{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,7,23]],"date-time":"2026-07-23T01:30:30Z","timestamp":1784770230596,"version":"3.55.0"},"reference-count":8,"publisher":"Wiley","issue":"7-8","license":[{"start":{"date-parts":[[2025,6,2]],"date-time":"2025-06-02T00:00:00Z","timestamp":1748822400000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"funder":[{"DOI":"10.13039\/100015539","name":"Australian Government","doi-asserted-by":"publisher","id":[{"id":"10.13039\/100015539","id-type":"DOI","asserted-by":"publisher"}]}],"content-domain":{"domain":["onlinelibrary.wiley.com"],"crossmark-restriction":true},"short-container-title":["ANZ Journal of Surgery"],"published-print":{"date-parts":[[2025,7]]},"abstract":"<jats:title>ABSTRACT<\/jats:title><jats:sec><jats:title>Background<\/jats:title><jats:p>While complete repair of pulmonary atresia with ventricular septal defect and major aortopulmonary collateral arteries (PA\/VSD\/MAPCAs) is achieved with low surgical mortality, this condition poses ongoing mid\u2010 and late\u2010term mortality. The long\u2010term data for repair of pulmonary atresia with ventricular septal defect and major aortopulmonary collateral arteries at a single institution are presented in this paper.<\/jats:p><\/jats:sec><jats:sec><jats:title>Methods<\/jats:title><jats:p>We reviewed the outcomes for 100 patients with PA\/VSD\/MAPCAs who had surgery between January 1987 and July 2018. Two patients were excluded who had palliative surgery not intended to reach a complete repair.<\/jats:p><\/jats:sec><jats:sec><jats:title>Results<\/jats:title><jats:p>Of the 98 patients who were suitable candidates for complete repair, 13% (13\/98) had primary complete repair and 64% (63\/98) had staged complete repair. Estimated survival at 1, 5, 10, and 20\u2009years of age was 93%, 87%, 81%, and 76%, respectively. The median age of those patients alive at follow\u2010up was 15 (interquartile range 9\u201321) years. Freedom from reintervention after staged complete repair was 58% at 5\u2009years after complete repair. Ligating or embolizing MAPCAs was associated with a decreased hazard of death in the staged complete repair group (hazard ratio 0.6, <jats:italic>p<\/jats:italic>\u2010value 0.04).<\/jats:p><\/jats:sec><jats:sec><jats:title>Conclusions<\/jats:title><jats:p>A strategy of staged complete repair can be used to achieve complete repair and stable long\u2010term survival for patients with PA\/VSD\/MAPCAs.<\/jats:p><\/jats:sec>","DOI":"10.1111\/ans.70193","type":"journal-article","created":{"date-parts":[[2025,6,2]],"date-time":"2025-06-02T05:10:54Z","timestamp":1748841054000},"page":"1400-1406","update-policy":"https:\/\/doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":1,"title":["Long\u2010Term Outcomes of Repair of Pulmonary Atresia With Ventricular Septal Defect and Major Aortopulmonary Collateral Arteries"],"prefix":"10.1111","volume":"95","author":[{"ORCID":"https:\/\/orcid.org\/0000-0001-9383-3498","authenticated-orcid":false,"given":"Samuel J.","family":"Macalister","sequence":"first","affiliation":[{"name":"Department of Cardiac Surgery Royal Children's Hospital  Melbourne Australia"},{"name":"Department of Paediatrics University of Melbourne  Melbourne Australia"},{"name":"Heart Research Group Murdoch Children's Research Institute  Melbourne Australia"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Igor E.","family":"Konstantinov","sequence":"additional","affiliation":[{"name":"Department of Cardiac Surgery Royal Children's Hospital  Melbourne Australia"},{"name":"Department of Paediatrics University of Melbourne  Melbourne Australia"},{"name":"Heart Research Group Murdoch Children's Research Institute  Melbourne Australia"},{"name":"Melbourne Children's Centre for Cardiovascular Genomics and Regenerative Medicine  Melbourne Australia"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-9924-7016","authenticated-orcid":false,"given":"Tyson A.","family":"Fricke","sequence":"additional","affiliation":[{"name":"Department of Cardiac Surgery Royal Children's Hospital  Melbourne Australia"},{"name":"Department of Paediatrics University of Melbourne  Melbourne Australia"},{"name":"Heart Research Group Murdoch Children's Research Institute  Melbourne Australia"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Robert G.","family":"Weintraub","sequence":"additional","affiliation":[{"name":"Department of Paediatrics University of Melbourne  Melbourne Australia"},{"name":"Heart Research Group Murdoch Children's Research Institute  Melbourne Australia"},{"name":"Melbourne Children's Centre for Cardiovascular Genomics and Regenerative Medicine  Melbourne Australia"},{"name":"Department of Cardiology Royal Children's Hospital  Melbourne Australia"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Christian P.","family":"Brizard","sequence":"additional","affiliation":[{"name":"Department of Cardiac Surgery Royal Children's Hospital  Melbourne Australia"},{"name":"Department of Paediatrics University of Melbourne  Melbourne Australia"},{"name":"Heart Research Group Murdoch Children's Research Institute  Melbourne Australia"},{"name":"Melbourne Children's Centre for Cardiovascular Genomics and Regenerative Medicine  Melbourne Australia"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Edward","family":"Buratto","sequence":"additional","affiliation":[{"name":"Department of Cardiac Surgery Royal Children's Hospital  Melbourne Australia"},{"name":"Department of Paediatrics University of Melbourne  Melbourne Australia"},{"name":"Heart Research Group Murdoch Children's Research Institute  Melbourne Australia"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"311","published-online":{"date-parts":[[2025,6,2]]},"reference":[{"key":"e_1_2_10_2_1","doi-asserted-by":"publisher","DOI":"10.1016\/S0022-5223(95)70305-5"},{"key":"e_1_2_10_3_1","doi-asserted-by":"publisher","DOI":"10.1111\/jocs.16299"},{"key":"e_1_2_10_4_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.athoracsur.2022.09.022"},{"key":"e_1_2_10_5_1","doi-asserted-by":"publisher","DOI":"10.1016\/s0003\u20104975(97)01126\u20100"},{"key":"e_1_2_10_6_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.jtcvs.2018.03.153"},{"key":"e_1_2_10_7_1","doi-asserted-by":"publisher","DOI":"10.3390\/children9040515"},{"key":"e_1_2_10_8_1","doi-asserted-by":"publisher","DOI":"10.1093\/ejcts\/ezz070"},{"key":"e_1_2_10_9_1","doi-asserted-by":"publisher","DOI":"10.1017\/S1047951120004047"}],"container-title":["ANZ Journal of Surgery"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/pdf\/10.1111\/ans.70193","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2025,9,6]],"date-time":"2025-09-06T06:28:53Z","timestamp":1757140133000},"score":1,"resource":{"primary":{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/10.1111\/ans.70193"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2025,6,2]]},"references-count":8,"journal-issue":{"issue":"7-8","published-print":{"date-parts":[[2025,7]]}},"alternative-id":["10.1111\/ans.70193"],"URL":"https:\/\/doi.org\/10.1111\/ans.70193","archive":["Portico"],"relation":{},"ISSN":["1445-1433","1445-2197"],"issn-type":[{"value":"1445-1433","type":"print"},{"value":"1445-2197","type":"electronic"}],"subject":[],"published":{"date-parts":[[2025,6,2]]},"assertion":[{"value":"2024-08-14","order":0,"name":"received","label":"Received","group":{"name":"publication_history","label":"Publication 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