{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,8,23]],"date-time":"2026-08-23T18:27:37Z","timestamp":1787509657663,"version":"build-2736575974"},"reference-count":26,"publisher":"Wiley","issue":"2","license":[{"start":{"date-parts":[[2014,2,17]],"date-time":"2014-02-17T00:00:00Z","timestamp":1392595200000},"content-version":"vor","delay-in-days":16,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"funder":[{"name":"The Australia and New Zealand Congenital Heart Research Centre"},{"name":"ANZ Bank Trustees"},{"name":"The National Health and Medical Research Council"},{"name":"Heart Foundation of Australia Career Development Fellowship","award":["CR 10M 5339"],"award-info":[{"award-number":["CR 10M 5339"]}]},{"name":"Australian National Health and Medical Research Council","award":["APP1012241"],"award-info":[{"award-number":["APP1012241"]}]},{"name":"Murdoch Childrens Research Institute"},{"name":"National Health and Medical Research Council and Heart Foundation of Australia","award":["APP1038802"],"award-info":[{"award-number":["APP1038802"]}]},{"DOI":"10.13039\/100011371","name":"Royal Australasian College of Surgeons","doi-asserted-by":"crossref","id":[{"id":"10.13039\/100011371","id-type":"DOI","asserted-by":"crossref"}]}],"content-domain":{"domain":["onlinelibrary.wiley.com"],"crossmark-restriction":true},"short-container-title":["Internal Medicine Journal"],"published-print":{"date-parts":[[2014,2]]},"abstract":"<jats:title>Abstract<\/jats:title>\n                  <jats:sec>\n                    <jats:title>Background<\/jats:title>\n                    <jats:p>\n                      The\n                      <jats:styled-content style=\"fixed-case\">F<\/jats:styled-content>\n                      ontan procedure is the final in a series of staged palliations for single\u2010ventricle congenital heart disease, which encompasses rare and heterogeneous cardiac lesions. It represents an unusual and novel physiological state characterised by absence of a subpulmonary ventricle.\n                    <\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec>\n                    <jats:title>Aims<\/jats:title>\n                    <jats:p>The population is growing steadily, prompting creation of this registry to study their epidemiology, demographic trends, treatment and outcomes.<\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec>\n                    <jats:title>Methods<\/jats:title>\n                    <jats:p>\n                      This multicentre, binational, prospective and retrospective, web\u2010based registry involving all congenital cardiac centres in the region has identified nearly all\n                      <jats:styled-content style=\"fixed-case\">F<\/jats:styled-content>\n                      ontan patients in\n                      <jats:styled-content style=\"fixed-case\">A<\/jats:styled-content>\n                      ustralia and\n                      <jats:styled-content style=\"fixed-case\">N<\/jats:styled-content>\n                      ew\n                      <jats:styled-content style=\"fixed-case\">Z<\/jats:styled-content>\n                      ealand. Patients identified retrospectively were approached for recruitment. New recipients are automatically enrolled prospectively unless they choose to opt\u2010out. Follow\u2010up data are collected yearly.\n                    <\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec>\n                    <jats:title>Results<\/jats:title>\n                    <jats:p>\n                      Baseline data were obtained in 1072 patients as at 1\n                      <jats:styled-content style=\"fixed-case\">J<\/jats:styled-content>\n                      anuary 2011. Ninety\u2010nine patients died; 64 were lost to follow up. Forty\u2010four per cent of patients lost were between 20 and 30 years of age. The size of the\n                      <jats:styled-content style=\"fixed-case\">F<\/jats:styled-content>\n                      ontan population is increasing steadily. Among 973 living patients, 541 (56%) gave consent for prospective collection of follow up. Between 1\n                      <jats:styled-content style=\"fixed-case\">J<\/jats:styled-content>\n                      anuary 2011 and 1\n                      <jats:styled-content style=\"fixed-case\">J<\/jats:styled-content>\n                      anuary 2013, an additional 47 subjects were enrolled prospectively. The current proportion of patients operated with hypoplastic left heart syndrome is currently 29% and is growing rapidly.