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Computed tomography following a witnessed collapse revealed diffuse subarachnoid hemorrhage and severe cerebral edema. An autopsy confirmed the radiographic findings and detected bilateral retinal hemorrhages, optic nerve sheath hemorrhages, and a ruptured saccular aneurysm due to focal fibromuscular dysplasia involving the intracranial right vertebral artery. This case documents a fatal subarachnoid hemorrhage in a child with an intracranial saccular aneurysm caused by fibromuscular dysplasia. The associated retinal hemorrhages are easily detected by postmortem monocular indirect ophthalmoscopy.<\/jats:p>","DOI":"10.1111\/1556-4029.14196","type":"journal-article","created":{"date-parts":[[2019,9,25]],"date-time":"2019-09-25T22:02:18Z","timestamp":1569448938000},"page":"649-654","update-policy":"http:\/\/dx.doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":3,"title":["Hemorrhagic Retinopathy and Optic Nerve Sheath Hemorrhage Associated With Fatal Subarachnoid Hemorrhage from a Ruptured Intracranial Aneurysm Due to Segmental Fibromuscular Dysplasia"],"prefix":"10.1111","volume":"65","author":[{"given":"Elizabeth O.","family":"Silloca\u2010Cabana","sequence":"first","affiliation":[{"name":"Department of Pathology Wake Forest Baptist Health Medical Center Blvd. Winston Salem NC 27157"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Vivian M.","family":"Hathuc","sequence":"additional","affiliation":[{"name":"Department of Pathology 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