{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,8]],"date-time":"2026-09-08T14:01:03Z","timestamp":1788876063549,"version":"build-2803163510"},"reference-count":39,"publisher":"Wiley","issue":"6","license":[{"start":{"date-parts":[[2023,9,17]],"date-time":"2023-09-17T00:00:00Z","timestamp":1694908800000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":["onlinelibrary.wiley.com"],"crossmark-restriction":true},"short-container-title":["Haemophilia"],"published-print":{"date-parts":[[2023,11]]},"abstract":"<jats:title>Abstract<\/jats:title>\n                  <jats:sec>\n                    <jats:title>Introduction<\/jats:title>\n                    <jats:p>People with haemophilia's life expectancies have improved over time. Whether progress has been experienced equitably is unknown.<\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec>\n                    <jats:title>Aim<\/jats:title>\n                    <jats:p>To examine recorded haemophilia death (rHD) rates according to race and ethnicity in the United States (US).<\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec>\n                    <jats:title>Methods<\/jats:title>\n                    <jats:p>In this cohort study, rHDs were examined with US National Vital Statistics\u2019 1999\u20132020 Multiple Cause\u2010of\u2010Death data. rHD was defined as having a haemophilia A (D66) or B (D67) ICD\u201010 code in the death certificate (underlying or multiple causes of death). Age\u2010adjusted rHD rates were compared with age\u2010adjusted rate ratios (aRR) and 95% Confidence Intervals (CI).<\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec>\n                    <jats:title>Results<\/jats:title>\n                    <jats:p>There were 3115 rHDs in males with an rHD rate of 0.98 per 1 million males. Between 1999 and 2020, rHD rates declined by 46% in NH (Non\u2010Hispanic) White, 44% in NH Black (aRR\u00a0=\u00a00.56, 95%CI 0.43, 0.74), and 42% in Hispanic (aRR\u00a0=\u00a00.58, 95%CI 0.39, 0.88) males. However, rHD rates remained higher and were on average 30% greater in NH Black versus NH White males (aRR\u00a0=\u00a01.30 95% CI 1.16, 1.46). Among males with rHD, the median age at death rose from 54.5 to 65.5\u00a0years between 1999 and 2020 and was 12\u00a0years lower in NH Black (56\u00a0years) versus NH White (68\u00a0years) males in 2010\u20132020. There were 930 females with rHD, with an age\u2010adjusted rate of 0.22 per 1 million females, which was consistent between 1999 and 2020.<\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec>\n                    <jats:title>Conclusion<\/jats:title>\n                    <jats:p>Reported haemophilia\u2010death rates improved in males across all race\/ethnicities, but rates were higher Black versus White males. Given the inherent limitations of the current study's data source, further investigation of survival rates and disparities in haemophilia are needed.<\/jats:p>\n                  <\/jats:sec>","DOI":"10.1111\/hae.14859","type":"journal-article","created":{"date-parts":[[2023,9,18]],"date-time":"2023-09-18T02:43:47Z","timestamp":1695005027000},"page":"1410-1418","update-policy":"https:\/\/doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":9,"title":["Racial and ethnic differences in reported haemophilia death rates in the United States"],"prefix":"10.1111","volume":"29","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-3624-6382","authenticated-orcid":false,"given":"Stacey A.","family":"Fedewa","sequence":"first","affiliation":[{"name":"Department of Hematology and Medical Oncology Emory University School of Medicine  Atlanta Georgia USA"},{"name":"Hemophilia of Georgia Center for Bleeding &amp; Clotting Disorders of Emory Emory University School of Medicine  Atlanta Georgia USA"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-1027-7639","authenticated-orcid":false,"given":"Amanda B.","family":"Payne","sequence":"additional","affiliation":[{"name":"National Centers for Birth Defects and Developmental Disabilities Division of Blood Disorders Centers for Disease Control and Prevention  Atlanta Georgia USA"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Duc","family":"Tran","sequence":"additional","affiliation":[{"name":"Department of Hematology and Medical Oncology Emory University School of Medicine  Atlanta Georgia USA"},{"name":"Hemophilia of Georgia Center for Bleeding &amp; Clotting Disorders of Emory Emory University School of Medicine  Atlanta Georgia USA"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Lorraine","family":"Cafuir","sequence":"additional","affiliation":[{"name":"Department of Hematology and Medical Oncology Emory University School of Medicine  Atlanta Georgia USA"},{"name":"Hemophilia of Georgia Center for Bleeding &amp; Clotting Disorders of Emory Emory University School of Medicine  Atlanta Georgia USA"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Ana","family":"Antun","sequence":"additional","affiliation":[{"name":"Department of Hematology and Medical Oncology Emory University School of Medicine  Atlanta Georgia USA"},{"name":"Hemophilia of Georgia Center for Bleeding &amp; Clotting Disorders of Emory Emory University School of Medicine  Atlanta Georgia USA"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-2391-2016","authenticated-orcid":false,"given":"Christine L.","family":"Kempton","sequence":"additional","affiliation":[{"name":"Department of Hematology and Medical Oncology Emory University School of Medicine  Atlanta Georgia USA"},{"name":"Hemophilia of Georgia Center for Bleeding &amp; Clotting Disorders of Emory Emory University School of Medicine  Atlanta Georgia USA"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"311","published-online":{"date-parts":[[2023,9,17]]},"reference":[{"key":"e_1_2_9_2_1","doi-asserted-by":"publisher","DOI":"10.1111\/jth.15182"},{"key":"e_1_2_9_3_1","doi-asserted-by":"publisher","DOI":"10.1002\/ajh.1050"},{"key":"e_1_2_9_4_1","doi-asserted-by":"publisher","DOI":"10.1097\/01.qai.0000179459.31562.16"},{"key":"e_1_2_9_5_1","doi-asserted-by":"publisher","DOI":"10.1111\/jth.15189"},{"issue":"8","key":"e_1_2_9_6_1","first-page":"1","article-title":"Mortality Trends and Causes of Death in Persons with Hemophilia in the United States, 1999\u20132014","author":"Payne AB","year":"2017","journal-title":"Blood"},{"key":"e_1_2_9_7_1","unstructured":"Centers for Disease Control and Prevention. 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