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Consulted sources, ranging from 1970 to 2010, included MEDLINE, EMBASE, CINAHL, The Cochrane Library, DARE, and the Cochrane controlled trials register (CENTRAL). In order to formulate the recommendations of the selected studies the SIGN system was used. The first draft was analysed and discussed by clinical experts, methodologists and patients representatives on a two days consensus meeting. The resulting document went through an external review process by a panel of experts, other health care professionals, patient representatives and lay reviewers. The final document was piloted in three different centres in United Kingdom, Czech Republic and Argentina.<\/jats:p><jats:p><jats:bold>Results.\u2002<\/jats:bold> The guideline is composed of 93 recommendations divided into 3 main areas: 1) Oral Care \u2010 access issues, early referral, preventative strategies, management of microstomia, prescriptions and review appointments\u2010, 2) Dental treatment: general treatment modifications, radiographs, restorations, endodontics, oral rehabilitation, periodontal treatment, oral surgery and orthodontics\u2010, and 3) Anaesthetic management of dental treatment.<\/jats:p><jats:p><jats:bold>Conclusions.\u2002<\/jats:bold> A preventive protocol is today's dental management approach of choice.<\/jats:p>","DOI":"10.1111\/j.1365-263x.2012.01247.x","type":"journal-article","created":{"date-parts":[[2012,9,3]],"date-time":"2012-09-03T09:16:48Z","timestamp":1346663808000},"page":"1-35","update-policy":"https:\/\/doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":55,"title":["Oral Health Care for Patients with Epidermolysis Bullosa \u2010 Best Clinical Practice Guidelines"],"prefix":"10.1111","volume":"22","author":[{"given":"Susanne M.","family":"Kr\u00e4mer","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Mar\u00eda Concepci\u00f3n","family":"Serrano","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Gisela","family":"Zillmann","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Pablo","family":"G\u00e1lvez","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Ignacio","family":"Araya","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Nicol\u00e1s","family":"Yanine","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Alonso","family":"Carrasco\u2010Labra","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Patricio","family":"Oliva","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Romina","family":"Brignardello\u2010Petersen","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Julio","family":"Villanueva","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"311","published-online":{"date-parts":[[2012,9,3]]},"reference":[{"key":"e_1_2_10_2_2","doi-asserted-by":"publisher","DOI":"10.1016\/j.joms.2007.06.672"},{"key":"e_1_2_10_3_2","unstructured":"SkogedalN SaltnesS StorhaugK.Recessive dystrophic epidermolysis bullosa (RDEB) Caries prevention and preventive extractions of molars. 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