{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,17]],"date-time":"2026-09-17T01:40:16Z","timestamp":1789609216291,"version":"build-2803163510"},"reference-count":15,"publisher":"Wiley","issue":"5","license":[{"start":{"date-parts":[[2015,9,11]],"date-time":"2015-09-11T00:00:00Z","timestamp":1441929600000},"content-version":"tdm","delay-in-days":0,"URL":"http:\/\/doi.wiley.com\/10.1002\/tdm_license_1"},{"start":{"date-parts":[[2015,9,11]],"date-time":"2015-09-11T00:00:00Z","timestamp":1441929600000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Br J Haematol"],"published-print":{"date-parts":[[2015,12]]},"DOI":"10.1111\/bjh.13654","type":"journal-article","created":{"date-parts":[[2015,9,11]],"date-time":"2015-09-11T08:14:24Z","timestamp":1441959264000},"page":"830-835","source":"Crossref","is-referenced-by-count":69,"title":["The utility of ADAMTS13 in differentiating TTP from other acute thrombotic microangiopathies: results from the UK TTP Registry"],"prefix":"10.1111","volume":"171","author":[{"given":"Sevda","family":"Hassan","sequence":"first","affiliation":[{"name":"Department of Nephrology; The Royal London Hospital; London UK"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"John-Paul","family":"Westwood","sequence":"additional","affiliation":[{"name":"Department of Haematology; University College London Hospital; London UK"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Debra","family":"Ellis","sequence":"additional","affiliation":[{"name":"Department of Haematology; University College London Hospital; London UK"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Chris","family":"Laing","sequence":"additional","affiliation":[{"name":"UCL Centre for Nephrology; Royal Free Hospital; London UK"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Siobhan","family":"Mc Guckin","sequence":"additional","affiliation":[{"name":"Department of Haematology; University College London Hospital; London UK"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Sylvia","family":"Benjamin","sequence":"additional","affiliation":[{"name":"NHSBT Therapeutic Apheresis Services (TAS) and Oxford University Hospitals Trust; Oxford UK"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Marie","family":"Scully","sequence":"additional","affiliation":[{"name":"Department of Haematology; University College London Hospital; London UK"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"311","published-online":{"date-parts":[[2015,9,11]]},"reference":[{"key":"10.1111\/bjh.13654-BIB0001|bjh13654-cit-0001","doi-asserted-by":"crossref","first-page":"329","DOI":"10.1111\/j.1445-5994.2007.01338.x","article-title":"Anti-CD20 antibody in thrombotic thrombocytopenic purpura refractory to plasma exchange","volume":"37","author":"Chow","year":"2007","journal-title":"Internal Medicine Journal"},{"key":"10.1111\/bjh.13654-BIB0002|bjh13654-cit-0002","doi-asserted-by":"crossref","first-page":"e10208","DOI":"10.1371\/journal.pone.0010208","article-title":"Predictive features of severe acquired ADAMTS13 deficiency in idiopathic thrombotic microangiopathies: the French TMA reference center experience","volume":"5","author":"Coppo","year":"2010","journal-title":"PLoS ONE"},{"key":"10.1111\/bjh.13654-BIB0003|bjh13654-cit-0003","doi-asserted-by":"crossref","first-page":"100","DOI":"10.1046\/j.1365-2141.2001.02704.x","article-title":"Microangiopathic haemolytic anaemia in metastasizing malignant tumours is not associated with a severe deficiency of the von Willebrand factor-cleaving protease","volume":"113","author":"Fontana","year":"2001","journal-title":"British Journal of Haematology"},{"key":"10.1111\/bjh.13654-BIB0004|bjh13654-cit-0004","doi-asserted-by":"crossref","first-page":"2839","DOI":"10.1182\/blood.V91.8.2839.2839_2839_2846","article-title":"Acquired deficiency of von Willebrand factor-cleaving protease in a patient with thrombotic thrombocytopenic purpura","volume":"91","author":"Furlan","year":"1998","journal-title":"Blood"},{"key":"10.1111\/bjh.13654-BIB0005|bjh13654-cit-0005","doi-asserted-by":"crossref","first-page":"2431","DOI":"10.1007\/s00467-010-1555-5","article-title":"Genetics and complement in atypical HUS","volume":"25","author":"Kavanagh","year":"2010","journal-title":"Pediatric