{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,5,5]],"date-time":"2026-05-05T12:22:58Z","timestamp":1777983778633,"version":"3.51.4"},"reference-count":19,"publisher":"Wiley","issue":"8","license":[{"start":{"date-parts":[[2012,3,27]],"date-time":"2012-03-27T00:00:00Z","timestamp":1332806400000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Pediatric Transplantation"],"published-print":{"date-parts":[[2012,12]]},"abstract":"<jats:p>Gomes AC, Rubino G, Pinto C, Cipriano A, Furtado E, Gon\u00e7alves I. Budd\u2013Chiari syndrome in children and outcome after liver transplant.<\/jats:p><jats:p><jats:bold>Abstract:\u2002<\/jats:bold> BCS is a rare form of portal hypertension in children. The authors describe two cases of BCS with differing presentations. <jats:italic>Case 1<\/jats:italic>: Previously healthy four\u2010yr\u2010old girl. BCS was diagnosed during the course of an episode of acute gastroenteritis with dehydration. Despite conservative therapy for two\u2003months, the condition was progressive resulting in liver failure leading ultimately to LT. Molecular studies showed that she was heterozygous for the Factor (F) V Leiden. At follow\u2010up, six\u2003yr post\u2010LT (two\u2003yr without anticoagulation therapy), no thromboembolic\/bleeding events were apparent. <jats:italic>Case 2<\/jats:italic>: Three\u2010yr\u2010old boy with IgA deficiency and liver disease. Following a febrile episode, he developed fulminant liver failure requiring urgent LT from a living donor (father). Molecular studies disclosed MTHFR C677T homozygosity and FV Leiden heterozygosity. The father was homozygous for the MTHFR mutation. Three\u2003months post\u2010LT, persistent graft dysfunction was associated with stenosis of the IVC, which improved upon stent placement. He received dipyridamole and aspirin for five\u2003yr, after which time dipyridamole was discontinued. Evidence is sparse on the follow\u2010up of BCS cases with liver transplant. The authors discuss their findings, particularly the need for long\u2010term anticoagulation.<\/jats:p>","DOI":"10.1111\/j.1399-3046.2012.01683.x","type":"journal-article","created":{"date-parts":[[2012,3,27]],"date-time":"2012-03-27T22:07:23Z","timestamp":1332886043000},"source":"Crossref","is-referenced-by-count":15,"title":["Budd\u2013Chiari syndrome in children and outcome after liver transplant"],"prefix":"10.1111","volume":"16","author":[{"given":"Ana Cristina","family":"Gomes","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Gina","family":"Rubino","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Carla","family":"Pinto","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Augusta","family":"Cipriano","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Emanuel","family":"Furtado","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Isabel","family":"Gon\u00e7alves","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"311","published-online":{"date-parts":[[2012,3,27]]},"reference":[{"key":"e_1_2_7_2_2","doi-asserted-by":"publisher","DOI":"10.1016\/j.cld.2008.10.002"},{"key":"e_1_2_7_3_2","doi-asserted-by":"publisher","DOI":"10.1055\/s-0028-1085094"},{"key":"e_1_2_7_4_2","doi-asserted-by":"publisher","DOI":"10.1002\/hep.22772"},{"key":"e_1_2_7_5_2","doi-asserted-by":"publisher","DOI":"10.1002\/lt.21282"},{"key":"e_1_2_7_6_2","doi-asserted-by":"publisher","DOI":"10.1016\/j.jpedsurg.2006.06.045"},{"key":"e_1_2_7_7_2","doi-asserted-by":"publisher","DOI":"10.1016\/j.jpeds.2004.10.036"},{"key":"e_1_2_7_8_2","doi-asserted-by":"publisher","DOI":"10.1038\/ncpgasthep0143"},{"key":"e_1_2_7_9_2","doi-asserted-by":"publisher","DOI":"10.1111\/j.1365-2036.2004.02190.x"},{"key":"e_1_2_7_10_2","doi-asserted-by":"publisher","DOI":"10.1097\/MPG.0b013e3181aecb63"},{"key":"e_1_2_7_11_2","doi-asserted-by":"publisher","DOI":"10.1016\/j.jamcollsurg.2004.03.024"},{"key":"e_1_2_7_12_2","doi-asserted-by":"publisher","DOI":"10.1016\/S1499-3872(11)60042-8"},{"key":"e_1_2_7_13_2","doi-asserted-by":"publisher","DOI":"10.1016\/j.jhep.2005.12.002"},{"key":"e_1_2_7_14_2","doi-asserted-by":"publisher","DOI":"10.1016\/j.transproceed.2003.10.038"},{"key":"e_1_2_7_15_2","doi-asserted-by":"publisher","DOI":"10.1053\/jlts.2000.7575"},{"key":"e_1_2_7_16_2","first-page":"925","article-title":"Acute Budd\u2013Chiari syndrome treated by liver transplantation in a woman homozygous for factor V Leiden","volume":"8","author":"Blanshard C","year":"1996","journal-title":"Eur J Gastroenterol Hepatol"},{"key":"e_1_2_7_17_2","doi-asserted-by":"publisher","DOI":"10.1111\/j.1600-6143.2006.01505.x"},{"key":"e_1_2_7_18_2","doi-asserted-by":"publisher","DOI":"10.1002\/hep.20704"},{"key":"e_1_2_7_19_2","doi-asserted-by":"publisher","DOI":"10.1016\/j.thromres.2010.09.001"},{"key":"e_1_2_7_20_2","doi-asserted-by":"publisher","DOI":"10.1160\/TH11-04-0217"}],"container-title":["Pediatric Transplantation"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.wiley.com\/onlinelibrary\/tdm\/v1\/articles\/10.1111%2Fj.1399-3046.2012.01683.x","content-type":"unspecified","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/pdf\/10.1111\/j.1399-3046.2012.01683.x","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2023,10,30]],"date-time":"2023-10-30T08:36:52Z","timestamp":1698655012000},"score":1,"resource":{"primary":{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/10.1111\/j.1399-3046.2012.01683.x"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2012,3,27]]},"references-count":19,"journal-issue":{"issue":"8","published-print":{"date-parts":[[2012,12]]}},"alternative-id":["10.1111\/j.1399-3046.2012.01683.x"],"URL":"https:\/\/doi.org\/10.1111\/j.1399-3046.2012.01683.x","archive":["Portico"],"relation":{},"ISSN":["1397-3142","1399-3046"],"issn-type":[{"value":"1397-3142","type":"print"},{"value":"1399-3046","type":"electronic"}],"subject":[],"published":{"date-parts":[[2012,3,27]]}}}