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Other disorders can present with a similar clinical picture, most commonly corticobasal degeneration and multiple system atrophy. Non\u2010neurodegenerative disorders are rare causes of the PSP syndrome. In this report we describe clinical and pathological features of two cases of Creutzfeldt\u2013Jakob disease (CJD) presenting with the PSP syndrome and discuss which features may help prevent misdiagnosis. To our knowledge, this is the first report of cases of CJD with autopsy confirmation that presented with a PSP syndrome.<\/jats:p>","DOI":"10.1111\/j.1468-1331.2004.00780.x","type":"journal-article","created":{"date-parts":[[2004,5,5]],"date-time":"2004-05-05T15:48:42Z","timestamp":1083772122000},"page":"343-346","update-policy":"https:\/\/doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":38,"title":["Creutzfeldt\u2013Jakob disease presenting as progressive supranuclear palsy"],"prefix":"10.1111","volume":"11","author":[{"given":"K. 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