{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,5,21]],"date-time":"2026-05-21T12:36:58Z","timestamp":1779367018282,"version":"3.53.0"},"reference-count":29,"publisher":"Hindawi Limited","issue":"3","license":[{"start":{"date-parts":[[2015,9,1]],"date-time":"2015-09-01T00:00:00Z","timestamp":1441065600000},"content-version":"tdm","delay-in-days":0,"URL":"http:\/\/doi.wiley.com\/10.1002\/tdm_license_1.1"}],"funder":[{"name":"Special Trustees of Chelsea & Westminster Hospital, London"}],"content-domain":{"domain":["wiley.com"],"crossmark-restriction":true},"short-container-title":["Int J Clin Pract"],"published-print":{"date-parts":[[2016,3]]},"DOI":"10.1111\/ijcp.12770","type":"journal-article","created":{"date-parts":[[2016,1,22]],"date-time":"2016-01-22T14:05:31Z","timestamp":1453471531000},"page":"229-235","update-policy":"https:\/\/doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":10,"title":["Safety of long-term restrictive diets for peroxisomal disorders: vitamin and trace element status of patients treated for Adult Refsum Disease"],"prefix":"10.1155","volume":"70","author":[{"given":"E. J.","family":"Baldwin","sequence":"first","affiliation":[{"name":"Adult Refsum Disease Clinic; Chelsea & Westminster Hospital; London UK"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"D. J.","family":"Harrington","sequence":"additional","affiliation":[{"name":"Nutristasis Unit; Viapath, Guy's & St Thomas' Hospitals; London UK"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"B.","family":"Sampson","sequence":"additional","affiliation":[{"name":"Trace Element Laboratory; Imperial College Healthcare; Charing Cross Hospital; London UK"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"M. D.","family":"Feher","sequence":"additional","affiliation":[{"name":"Adult Refsum Disease Clinic; Chelsea & Westminster Hospital; London UK"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"A. S.","family":"Wierzbicki","sequence":"additional","affiliation":[{"name":"Adult Refsum Disease Clinic; Chelsea & Westminster Hospital; London UK"},{"name":"Department of Metabolic Medicine\/Chemical Pathology; Guy's & St Thomas' Hospitals; London UK"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"98","published-online":{"date-parts":[[2016,1,22]]},"reference":[{"key":"10.1111\/ijcp.12770-BIB0001|ijcp12770-cit-0001","doi-asserted-by":"crossref","first-page":"727","DOI":"10.1046\/j.0022-3042.2002.00766.x","article-title":"Refsum's disease: a peroxisomal disorder affecting phytanic acid alpha-oxidation","volume":"80","author":"Wierzbicki","year":"2002","journal-title":"J Neurochem"},{"key":"10.1111\/ijcp.12770-BIB0002|ijcp12770-cit-0002","doi-asserted-by":"crossref","first-page":"498","DOI":"10.1016\/j.bbalip.2011.06.006","article-title":"Phytanic acid metabolism in health and disease","volume":"1811","author":"Wanders","year":"2011","journal-title":"Biochim Biophys Acta"},{"key":"10.1111\/ijcp.12770-BIB0003|ijcp12770-cit-0003","doi-asserted-by":"crossref","first-page":"471","DOI":"10.1086\/346093","article-title":"Identification of PEX7 as the Second Gene Involved in Refsum Disease","volume":"72","author":"van den Brink","year":"2003","journal-title":"Am J Hum Genet"},{"key":"10.1111\/ijcp.12770-BIB0004|ijcp12770-cit-0004","doi-asserted-by":"crossref","first-page":"1553","DOI":"10.1007\/s00018-005-5603-4","article-title":"Thiamine pyrophosphate: an essential cofactor for the alpha-oxidation in mammals-implications for thiamine deficiencies?","volume":"63","author":"Sniekers","year":"2006","journal-title":"Cell Mol Life Sci"},{"key":"10.1111\/ijcp.12770-BIB0005|ijcp12770-cit-0005","doi-asserted-by":"crossref","first-page":"10","DOI":"10.1186\/1471-2091-8-10","article-title":"Presence of thiamine pyrophosphate in mammalian peroxisomes","volume":"8","author":"Fraccascia","year":"2007","journal-title":"BMC Biochem"},{"key":"10.1111\/ijcp.12770-BIB0006|ijcp12770-cit-0006","doi-asserted-by":"crossref","first-page":"1752","DOI":"10.1007\/s00018-005-5463-y","article-title":"Phytanic acid: production from phytol, its breakdown and role in human disease","volume":"63","author":"van den Brink","year":"2006","journal-title":"Cell Mol Life Sci"},{"key":"10.1111\/ijcp.12770-BIB0007|ijcp12770-cit-0007","doi-asserted-by":"crossref","first-page":"1481","DOI":"10.1194\/jlr.M300121-JLR200","article-title":"Metabolism