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Such an association between two rare diseases cannot be fortuitous and implies a physiopathological link that we discuss in this paper. This association is a new significant fact to add to the reflexion on FD causes, suggesting that skin abnormality of DEB could act as a factor of a specific skin barrier alteration which could favor FD. Scarring alopecia with tufted folliculitis and pustules on inflamed skin at the vertex of a woman with dominant dystrophic epidermolysis bullosa.<\/jats:p>","DOI":"10.1111\/bjd.21796","type":"journal-article","created":{"date-parts":[[2022,7,29]],"date-time":"2022-07-29T09:15:34Z","timestamp":1659086134000},"page":"1026-1028","update-policy":"https:\/\/doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":2,"title":["Folliculitis decalvans and dystrophic epidermolysis bullosa: a significant association"],"prefix":"10.1093","volume":"187","author":[{"ORCID":"https:\/\/orcid.org\/0000-0001-7137-8527","authenticated-orcid":false,"given":"Bruno","family":"Matard","sequence":"first","affiliation":[{"name":"Sabouraud Centre for Hair Diseases H\u00f4pital Saint-Louis Paris France"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Emmanuelle","family":"Bourrat","sequence":"additional","affiliation":[{"name":"Department of Dermatology Expert Centre for Epidermolysis Bullosa (MAGEC), H\u00f4pital Saint-Louis Paris France"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Marine","family":"Cavali\u00e9","sequence":"additional","affiliation":[{"name":"CRMRP-Sud Nice, Department of Dermatology H\u00f4pital L\u2019Archet, Centre Hospitalier Universitaire de Nice Nice France"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-6063-5409","authenticated-orcid":false,"given":"Christine","family":"Chiaverini","sequence":"additional","affiliation":[{"name":"CRMRP-Sud Nice, Department of Dermatology H\u00f4pital L\u2019Archet, Centre Hospitalier Universitaire de Nice Nice France"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Pascal","family":"Reygagne","sequence":"additional","affiliation":[{"name":"Sabouraud Centre for Hair Diseases H\u00f4pital Saint-Louis Paris France"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"286","published-online":{"date-parts":[[2022,12,1]]},"reference":[{"key":"2023010808105623000_bjd21796-bib-0001","doi-asserted-by":"crossref","first-page":"295","DOI":"10.1111\/exd.13916","article-title":"Folliculitis decalvans is characterized by a persistent, abnormal subepidermal microbiota","volume":"29","author":"Matard","year":"2020","journal-title":"Exp Dermatol"},{"key":"2023010808105623000_bjd21796-bib-0002","doi-asserted-by":"crossref","first-page":"1355","DOI":"10.1016\/j.jaad.2020.10.073","article-title":"Folliculitis decalvans microbiological signature is specific for disease clinical phenotype","volume":"85","author":"Moreno-Arrones","year":"2021","journal-title":"J Am Acad Dermatol"},{"key":"2023010808105623000_bjd21796-bib-0003","doi-asserted-by":"crossref","first-page":"570","DOI":"10.2340\/00015555-2924","article-title":"Inflammasome activation characterizes lesional skin of folliculitis decalvans","volume":"98","author":"Eyraud","year":"2018","journal-title":"Acta Derm Venereol"},{"key":"2023010808105623000_bjd21796-bib-0004","doi-asserted-by":"crossref","first-page":"339","DOI":"10.1159\/000485521","article-title":"Epidermolysis bullosa pruriginosa associated with folliculitis decalvans: case report and review of the literature","volume":"4","author":"Rivitti-Machado","year":"2018","journal-title":"Skin Appendage Disord"},{"key":"2023010808105623000_bjd21796-bib-0005","doi-asserted-by":"crossref","first-page":"165","DOI":"10.1016\/j.det.2009.10.018","article-title":"Alopecia in epidermolysis bullosa","volume":"28","author":"Tosti","year":"2010","journal-title":"Dermatol Clin"},{"key":"2023010808105623000_bjd21796-bib-0006","doi-asserted-by":"crossref","first-page":"1080","DOI":"10.1111\/exd.14212","article-title":"A niche in the spotlight: could external factors critically disturb hair follicle homeostasis and contribute to inflammatory hair follicle diseases? 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