{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,18]],"date-time":"2026-08-18T00:47:44Z","timestamp":1787014064823,"version":"build-2736575974"},"reference-count":50,"publisher":"Wiley","issue":"2","license":[{"start":{"date-parts":[[2023,8,30]],"date-time":"2023-08-30T00:00:00Z","timestamp":1693353600000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":["onlinelibrary.wiley.com"],"crossmark-restriction":true},"short-container-title":["J Cutan Pathol"],"published-print":{"date-parts":[[2024,2]]},"abstract":"<jats:title>Abstract<\/jats:title>\n                  <jats:p>So far, confusion exists regarding the question of whether hereditary perifollicular fibromas and fibrofolliculomas can be distinguished from each other. Here, histopathological arguments are presented to clarify this terminological problem. In 1977, Birt et al. described a large kindred affected with hereditary multiple \u201cfibrofolliculomas,\u201d which they thought were \u201ca hitherto unrecognized pilar hamartoma,\u201d but they never claimed the fibrofolliculomas were part of a syndrome. A careful microscopic comparison shows, however, that the tumors are clinically and histopathologically identical to perifollicular fibromas, as first described by Burnier and Rej\u0161ek in 1925. Their familial occurrence was discovered in 1971 by Civatte and Le Tr\u00e9guilly. Before 1977, the term \u201cperifollicular fibroma\u201d was used for these skin tumors. By contrast, Hornstein and Knickenberg described in 1975 perifollicular fibromas as a cutaneous marker of a syndrome characterized by a predisposition to colon cancer and pneumothorax. Later, two French groups erroneously proposed the term \u201cBirt\u2013Hogg\u2013Dub\u00e9 syndrome\u201d to describe the co\u2010occurrence of fibrofolliculomas, trichodiscomas, and acrochordons, which was contrary to what Birt et al. had in mind. Hence, today, we should discriminate between the hereditary nonsyndromic perifollicular fibromas, as documented by Civatte and Le Tr\u00e9guilly and later by Birt et al., and the syndromic perifollicular fibromas, as delineated by Hornstein and Knickenberg.<\/jats:p>","DOI":"10.1111\/cup.14522","type":"journal-article","created":{"date-parts":[[2023,8,31]],"date-time":"2023-08-31T02:14:55Z","timestamp":1693448095000},"page":"170-175","update-policy":"https:\/\/doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":3,"title":["What is in a name\u2014Perifollicular fibroma or fibrofolliculoma?"],"prefix":"10.1111","volume":"51","author":[{"ORCID":"https:\/\/orcid.org\/0000-0001-9957-1441","authenticated-orcid":false,"given":"Eckart","family":"Haneke","sequence":"first","affiliation":[{"name":"Department of Dermatology Inselspital University of Berne  Bern Switzerland"},{"name":"Dermatologic Practice Dermaticum  Freiburg Germany"},{"name":"Centro de Dermatolog\u00eda Epidermis, Instituto CUF, Senhora da Hora  Matosinhos Grande Porto Portugal"},{"name":"Department of Dermatology University Hospital of Ghent  Ghent Belgium"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Rudolf","family":"Happle","sequence":"additional","affiliation":[{"name":"Department of Dermatology Medical Center\u2014University of Freiburg  Germany"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"311","published-online":{"date-parts":[[2023,8,30]]},"reference":[{"key":"e_1_2_15_2_1","doi-asserted-by":"publisher","DOI":"10.1001\/archderm.1977.01640120042005"},{"key":"e_1_2_15_3_1","doi-asserted-by":"publisher","DOI":"10.1007\/BF00582068"},{"key":"e_1_2_15_4_1","first-page":"242","article-title":"Fibromes sous\u2010cutanes p\u00e9ripilares multiples du cou [Multiple subcutaneous perifoillicular fibromas of the neck]","volume":"32","author":"Burnier R","year":"1925","journal-title":"Bull Soc Fr Dermatol Syphiligr"},{"key":"e_1_2_15_5_1","doi-asserted-by":"publisher","DOI":"10.1001\/archderm.1960.01580060067008"},{"key":"e_1_2_15_6_1","doi-asserted-by":"publisher","DOI":"10.1111\/j.1600\u20100560.1977.tb00920.x"},{"issue":"8","key":"e_1_2_15_7_1","first-page":"601","article-title":"Fibrofolliculomes, trichodiscomes et acrochordons. 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