of phytanic acid and 3-methyl-adipic acid excretion in patients with adult Refsum disease","volume":"44","author":"Wierzbicki","year":"2003","journal-title":"J Lipid Res"},{"key":"10.1111\/ijcp.12770-BIB0008|ijcp12770-cit-0008","doi-asserted-by":"crossref","first-page":"295","DOI":"10.1111\/j.1365-277X.1993.tb00375.x","article-title":"Diet and Refsum's disease. The determination of phytanic acid and phytol in certain foods and application of this knowledge to the choice of suitable convenience foods for patients with Refsum's disease","volume":"6","author":"Brown","year":"1993","journal-title":"J Human Nutr Diet"},{"key":"10.1111\/ijcp.12770-BIB0009|ijcp12770-cit-0009","volume-title":"McCance and Widdowson's The Composition of Foods","author":"Finglas","year":"2014","edition":"7"},{"key":"10.1111\/ijcp.12770-BIB0010|ijcp12770-cit-0010","doi-asserted-by":"crossref","first-page":"1133","DOI":"10.1079\/PHN2005801","article-title":"Basal metabolic rate studies in humans: measurement and development of new equations","volume":"8","author":"Henry","year":"2005","journal-title":"Public Health Nutr"},{"key":"10.1111\/ijcp.12770-BIB0011|ijcp12770-cit-0011","doi-asserted-by":"crossref","first-page":"146","DOI":"10.1093\/ije\/26.1.146","article-title":"Who are the \u2018low energy reporters\u2019 in the dietary and nutritional survey of British adults?","volume":"26","author":"Pryer","year":"1997","journal-title":"Int J Epidemiol"},{"key":"10.1111\/ijcp.12770-BIB0012|ijcp12770-cit-0012","doi-asserted-by":"crossref","first-page":"271","DOI":"10.1079\/BJN2000253","article-title":"A perspective on food energy standards for nutrition labellling","volume":"85","author":"Livesey","year":"2001","journal-title":"Br J Nutr"},{"key":"10.1111\/ijcp.12770-BIB0013|ijcp12770-cit-0013","doi-asserted-by":"crossref","first-page":"1649","DOI":"10.1093\/ajcn\/86.6.1649","article-title":"Accuracy of the Atwater factors and related food energy conversion factors with low-fat, high-fiber diets when energy intake is reduced spontaneously","volume":"86","author":"Zou","year":"2007","journal-title":"Am J Clin Nutr"},{"key":"10.1111\/ijcp.12770-BIB0014|ijcp12770-cit-0014","volume-title":"Dietary Reference Values for Food Energy and Nutrients for the United Kingdom","author":"Department of Health","year":"1991"},{"issue":"Suppl. 1","key":"10.1111\/ijcp.12770-BIB0015|ijcp12770-cit-0015","doi-asserted-by":"crossref","first-page":"S6","DOI":"10.1038\/ejcn.2008.60","article-title":"Nutrition in advanced age: dietary assessment in the Newcastle 85 + study","volume":"63","author":"Adamson","year":"2009","journal-title":"Eur J Clin Nutr"},{"key":"10.1111\/ijcp.12770-BIB0016|ijcp12770-cit-0016","doi-asserted-by":"crossref","first-page":"1286","DOI":"10.1093\/jn\/137.5.1286","article-title":"High levels of low energy reporting on 24-hour recalls and three questionnaires in an elderly low-socioeconomic status population","volume":"137","author":"Tooze","year":"2007","journal-title":"J Nutr"},{"key":"10.1111\/ijcp.12770-BIB0017|ijcp12770-cit-0017","doi-asserted-by":"crossref","first-page":"160","DOI":"10.1007\/s00394-004-0454-6","article-title":"Validation of a food frequency questionnaire to assess macro- and micro-nutrient intake among South Asians in the United Kingdom","volume":"43","author":"Sevak","year":"2004","journal-title":"Eur J Nutr"},{"key":"10.1111\/ijcp.12770-BIB0018|ijcp12770-cit-0018","doi-asserted-by":"crossref","first-page":"408","DOI":"10.1016\/S0076-6879(97)82124-6","article-title":"Determination of vitamin K compounds in plasma or serum by high-performance liquid chromatography using postcolumn chemical reduction and fluorimetric detection","volume":"282","author":"Davidson","year":"1997","journal-title":"Methods Enzymol"},{"key":"10.1111\/ijcp.12770-BIB0019|ijcp12770-cit-0019","doi-asserted-by":"crossref","first-page":"213","DOI":"10.1080\/15321819508013559","article-title":"Production of a new monoclonal antibody specific to human des-gamma-carboxyprothrombin in the presence of calcium ions. Application to the development of a sensitive ELISA-test","volume":"16","author":"Belle","year":"1995","journal-title":"J