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This definition encompasses pathologies with very different pathological backgrounds, ultimately resulting in PH. For this reason, the latter can be possibly (though seldom) accompanied by cardiomyopathies, pathologies characterized by a structural and functionally abnormal myocardium not secondary to coronary disease, hypertension, valvular disease, or congenital heart disease. Notable examples of these diseases are sarcoidosis (a multi\u2010systemic inflammatory granulomatous disease, possibly involving the lung and the heart), systemic sclerosis (SSc) (a connective tissue disease [CTD], possibly causing interstitial lung disease [ILD], direct as well indirect involvement of the cardiovascular system), and chronic kidney disease (CKD) (a progressive pathological process involving the kidneys, with multi\u2010systemic involvement and possible development of a peculiar form of cardiomyopathy, i.e., uremic cardiomyopathy [UC]). The diagnostic work\u2010up of patients with coexistent PH and cardiomyopathies implies the use of multiple imaging techniques, with computed tomography (CT) and cardiovascular magnetic resonance (CMR) being among the most important. The knowledge of CT and MRI findings, together with a suggestive clinical picture, forms the basis for a correct diagnosis, therefore it is important for the radiologist to recognize them in complex clinical scenarios. The advent of new technologies (e.g., photon counting detectors) and the development of new artificial intelligence (AI) algorithms will further pave the way for improved diagnostic processes (also regarding this kind of pathologies) as well as allowing to perform a better prognostic evaluation.<\/jats:p>","DOI":"10.1111\/echo.70103","type":"journal-article","created":{"date-parts":[[2025,2,14]],"date-time":"2025-02-14T05:46:50Z","timestamp":1739512010000},"update-policy":"https:\/\/doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":2,"title":["Uncommon Causes of Pulmonary Hypertension With Associated Cardiomyopathy: Computed Tomography and Magnetic Resonance Imaging of Cardiothoracic Manifestations"],"prefix":"10.1111","volume":"42","author":[{"ORCID":"https:\/\/orcid.org\/0000-0001-8844-8210","authenticated-orcid":false,"given":"Emanuele","family":"Muscogiuri","sequence":"first","affiliation":[{"name":"Department of Radiology UZ Leuven  Leuven Belgium"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-6881-7533","authenticated-orcid":false,"given":"Valerie","family":"Van Ballaer","sequence":"additional","affiliation":[{"name":"Department of Radiology UZ Leuven  Leuven Belgium"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Walter","family":"De Wever","sequence":"additional","affiliation":[{"name":"Department of Radiology UZ Leuven  Leuven Belgium"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0009-0003-7699-5462","authenticated-orcid":false,"given":"Emanuele","family":"Di Dedda","sequence":"additional","affiliation":[{"name":"Department of Radiology UZ Leuven  Leuven Belgium"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-7410-6495","authenticated-orcid":false,"given":"Adriana","family":"Dubbeldam","sequence":"additional","affiliation":[{"name":"Department of Radiology UZ Leuven  Leuven Belgium"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-2214-5879","authenticated-orcid":false,"given":"Laurent","family":"Godinas","sequence":"additional","affiliation":[{"name":"Department of Pneumology UZ Leuven  Leuven Belgium"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-8394-9809","authenticated-orcid":false,"given":"Marion","family":"Delcroix","sequence":"additional","affiliation":[{"name":"Department of Pneumology UZ Leuven  Leuven Belgium"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-7495-9183","authenticated-orcid":false,"given":"Jan","family":"Bogaert","sequence":"additional","affiliation":[{"name":"Department of Radiology UZ Leuven  Leuven Belgium"},{"name":"Department of Imaging and Pathology KU Leuven  Leuven Belgium"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"311","published-online":{"date-parts":[[2025,2,14]]},"reference":[{"key":"e_1_2_8_2_1","doi-asserted-by":"publisher","DOI":"10.1093\/eurheartj\/ehac237"},{"key":"e_1_2_8_3_1","doi-asserted-by":"publisher","DOI":"10.1183\/13993003.01913-2018"},{"key":"e_1_2_8_4_1","doi-asserted-by":"publisher","DOI":"10.1161\/CIRCULATIONAHA.119.040295"},{"key":"e_1_2_8_5_1","doi-asserted-by":"publisher","DOI":"10.1001\/jama.2022.4402"},{"key":"e_1_2_8_6_1","doi-asserted-by":"publisher","DOI":"10.1038\/s41572-023-00486-7"},{"key":"e_1_2_8_7_1","doi-asserted-by":"publisher","DOI":"10.1136\/bmjmed-2022-000137"},{"key":"e_1_2_8_8_1","doi-asserted-by":"publisher","DOI":"10.1161\/CIRCRESAHA.113.301129"},{"key":"e_1_2_8_9_1","doi-asserted-by":"publisher","DOI":"10.4414\/SMW.2022.w30055"},{"key":"e_1_2_8_10_1","doi-asserted-by":"publisher","DOI":"10.1093\/eurheartj\/ehad194"},{"key":"e_1_2_8_11_1","doi-asserted-by":"publisher","DOI":"10.1148\/rg.2018170046"},{"key":"e_1_2_8_12_1","doi-asserted-by":"publisher","DOI":"10.3390\/diagnostics13091607"},{"key":"e_1_2_8_13_1","doi-asserted-by":"publisher","DOI":"10.1183\/20734735.0130-2023"},{"key":"e_1_2_8_14_1","doi-asserted-by":"publisher","DOI":"10.1148\/radiol.2020203108"},{"key":"e_1_2_8_15_1","doi-asserted-by":"publisher","DOI":"10.1007\/s00330-020-06846-1"},{"key":"e_1_2_8_16_1","doi-asserted-by":"publisher","DOI":"10.4103\/1817-1737.203742"},{"key":"e_1_2_8_17_1","doi-asserted-by":"publisher","DOI":"10.1148\/rg.210076"},{"key":"e_1_2_8_18_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.ijcard.2016.08.314"},{"key":"e_1_2_8_19_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.chest.2017.04.184"},{"key":"e_1_2_8_20_1","doi-asserted-by":"publisher","DOI":"10.1007\/s44326-024-00010-5"},{"key":"e_1_2_8_21_1","doi-asserted-by":"publisher","DOI":"10.1007\/978-3-642-23035-6"},{"issue":"3","key":"e_1_2_8_22_1","first-page":"2022","article-title":"Integrated Cardiopulmonary MRI Assessment of Pulmonary Hypertension","volume":"55","author":"Saunders L. 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