{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,10,1]],"date-time":"2025-10-01T16:14:06Z","timestamp":1759335246187,"version":"3.37.3"},"reference-count":15,"publisher":"Wiley","issue":"4","license":[{"start":{"date-parts":[[2016,12,3]],"date-time":"2016-12-03T00:00:00Z","timestamp":1480723200000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["The Journal of Dermatology"],"published-print":{"date-parts":[[2017,4]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:p>Bronchiolitis obliterans is a small\u2010airway obstructive lung disease for which immunologically mediated pathogenesis is supposed. Frequent association of bronchiolitis obliterans with paraneoplastic pemphigus is well known, but its association with other autoimmune bullous diseases has not been reported except for a case of anti\u2010laminin\u2010332\u2010type mucous membrane pemphigoid in a patient with chronic graft\u2010versus\u2010host disease. We report a case of non\u2010paraneoplastic autoimmune subepidermal bullous disease associated with fatal bronchiolitis obliterans in a patient without transplantation. Although the patient's serum contained immunoglobulin (Ig)A antibodies to the 180\u2010kDa bullous pemphigoid antigen\/type XVII collagen and IgG antibodies to laminin\u2010332, diagnosis of either linear IgA bullous dermatosis or mucous membrane pemphigoid could not be made because of the failure to detect linear IgA deposition at the basement membrane zone by direct immunofluorescence and the lack of mucous membrane lesions. Physicians should be aware that autoimmune bullous diseases other than paraneoplastic pemphigus can also associate with this rare but potentially fatal lung disease.<\/jats:p>","DOI":"10.1111\/1346-8138.13706","type":"journal-article","created":{"date-parts":[[2016,12,3]],"date-time":"2016-12-03T07:05:26Z","timestamp":1480748726000},"page":"461-464","source":"Crossref","is-referenced-by-count":3,"title":["Non\u2010paraneoplastic autoimmune subepidermal bullous disease associated with fatal bronchiolitis obliterans"],"prefix":"10.1111","volume":"44","author":[{"given":"Mari","family":"Orime","sequence":"first","affiliation":[{"name":"Division of Dermatology Niigata University Graduate School of Medical and Dental Sciences Niigata Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Katsuhiro","family":"Tomiyama","sequence":"additional","affiliation":[{"name":"Department of Dermatology Niigata City General Hospital Niigata 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