Nephrology(Berlin, Germany)"},{"key":"10.1111\/bjh.13654-BIB0006|bjh13654-cit-0006","doi-asserted-by":"crossref","first-page":"93","DOI":"10.1111\/j.1365-2141.2005.05420.x","article-title":"FRETS-VWF73, a first fluorogenic substrate for ADAMTS13 assay","volume":"129","author":"Kokame","year":"2005","journal-title":"British Journal of Haematology"},{"key":"10.1111\/bjh.13654-BIB0007|bjh13654-cit-0007","doi-asserted-by":"crossref","first-page":"60","DOI":"10.1186\/1750-1172-6-60","article-title":"Atypical hemolytic uremic syndrome","volume":"6","author":"Loirat","year":"2011","journal-title":"Orphanet journal of rare diseases"},{"key":"10.1111\/bjh.13654-BIB0008|bjh13654-cit-0008","volume-title":"Eculizumab for Treating Atypical Haemolytic Uraemic Syndrome. NICE Highly Specialised Technology Guidance (HST1)","author":"NICE","year":"2015"},{"key":"10.1111\/bjh.13654-BIB0009|bjh13654-cit-0009","doi-asserted-by":"crossref","first-page":"1017","DOI":"10.1093\/qjmed\/hct142","article-title":"Hemolysis and schistocytosis in the emergency department: consider pseudothrombotic microangiopathy related to vitamin B12 deficiency","volume":"106","author":"Noel","year":"2013","journal-title":"QJM"},{"key":"10.1111\/bjh.13654-BIB0010|bjh13654-cit-0010","doi-asserted-by":"crossref","first-page":"759","DOI":"10.1111\/bjh.12718","article-title":"How I treat thrombotic thrombocytopenic purpura and atypical haemolytic uraemic syndrome","volume":"164","author":"Scully","year":"2014","journal-title":"British Journal of Haematology"},{"key":"10.1111\/bjh.13654-BIB0011|bjh13654-cit-0011","doi-asserted-by":"crossref","first-page":"451","DOI":"10.1111\/j.1365-2141.2006.06448.x","article-title":"Remission in acute refractory and relapsing thrombotic thrombocytopenic purpura following rituximab is associated with a reduction in IgG antibodies to ADAMTS-13","volume":"136","author":"Scully","year":"2007","journal-title":"British Journal of Haematology"},{"key":"10.1111\/bjh.13654-BIB0012|bjh13654-cit-0012","doi-asserted-by":"crossref","first-page":"323","DOI":"10.1111\/j.1365-2141.2012.09167.x","article-title":"Guidelines on the diagnosis and management of thrombotic thrombocytopenic purpura and other thrombotic microangiopathies","volume":"158","author":"Scully","year":"2012","journal-title":"British Journal of Haematology"},{"key":"10.1111\/bjh.13654-BIB0013|bjh13654-cit-0013","doi-asserted-by":"crossref","first-page":"2525","DOI":"10.1111\/j.1537-2995.2012.03646.x","article-title":"Decreasing frequency of plasma exchange complications in patients treated for thrombotic thrombocytopenic purpura-hemolytic uremic syndrome, 1996 to 2011","volume":"52","author":"Som","year":"2012","journal-title":"Transfusion"},{"key":"10.1111\/bjh.13654-BIB0014|bjh13654-cit-0014","doi-asserted-by":"crossref","first-page":"1585","DOI":"10.1056\/NEJM199811263392203","article-title":"Antibodies to von Willebrand factor-cleaving protease in acute thrombotic thrombocytopenic purpura","volume":"339","author":"Tsai","year":"1998","journal-title":"New England Journal of Medicine"},{"key":"10.1111\/bjh.13654-BIB0015|bjh13654-cit-0015","doi-asserted-by":"crossref","first-page":"643","DOI":"10.1038\/nrneph.2012.214","article-title":"Use of eculizumab for atypical haemolytic uraemic syndrome and C3 glomerulopathies","volume":"8","author":"Zuber","year":"2012","journal-title":"Nature Reviews Nephrology"}],"container-title":["British Journal of Haematology"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.wiley.com\/onlinelibrary\/tdm\/v1\/articles\/10.1111%2Fbjh.13654","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.wiley.com\/onlinelibrary\/tdm\/v1\/articles\/10.1111%2Fbjh.13654","content-type":"unspecified","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/onlinelibrary.wiley.com\/wol1\/doi\/10.1111\/bjh.13654\/fullpdf","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2021,7,4]],"date-time":"2021-07-04T08:54:08Z","timestamp":1625388848000},"score":1,"resource":{"primary":{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/10.1111\/bjh.13654"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2015,9,11]]},"references-count":15,"journal-issue":{"issue":"5","published-print":{"date-parts":[[2015,12]]}},"URL":"https:\/\/doi.org\/10.1111\/bjh.13654","archive":["Portico"],"relation":{},"ISSN":["0007-1048"],"issn-type":[{"value":"0007-1048","type":"print"}],"subject":[],"published":{"date-parts":[[2015,9,11]]}}}