{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,5,21]],"date-time":"2026-05-21T09:48:00Z","timestamp":1779356880575,"version":"3.51.4"},"reference-count":11,"publisher":"Wiley","issue":"4","license":[{"start":{"date-parts":[[2025,4,14]],"date-time":"2025-04-14T00:00:00Z","timestamp":1744588800000},"content-version":"vor","delay-in-days":13,"URL":"http:\/\/creativecommons.org\/licenses\/by\/4.0\/"}],"content-domain":{"domain":["onlinelibrary.wiley.com"],"crossmark-restriction":true},"short-container-title":["Int J of Rheum Dis"],"published-print":{"date-parts":[[2025,4]]},"abstract":"<jats:title>ABSTRACT<\/jats:title>\n                  <jats:p>Hughes\u2013Stovin Syndrome (HSS) is a rare, life\u2010threatening condition characterized by thrombophlebitis and pulmonary artery aneurysms, often viewed as a variant of Beh\u00e7et's disease. Its diagnosis and management are challenging due to its rarity and overlapping symptoms with other vascular disorders. A 33\u2010year\u2010old male presented with massive hemoptysis and a history of recurrent oral and scrotal ulcers. Imaging revealed bilateral pulmonary emboli, a pulmonary artery aneurysm, and a large right atrial thrombus. These findings, coupled with his clinical history, led to a diagnosis of HSS. A multidisciplinary team initiated anticoagulation for the thrombus and immunosuppressive therapy (steroids, cyclophosphamide). Follow\u2010up imaging showed improvement in both the aneurysm and thrombus. This case highlights the complexity of diagnosing and managing HSS. Early recognition, supported by a collaborative approach, is critical to improving outcomes in this rare syndrome.<\/jats:p>","DOI":"10.1111\/1756-185x.70227","type":"journal-article","created":{"date-parts":[[2025,4,14]],"date-time":"2025-04-14T03:31:01Z","timestamp":1744601461000},"update-policy":"https:\/\/doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":2,"title":["Hughes\u2013Stovin Syndrome: A Rare Cause of Pulmonary Artery Aneurysm and Thrombosis\u2014A Case Report"],"prefix":"10.1111","volume":"28","author":[{"ORCID":"https:\/\/orcid.org\/0009-0003-0269-3103","authenticated-orcid":false,"given":"Abdul","family":"Qadir","sequence":"first","affiliation":[{"name":"Department of Medicine Hamad Medical Corporation HGH  Doha Qatar"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Amal Wael","family":"Abdellatif","sequence":"additional","affiliation":[{"name":"Department of Medicine Hamad Medical Corporation HGH  Doha Qatar"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Aamir","family":"Waheed","sequence":"additional","affiliation":[{"name":"Department of Medicine Hamad Medical Corporation HGH  Doha Qatar"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0009-0002-4350-0040","authenticated-orcid":false,"given":"Mamunul","family":"Islam","sequence":"additional","affiliation":[{"name":"Medical Education Department Hamad Medical Corporation  Doha Qatar"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"311","published-online":{"date-parts":[[2025,4,14]]},"reference":[{"key":"e_1_2_1_11_2_1","doi-asserted-by":"publisher","DOI":"10.1186\/1750-1172-6-15"},{"issue":"5","key":"e_1_2_1_11_3_1","article-title":"Hughes Stovin Syndrome, a Rare Form of Behcet's Disease Presenting as Recurrent Intracardiac Thrombus","volume":"12","author":"Anupama B. 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