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Although corticosteroids for AIH and ursodeoxycholic acid for PBC have been shown to significantly improve liver transplantation (LT)\u2010free survival and are recommended as first\u2010line drugs, treatment strategies for patients who show incomplete response to these drugs have not yet been fully established. No drug is significantly associated with long LT\u2010free survival in PSC patients. Nevertheless, with progress in genetics, immunology, and cellular biology, several new compounds or antibodies are expected to have an effect on autoimmune liver diseases and several drugs are under consideration for clinical use. Although most clinical trials have been carried out in the USA or Europe, some are, or will be, undertaken in Japan in the future. In this review, the current standard\u2010of\u2010care of autoimmune liver diseases will be summarized, together with emerging novel treatments relevant to clinical practice in Japan.<\/jats:p>","DOI":"10.1111\/hepr.13347","type":"journal-article","created":{"date-parts":[[2019,4,10]],"date-time":"2019-04-10T09:58:45Z","timestamp":1554890325000},"page":"489-499","update-policy":"https:\/\/doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":19,"title":["Emerging novel treatments for autoimmune liver diseases"],"prefix":"10.1111","volume":"49","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-6358-5283","authenticated-orcid":false,"given":"Atsushi","family":"Tanaka","sequence":"first","affiliation":[{"name":"School of Medicine Teikyo University  Tokyo 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