiliation":[{"name":"Department of Dermatology Santa Casa de Misericordia Hospital Complex Porto Alegre RS Brazil"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Lujdmila 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