Immunoassay"},{"key":"10.1111\/ijcp.12770-BIB0020|ijcp12770-cit-0020","doi-asserted-by":"crossref","first-page":"423","DOI":"10.1373\/clinchem.2003.026955","article-title":"Determination of folate vitamers in human serum by stable-isotope-dilution tandem mass spectrometry and comparison with radioassay and microbiologic assay","volume":"50","author":"Pfeiffer","year":"2004","journal-title":"Clin Chem"},{"key":"10.1111\/ijcp.12770-BIB0021|ijcp12770-cit-0021","doi-asserted-by":"crossref","first-page":"60","DOI":"10.1136\/jcp.2007.055111","article-title":"The copper\/caeruloplasmin ratio in routine clinical practice in different laboratories","volume":"62","author":"Twomey","year":"2009","journal-title":"J Clin Pathol"},{"key":"10.1111\/ijcp.12770-BIB0022|ijcp12770-cit-0022","doi-asserted-by":"crossref","first-page":"954","DOI":"10.1136\/jnnp.2008.161059","article-title":"The effectiveness of long-term dietary therapy in the treatment of adult Refsum disease","volume":"81","author":"Baldwin","year":"2010","journal-title":"J Neurol Neurosurg Psychiatry"},{"key":"10.1111\/ijcp.12770-BIB0023|ijcp12770-cit-0023","doi-asserted-by":"crossref","first-page":"266","DOI":"10.1093\/ajcn\/68.2.266","article-title":"Under- and overreporting of energy intake related to weight status and lifestyle in a nationwide sample","volume":"68","author":"Johansson","year":"1998","journal-title":"Am J Clin Nutr"},{"key":"10.1111\/ijcp.12770-BIB0024|ijcp12770-cit-0024","doi-asserted-by":"crossref","first-page":"199","DOI":"10.1079\/PHN19980031","article-title":"Validation with biological markers for food intake of a dietary assessment method used by Swedish women with three different dietary preferences","volume":"1","author":"Johansson","year":"1998","journal-title":"Public Health Nutr"},{"key":"10.1111\/ijcp.12770-BIB0025|ijcp12770-cit-0025","doi-asserted-by":"crossref","first-page":"281","DOI":"10.1016\/S1096-7192(03)00108-2","article-title":"Evidence for increased oxidative stress in peroxisomal D-bifunctional protein deficiency","volume":"79","author":"Ferdinandusse","year":"2003","journal-title":"Mol Genet Metab"},{"key":"10.1111\/ijcp.12770-BIB0026|ijcp12770-cit-0026","doi-asserted-by":"crossref","first-page":"1590","DOI":"10.1002\/mnfr.201300683","article-title":"Vitamin K metabolism: current knowledge and future research","volume":"58","author":"Card","year":"2014","journal-title":"Mol Nutr Food Res"},{"key":"10.1111\/ijcp.12770-BIB0027|ijcp12770-cit-0027","doi-asserted-by":"crossref","first-page":"G939","DOI":"10.1152\/ajpgi.00308.2006","article-title":"Effect of SCP-x gene ablation on branched-chain fatty acid metabolism","volume":"292","author":"Atshaves","year":"2007","journal-title":"Am J Physiol Gastrointest Liver Physiol"},{"key":"10.1111\/ijcp.12770-BIB0028|ijcp12770-cit-0028","doi-asserted-by":"crossref","first-page":"224","DOI":"10.1016\/j.ymgme.2004.04.010","article-title":"Hyperpipecolic acidaemia: a diagnostic tool for peroxisomal disorders","volume":"82","author":"Peduto","year":"2004","journal-title":"Mol Genet Metab"},{"key":"10.1111\/ijcp.12770-BIB0029|ijcp12770-cit-0029","doi-asserted-by":"crossref","first-page":"714","DOI":"10.1046\/j.1365-2362.2001.00877.x","article-title":"Fibroblast studies documenting a case of peroxisomal 2-methylacyl-CoA racemase deficiency: possible link between racemase deficiency and malabsorption and vitamin K deficiency","volume":"31","author":"Van Veldhoven","year":"2001","journal-title":"Eur J Clin Invest"}],"container-title":["International Journal of Clinical Practice"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.wiley.com\/onlinelibrary\/tdm\/v1\/articles\/10.1111%2Fijcp.12770","content-type":"unspecified","content-version":"vor","intended-application":"text-mining"}],"deposited":{"date-parts":[[2022,1,28]],"date-time":"2022-01-28T06:09:18Z","timestamp":1643350158000},"score":1,"resource":{"primary":{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/10.1111\/ijcp.12770"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2016,1,22]]},"references-count":29,"journal-issue":{"issue":"3","published-print":{"date-parts":[[2016,3]]}},"URL":"https:\/\/doi.org\/10.1111\/ijcp.12770","archive":["Portico"],"relation":{},"ISSN":["1368-5031"],"issn-type":[{"value":"1368-5031","type":"print"}],"subject":[],"published":{"date-parts":[[2016,1,22]]}}}