{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,1,28]],"date-time":"2026-01-28T21:05:11Z","timestamp":1769634311249,"version":"3.49.0"},"reference-count":9,"publisher":"Wiley","issue":"10","license":[{"start":{"date-parts":[[2006,3,31]],"date-time":"2006-03-31T00:00:00Z","timestamp":1143763200000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Pediatric Anesthesia"],"published-print":{"date-parts":[[2006,10]]},"abstract":"<jats:title>Summary<\/jats:title><jats:p>Patients diagnosed with abdominal pain related to mitochondrial neurogastrointestinal encephalopathy (MNGIE) may benefit from splanchnic nerve blockade. MNGIE, varying in age of onset and rate of progression, is caused by loss of function mutation in thymidine phosphorylase gene. Gastrointestinal dysmotility, pseudo\u2010obstruction and demyelinating sensorimotor peripheral neuropathy (stocking\u2010glove sensory loss, absent tendon reflexes, distal limb weakness, and wasting) are the most prominent manifestations. Patients usually die in early adulthood (mean 37.6\u2003years; range 26\u201358\u2003years). We report a case of an 18\u2010year\u2010old patient with MNGIE. Our patient's abdominal pain was relieved after splanchnic nerve blockade.<\/jats:p>","DOI":"10.1111\/j.1460-9592.2006.01918.x","type":"journal-article","created":{"date-parts":[[2006,3,31]],"date-time":"2006-03-31T12:32:27Z","timestamp":1143808347000},"page":"1073-1076","source":"Crossref","is-referenced-by-count":12,"title":["Abdominal pain related to mitochondrial neurogastrointestinal encephalomyopathy syndrome may benefit from splanchnic nerve blockade"],"prefix":"10.1111","volume":"16","author":[{"given":"NALAN","family":"\u00c7ELEBI","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"ALTAN","family":"\u015eAHIN","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"\u00d6ZG\u00dcR","family":"CANBAY","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"FILIZ","family":"\u00dcZ\u00dcMC\u00dcGIL","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"ULK\u00dc","family":"AYPAR","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"311","published-online":{"date-parts":[[2006,3,31]]},"reference":[{"key":"e_1_2_4_2_2","doi-asserted-by":"publisher","DOI":"10.1002\/1531-8249(200006)47:6<792::AID-ANA12>3.0.CO;2-Y"},{"key":"e_1_2_4_3_2","doi-asserted-by":"publisher","DOI":"10.1002\/mus.10546"},{"key":"e_1_2_4_4_2","doi-asserted-by":"publisher","DOI":"10.1212\/WNL.51.4.1086"},{"key":"e_1_2_4_5_2","doi-asserted-by":"publisher","DOI":"10.1002\/1531-8249(200006)47:6<792::AID-ANA12>3.0.CO;2-Y"},{"key":"e_1_2_4_6_2","doi-asserted-by":"publisher","DOI":"10.1086\/301979"},{"key":"e_1_2_4_7_2","doi-asserted-by":"publisher","DOI":"10.1212\/WNL.44.4.721"},{"key":"e_1_2_4_8_2","doi-asserted-by":"publisher","DOI":"10.1097\/00005176-200209000-00029"},{"key":"e_1_2_4_9_2","volume-title":"Techniques of Regional Anaesthesia","author":"Bruce Scott D.","year":"1989"},{"key":"e_1_2_4_10_2","doi-asserted-by":"publisher","DOI":"10.1016\/S0031-3955(03)00115-9"}],"container-title":["Pediatric Anesthesia"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.wiley.com\/onlinelibrary\/tdm\/v1\/articles\/10.1111%2Fj.1460-9592.2006.01918.x","content-type":"unspecified","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/pdf\/10.1111\/j.1460-9592.2006.01918.x","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2023,10,10]],"date-time":"2023-10-10T10:17:33Z","timestamp":1696933053000},"score":1,"resource":{"primary":{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/10.1111\/j.1460-9592.2006.01918.x"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2006,3,31]]},"references-count":9,"journal-issue":{"issue":"10","published-print":{"date-parts":[[2006,10]]}},"alternative-id":["10.1111\/j.1460-9592.2006.01918.x"],"URL":"https:\/\/doi.org\/10.1111\/j.1460-9592.2006.01918.x","archive":["Portico"],"relation":{},"ISSN":["1155-5645","1460-9592"],"issn-type":[{"value":"1155-5645","type":"print"},{"value":"1460-9592","type":"electronic"}],"subject":[],"published":{"date-parts":[[2006,3,31]]}}}