{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,9,20]],"date-time":"2026-09-20T10:09:32Z","timestamp":1789898972183,"version":"4.0.1"},"reference-count":13,"publisher":"Wiley","issue":"3","license":[{"start":{"date-parts":[[2011,11,9]],"date-time":"2011-11-09T00:00:00Z","timestamp":1320796800000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Clinical Transplantation"],"published-print":{"date-parts":[[2012,5]]},"abstract":"Maheshwari A, Rankin R, Segev DL, Thuluvath PJ. Outcomes of liver transplantation for glycogen storage disease: a matched\u2010control study and a review of literature. \u2028Clin Transplant 2011 DOI: 10.1111\/j.1399\u20100012.2011.01549.x. \u2028\u00a9 2011 John Wiley & Sons A\/S.<\/jats:p>\n \n Abstract:\u2002<\/jats:bold>\n Background:\u2002<\/jats:bold>\n The clinical characteristics and outcomes of patients with glycogen storage disease (GSD) who undergo liver transplantation (LT) have not been well defined. In this study, our objective was to determine the outcome of LT in patients with GSD and compare it with a comparable group of patients without GSD (matched controls).\n <\/jats:p>\n \n Methods:\u2002<\/jats:bold>\n UNOS data from 1986 to 2007 were used for this study. For each GSD patient (n\u2003=\u200395; men 62%) who was transplanted, three patients (n\u2003=\u2003285, men 60%) without GSD (case controls) matched for age\u2003\u00b1\u2003five\u2003yr, year of transplantation and donor risk index (DRI)\u2003\u00b1\u20030.2 were identified from the UNOS database in a random manner. Unadjusted patient survival was determined by Kaplan\u2013Meier survival analysis and significance determined by log\u2010rank test.\n <\/jats:p>\n \n Results:\u2002<\/jats:bold>\n The mean age of the group was 17.9\u2003yr. GSD patients had lower BMI (22 vs. 24, p\u2003=\u20030.002), lower serum bilirubin (2.7 vs. 13.5\u2003mg\/dL, p\u2003<\u20030.0001), higher serum albumin (3.7 vs. 3.1\u2003g\/dL, p\u2003<\u20030.0001), and higher wait\u2010list time (239 vs. 74\u2003d, p\u2003<\u20030.0001) compared to case controls. Recipient age and DRI were similar between the groups. Tumors were more common in GSD group (13.7% vs. 5%). Patient survival was significantly better (p\u2003=\u20030.024) in GSD group at one, five, and 10\u2003yr (82%, 76%, and 64%) than non\u2010GSD (73%, 65%, and 59%) group.\n <\/jats:p>\n \n Conclusions:\u2002<\/jats:bold>\n In this matched\u2010control study, patients who underwent LT for GSD had a better long\u2010term survival than a comparable group of patients without GSD.\n <\/jats:p>","DOI":"10.1111\/j.1399-0012.2011.01549.x","type":"journal-article","created":{"date-parts":[[2011,11,9]],"date-time":"2011-11-09T04:21:53Z","timestamp":1320812513000},"page":"432-436","source":"Crossref","is-referenced-by-count":27,"title":["Outcomes of liver transplantation for glycogen storage disease: a matched\u2010control study and a review of literature"],"prefix":"10.1111","volume":"26","author":[{"given":"Anurag","family":"Maheshwari","sequence":"first","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Rebecca","family":"Rankin","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Dorry L.","family":"Segev","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Paul J.","family":"Thuluvath","sequence":"additional","affiliation":[],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"311","published-online":{"date-parts":[[2011,11,9]]},"reference":[{"key":"e_1_2_5_2_2","doi-asserted-by":"publisher","DOI":"10.1007\/BF02680007"},{"key":"e_1_2_5_3_2","doi-asserted-by":"publisher","DOI":"10.1111\/j.1600-6143.2006.01242.x"},{"key":"e_1_2_5_4_2","doi-asserted-by":"publisher","DOI":"10.1023\/B:BOLI.0000037400.49488.20"},{"key":"e_1_2_5_5_2","doi-asserted-by":"publisher","DOI":"10.1007\/PL00014320"},{"key":"e_1_2_5_6_2","doi-asserted-by":"publisher","DOI":"10.1002\/lt.21151"},{"key":"e_1_2_5_7_2","doi-asserted-by":"publisher","DOI":"10.1111\/j.1600-6143.2005.01084.x"},{"key":"e_1_2_5_8_2","doi-asserted-by":"publisher","DOI":"10.1016\/S0041-1345(02)03951-9"},{"key":"e_1_2_5_9_2","doi-asserted-by":"publisher","DOI":"10.1111\/j.1399-3046.2007.00803.x"},{"key":"e_1_2_5_10_2","doi-asserted-by":"publisher","DOI":"10.1111\/j.1432-2277.2003.tb00258.x"},{"key":"e_1_2_5_11_2","doi-asserted-by":"publisher","DOI":"10.1016\/j.jhep.2006.09.022"},{"key":"e_1_2_5_12_2","doi-asserted-by":"publisher","DOI":"10.1016\/j.jhep.2007.05.012"},{"key":"e_1_2_5_13_2","doi-asserted-by":"publisher","DOI":"10.1097\/00005176-199703000-00008"},{"key":"e_1_2_5_14_2","doi-asserted-by":"publisher","DOI":"10.1007\/s10545-005-7500-2"}],"container-title":["Clinical Transplantation"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.wiley.com\/onlinelibrary\/tdm\/v1\/articles\/10.1111%2Fj.1399-0012.2011.01549.x","content-type":"unspecified","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/pdf\/10.1111\/j.1399-0012.2011.01549.x","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2023,10,31]],"date-time":"2023-10-31T09:38:26Z","timestamp":1698745106000},"score":1,"resource":{"primary":{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/10.1111\/j.1399-0012.2011.01549.x"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2011,11,9]]},"references-count":13,"journal-issue":{"issue":"3","published-print":{"date-parts":[[2012,5]]}},"alternative-id":["10.1111\/j.1399-0012.2011.01549.x"],"URL":"https:\/\/doi.org\/10.1111\/j.1399-0012.2011.01549.x","archive":["Portico"],"relation":{},"ISSN":["0902-0063","1399-0012"],"issn-type":[{"value":"0902-0063","type":"print"},{"value":"1399-0012","type":"electronic"}],"subject":[],"published":{"date-parts":[[2011,11,9]]}}}