{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,10,1]],"date-time":"2025-10-01T15:38:35Z","timestamp":1759333115787},"reference-count":15,"publisher":"Wiley","issue":"5","license":[{"start":{"date-parts":[[2013,11,14]],"date-time":"2013-11-14T00:00:00Z","timestamp":1384387200000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":["onlinelibrary.wiley.com"],"crossmark-restriction":true},"short-container-title":["Br J Haematol"],"published-print":{"date-parts":[[2014,3]]},"abstract":"<jats:title>Summary<\/jats:title><jats:p>The significance of paroxysmal nocturnal haemoglobinuria (<jats:styled-content style=\"fixed-case\">PNH<\/jats:styled-content><jats:sup>pos<\/jats:sup>) cells and leucocyte subset telomere lengths in paediatric aplastic anaemia (<jats:styled-content style=\"fixed-case\">AA<\/jats:styled-content>) is unknown. Among 22 children receiving immunosuppressive therapy (<jats:styled-content style=\"fixed-case\">IST<\/jats:styled-content>) for <jats:styled-content style=\"fixed-case\">AA<\/jats:styled-content>, 73% (16\/22) were <jats:styled-content style=\"fixed-case\">PNH<\/jats:styled-content><jats:sup>pos<\/jats:sup>, of whom 94% achieved at least a partial response (<jats:styled-content style=\"fixed-case\">PR<\/jats:styled-content>) to <jats:styled-content style=\"fixed-case\">IST<\/jats:styled-content>; 11\/16 (69%) achieved complete response (<jats:styled-content style=\"fixed-case\">CR<\/jats:styled-content>). Only 2\/6 (33%) <jats:styled-content style=\"fixed-case\">PNH<\/jats:styled-content><jats:sup>neg<\/jats:sup> patients achieved <jats:styled-content style=\"fixed-case\">PR<\/jats:styled-content>. <jats:styled-content style=\"fixed-case\">PNH<\/jats:styled-content><jats:sup>pos<\/jats:sup> patients were less likely to fail <jats:styled-content style=\"fixed-case\">IST<\/jats:styled-content> compared to <jats:styled-content style=\"fixed-case\">PNH<\/jats:styled-content><jats:sup>neg<\/jats:sup> patients (odds ratio 0\u00b7033; 95% confidence interval 0\u00b7002\u20130\u00b7468; <jats:italic>P<\/jats:italic>\u00a0=\u00a00\u00b7012). Children with <jats:styled-content style=\"fixed-case\">AA<\/jats:styled-content> had short granulocyte (<jats:italic>P<\/jats:italic>\u00a0=\u00a07\u00b78\u00a0\u00d7\u00a010<jats:sup>\u22129<\/jats:sup>), natural killer cell (<jats:italic>P<\/jats:italic>\u00a0=\u00a06\u00b70\u00a0\u00d7\u00a010<jats:sup>\u22124<\/jats:sup>), na\u00efve T lymphocyte (<jats:italic>P<\/jats:italic>\u00a0=\u00a00\u00b7002) and B lymphocyte (<jats:italic>P<\/jats:italic>\u00a0=\u00a00\u00b7005) telomeres compared to age\u2010matched normative data.<\/jats:p>","DOI":"10.1111\/bjh.12656","type":"journal-article","created":{"date-parts":[[2013,11,14]],"date-time":"2013-11-14T22:41:11Z","timestamp":1384468871000},"page":"717-721","update-policy":"http:\/\/dx.doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":26,"title":["Paroxysmal nocturnal haemoglobinuria phenotype cells and leucocyte subset telomere length in childhood acquired aplastic anaemia"],"prefix":"10.1111","volume":"164","author":[{"given":"Perri R.","family":"Tutelman","sequence":"first","affiliation":[{"name":"Division of Pediatric Hematology\/Oncology\/Bone Marrow Transplantation British Columbia Children's Hospital University of British Columbia Vancouver BC Canada"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Geraldine","family":"Aubert","sequence":"additional","affiliation":[{"name":"Terry Fox Laboratory British Columbia Cancer Agency Vancouver BC Canada"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Ruth A.","family":"Milner","sequence":"additional","affiliation":[{"name":"Child and Family Research Institute University of British Columbia Vancouver BC Canada"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Bakul I.","family":"Dalal","sequence":"additional","affiliation":[{"name":"Division of Laboratory Hematology Department of Pathology and Laboratory Medicine Vancouver General Hospital Vancouver BC 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