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Historically, treatment is based on glucocorticoids and\/or blood transfusions, which is accompanied by significant toxicity and long\u2010term sequelae. Currently, stem cell transplantation is the only curative option for the haematological<jats:styled-content style=\"fixed-case\">DBA<\/jats:styled-content>phenotype. Whereas this procedure has been quite successful in the last decade in selected patients, novel therapies and biological insights are still warranted to improve clinical care for all<jats:styled-content style=\"fixed-case\">DBA<\/jats:styled-content>patients. In addition to paediatric haematologists, other physicians (e.g. endocrinologist, gynaecologist) should ideally be involved in the care of this chronic condition from an early age, to improve lifelong management of haematological and non\u2010haematological symptoms, and screen for<jats:styled-content style=\"fixed-case\">DBA<\/jats:styled-content>\u2010associated malignancies. Here we provide an overview of current knowledge and recommendations for the day\u2010to\u2010day care of<jats:styled-content style=\"fixed-case\">DBA<\/jats:styled-content>patients.<\/jats:p>","DOI":"10.1111\/bjh.15701","type":"journal-article","created":{"date-parts":[[2018,12,5]],"date-time":"2018-12-05T06:44:08Z","timestamp":1543992248000},"page":"123-133","update-policy":"https:\/\/doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":67,"title":["How I manage children with Diamond\u2010Blackfan anaemia"],"prefix":"10.1111","volume":"184","author":[{"given":"Marije","family":"Bartels","sequence":"first","affiliation":[{"name":"Paediatric Haematology Department Wilhelmina Children's Hospital University Medical Centre Utrecht Utrecht the Netherlands"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Marc","family":"Bierings","sequence":"additional","affiliation":[{"name":"Department of Stem cell transplantation Princess Maxima Centre for 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