\n                    <\/jats:p>\n                  <\/jats:sec>\n                  <jats:sec>\n                    <jats:title>Conclusion<\/jats:title>\n                    <jats:p>\n                      The population surviving after the\n                      <jats:styled-content style=\"fixed-case\">F<\/jats:styled-content>\n                      ontan procedure has been growing in recent decades, especially since survival with hypoplastic left heart syndrome has improved. The\n                      <jats:styled-content style=\"fixed-case\">A<\/jats:styled-content>\n                      ustralia and\n                      <jats:styled-content style=\"fixed-case\">N<\/jats:styled-content>\n                      ew\n                      <jats:styled-content style=\"fixed-case\">Z<\/jats:styled-content>\n                      ealand\n                      <jats:styled-content style=\"fixed-case\">F<\/jats:styled-content>\n                      ontan\n                      <jats:styled-content style=\"fixed-case\">R<\/jats:styled-content>\n                      egistry provides population\u2010based data, and only large databases like this will give opportunities for understanding the population and performing prospective trials.\n                    <\/jats:p>\n                  <\/jats:sec>","DOI":"10.1111\/imj.12318","type":"journal-article","created":{"date-parts":[[2013,11,7]],"date-time":"2013-11-07T07:21:27Z","timestamp":1383808887000},"page":"148-155","update-policy":"https:\/\/doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":105,"title":["<scp>T<\/scp>\n                    he\n                    <scp>A<\/scp>\n                    ustralia and\n                    <scp>N<\/scp>\n                    ew\n                    <scp>Z<\/scp>\n                    ealand\n                    <scp>F<\/scp>\n                    ontan\n                    <scp>R<\/scp>\n                    egistry: description and initial results from the first population\u2010based\n                    <scp>F<\/scp>\n                    ontan registry"],"prefix":"10.1111","volume":"44","author":[{"given":"A. J.","family":"Iyengar","sequence":"first","affiliation":[{"name":"Department of Cardiac Surgery Royal Children's Hospital  Melbourne Victoria Australia"},{"name":"Heart Research Group Murdoch Children's Research Institute  Melbourne Victoria Australia"},{"name":"Department of Paediatrics University of Melbourne  Melbourne Victoria Australia"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"D. S.","family":"Winlaw","sequence":"additional","affiliation":[{"name":"Heart Centre for Children The Children's Hospital at Westmead  Sydney New South Wales Australia"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"J. C.","family":"Galati","sequence":"additional","affiliation":[{"name":"Heart Research Group Murdoch Children's Research Institute  Melbourne Victoria Australia"},{"name":"Clinical Epidemiology and Biostatistics Unit Murdoch Children's Research Institute  Melbourne Victoria Australia"},{"name":"Department of Mathematics and Statistics La Trobe University  Melbourne Victoria Australia"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"T. L.","family":"Gentles","sequence":"additional","affiliation":[{"name":"Green Lane Congenital Cardiac Service Starship Children's Hospital  Auckland New Zealand"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"R. G.","family":"Weintraub","sequence":"additional","affiliation":[{"name":"Department of Cardiology Royal Children's Hospital  Melbourne Victoria Australia"},{"name":"Heart Research Group Murdoch Children's Research Institute  Melbourne Victoria Australia"},{"name":"Department of Paediatrics University of Melbourne  Melbourne Victoria Australia"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"R. N.","family":"Justo","sequence":"additional","affiliation":[{"name":"Paediatric Cardiology Queensland Paediatric Cardiac Service Mater Children's Hospital  Brisbane Queensland Australia"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"G. R.","family":"Wheaton","sequence":"additional","affiliation":[{"name":"Department of Cardiology Women's and Children's Hospital  Adelaide South Australia Australia"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"A.","family":"Bullock","sequence":"additional","affiliation":[{"name":"Children's Cardiac Centre Princess Margaret Hospital for Children  Perth Western Australia Australia"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"D. 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