{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,2,14]],"date-time":"2026-02-14T05:28:11Z","timestamp":1771046891315,"version":"3.50.1"},"reference-count":30,"publisher":"Wiley","issue":"3","license":[{"start":{"date-parts":[[2023,3,6]],"date-time":"2023-03-06T00:00:00Z","timestamp":1678060800000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/creativecommons.org\/licenses\/by-nc\/4.0\/"}],"content-domain":{"domain":["onlinelibrary.wiley.com"],"crossmark-restriction":true},"short-container-title":["Haemophilia"],"published-print":{"date-parts":[[2023,5]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:sec><jats:title>Introduction<\/jats:title><jats:p>Von Willebrand Disease (VWD) is the most common inherited bleeding disorder. However, recognition of the disease by both the public and healthcare professionals lags behind that of other bleeding disorders, leading to delays in diagnosis and treatment for patients. Updated national guidelines are needed to highlight an appropriate pathway for managing VWD patients in a timelier manner.<\/jats:p><\/jats:sec><jats:sec><jats:title>Aim<\/jats:title><jats:p>To identify ways in which care for VWD can be achieved on a more equitable basis.<\/jats:p><\/jats:sec><jats:sec><jats:title>Methods<\/jats:title><jats:p>Using a modified Delphi approach, a panel of VWD experts developed 29 statements across five key themes. These were used to form an online survey that was distributed to healthcare professionals involved in VWD care across the UK and Republic of Ireland (ROI). Stopping criteria comprised 50 responses received, a 3\u2010month window for response (February\u2014April 2022) and 90% of statements passing consensus threshold. Threshold for consensus for each statement was agreed at 75%.<\/jats:p><\/jats:sec><jats:sec><jats:title>Results<\/jats:title><jats:p>A total of 66 responses were analysed with 29\/29 statements achieving consensus of which 27 attained \u226590% agreement. From the high degree of consensus, eight recommendations were derived regarding how detection and management of VWD can be improved to provide equity of care between men and women.<\/jats:p><\/jats:sec><jats:sec><jats:title>Conclusion<\/jats:title><jats:p>Implementation of these eight recommendations across the VWD pathway has the potential to raise the standard of care for patients in the UK and ROI by reducing delays to diagnosis and treatment initiation.<\/jats:p><\/jats:sec>","DOI":"10.1111\/hae.14765","type":"journal-article","created":{"date-parts":[[2023,3,6]],"date-time":"2023-03-06T17:39:07Z","timestamp":1678124347000},"page":"819-826","update-policy":"https:\/\/doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":5,"title":["An expert consensus to define how higher standards of equitable care for von Willebrand disease can be achieved in the UK and Republic of Ireland"],"prefix":"10.1111","volume":"29","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-8268-3268","authenticated-orcid":false,"given":"Mike","family":"Laffan","sequence":"first","affiliation":[{"name":"Centre for Haematology, Imperial College London  London UK"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-4269-8713","authenticated-orcid":false,"given":"Gary","family":"Benson","sequence":"additional","affiliation":[{"name":"NI Haemophilia Comprehensive Care Centre Belfast City Hospital  Belfast UK"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Cathy","family":"Farrelly","sequence":"additional","affiliation":[{"name":"Liverpool Hospital  Liverpool UK"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Keith","family":"Gomez","sequence":"additional","affiliation":[{"name":"Haemophilia Centre and Thrombosis Unit Royal Free London NHS Foundation Trust  London UK"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"April","family":"Jones","sequence":"additional","affiliation":[{"name":"Royal Victoria Infirmary  Newcastle UK"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Rhona","family":"Maclean","sequence":"additional","affiliation":[{"name":"Sheffield Royal Hallamshire  Sheffield UK"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"James","family":"O'Donnell","sequence":"additional","affiliation":[{"name":"Irish Centre for Vascular Biology, School of Pharmacy and Biomolecular Sciences Royal College of Surgeons in Ireland  Dublin UK"},{"name":"National Coagulation Centre St James's Hospital  Dublin UK"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-2999-4216","authenticated-orcid":false,"given":"Michelle","family":"Lavin","sequence":"additional","affiliation":[{"name":"Irish Centre for Vascular Biology, School of Pharmacy and Biomolecular Sciences Royal College of Surgeons in Ireland  Dublin UK"},{"name":"National Coagulation Centre St James's Hospital  Dublin UK"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"311","published-online":{"date-parts":[[2023,3,6]]},"reference":[{"key":"e_1_2_9_2_1","doi-asserted-by":"publisher","DOI":"10.1182\/bloodadvances.2020003265"},{"key":"e_1_2_9_3_1","doi-asserted-by":"publisher","DOI":"10.1177\/20406207211064064"},{"key":"e_1_2_9_4_1","doi-asserted-by":"publisher","DOI":"10.1111\/bjh.16681"},{"key":"e_1_2_9_5_1","unstructured":"Irish Haemophilia Society. 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