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Diagnostic criteria have evolved, and many attempts have been made to classify the vasculitides based on clinical and\/or histopathologic features, with an aim to develop standardized criteria. According to the EGPA Consensus Task Force recommendations, EGPA is a syndrome of asthma, eosinophilia, pulmonary infiltrates, and extrapulmonary vasculitis (such as cutaneous involvement with purpura). Histopathologic evidence of vasculitis in EGPA may be associated with eosinophilic infiltration and\/or perivascular granulomatous inflammation. We review clinicopathologic criteria of this enigmatic vasculopathy.<\/jats:p>","DOI":"10.1111\/cup.14065","type":"journal-article","created":{"date-parts":[[2021,5,21]],"date-time":"2021-05-21T12:31:37Z","timestamp":1621600297000},"page":"1379-1386","update-policy":"https:\/\/doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":31,"title":["Eosinophilic granulomatosis with polyangiitis: Cutaneous clinical and histopathologic differential diagnosis"],"prefix":"10.1111","volume":"48","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-7196-0637","authenticated-orcid":false,"given":"Elisabeth S.","family":"Tabb","sequence":"first","affiliation":[{"name":"Pathology Service Massachusetts General Hospital and Harvard Medical School  Boston Massachusetts USA"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Lyn M.","family":"Duncan","sequence":"additional","affiliation":[{"name":"Pathology Service Massachusetts General Hospital and Harvard Medical 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