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Anti\u2010melanoma differentiation\u2010associated protein 5 (anti\u2010MDA5)\u2010positive JDM patients are typically characterized by the presence of skin ulcers and rapidly progressing ILD (RP\u2010ILD). Although cardiac involvement is not an expected involvement in anti\u2010MDA5\u2010positive JDM cases, it is significant because it can be fatal. In this report, an anti\u2010MDA5 myositis\u2010specific autoantibody\u2010positive JDM case referred with the diagnosis of psoriatic arthritis in whom cardiomyopathy and arrhythmia were detected in follow\u2010up is presented. Since cardiac involvement is associated with mortality, it would be useful to follow up anti\u2010MDA5 positive patients for cardiac involvement in addition to lung involvement. Tofacitinib is a promising treatment option in treatment\u2010resistant JDM.<\/jats:p>","DOI":"10.1111\/1756-185x.14630","type":"journal-article","created":{"date-parts":[[2023,2,28]],"date-time":"2023-02-28T12:23:09Z","timestamp":1677586989000},"page":"1582-1585","update-policy":"https:\/\/doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":8,"title":["Cardiac involvement in a case of juvenile dermatomyositis with positive anti\u2010melanoma differentiation associated protein 5 antibody"],"prefix":"10.1111","volume":"26","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-8012-2774","authenticated-orcid":false,"given":"Melike Mehve\u015f","family":"Kaplan","sequence":"first","affiliation":[{"name":"Division of Pediatric Rheumatology, Department of Pediatrics University of Health Sciences, Ankara City Hospital  Ankara 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