{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,18]],"date-time":"2026-08-18T00:46:37Z","timestamp":1787013997713,"version":"build-2736575974"},"reference-count":10,"publisher":"Oxford University Press (OUP)","issue":"8","license":[{"start":{"date-parts":[[2013,12,1]],"date-time":"2013-12-01T00:00:00Z","timestamp":1385856000000},"content-version":"vor","delay-in-days":0,"URL":"https:\/\/academic.oup.com\/journals\/pages\/open_access\/funder_policies\/chorus\/standard_publication_model"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":[],"published-print":{"date-parts":[[2013,12,1]]},"abstract":"<jats:title>Summary<\/jats:title>\n                  <jats:p>Waldenstr\u00f6m macroglobulinaemia (WM) is a chronic lymphoproliferative disorder characterized by the presence of a monoclonal IgM paraprotein. Specific cutaneous features of WM include neoplastic cell infiltrates, IgM storage papules and IgM bullous dermatosis. We report a patient with subepidermal bullous disease associated with WM. Immunofluorescence identified IgM deposition along the basement membrane zone (BMZ) with circulating anti-BMZ IgM antibodies reacting with the dermal side of salt-split skin. The autoantibodies did not react with type VII collagen or laminin 332. Following failed treatment with doxycycline, prednisolone, intravenous immunoglobulin and dapsone, the patient was successfully treated with a modified RCVP regimen (rituximab, cyclophosphamide and prednisolone). To our knowledge, this is the first reported case of IgM bullous disease of WM treated with rituximab.<\/jats:p>","DOI":"10.1111\/ced.12166","type":"journal-article","created":{"date-parts":[[2013,6,19]],"date-time":"2013-06-19T07:53:13Z","timestamp":1371628393000},"page":"866-869","source":"Crossref","is-referenced-by-count":17,"title":["Immunobullous dermatosis associated with Waldenstr\u00f6m macroglobulinaemia treated with rituximab"],"prefix":"10.1093","volume":"38","author":[{"given":"M.","family":"Chattopadhyay","sequence":"first","affiliation":[{"name":"Department of Dermatology Cambridge University Hospitals NHS Foundation Trust Cambridge UK"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"E.","family":"Rytina","sequence":"additional","affiliation":[{"name":"Department of Histopathology Cambridge University Hospitals NHS Foundation Trust Cambridge UK"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"M.","family":"Dada","sequence":"additional","affiliation":[{"name":"Department of Histopathology West Suffolk Hospital NHS Trust Bury St Edmunds UK"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"B. 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