{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,9,27]],"date-time":"2025-09-27T13:20:18Z","timestamp":1758979218038},"reference-count":23,"publisher":"Wiley","issue":"6","license":[{"start":{"date-parts":[[2004,9,21]],"date-time":"2004-09-21T00:00:00Z","timestamp":1095724800000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Acad Dermatol Venereol"],"published-print":{"date-parts":[[2004,11]]},"abstract":"<jats:title>ABSTRACT<\/jats:title><jats:p><jats:bold>Background\u2002<\/jats:bold> A total of 10\u00a0455 new dermatology patients were seen in the dermatology clinics of King Fahd Hospital of the University (KFHU), Al\u2010Khobar, Eastern Saudi Arabia, between January 1990 and December 1995. We identified 21 patients with a histopathologically confirmed diagnosis of congenital nonbullous ichthyosiform erythroderma (CNBIE). We have reviewed the epidemiological and clinical features of these patients.<\/jats:p><jats:p><jats:bold>Objective\u2002<\/jats:bold> To document the epidemiological and clinical features of patients with CNBIE in eastern Saudi Arabia.<\/jats:p><jats:p><jats:bold>Methods\u2002<\/jats:bold> We used the dermatology outpatient department (OPD) logbooks to identify diagnosed cases of CNBIE from new patients presenting with different dermatological problems over a 6\u2010year period. We used specifically designed data\u2010collection protocol forms to extract epidemiological and clinical data from the patients\u2019 medical records. These were entered into a computer database and analysed using standard statistical software.<\/jats:p><jats:p><jats:bold>Results\u2002<\/jats:bold> A total of 21 patients (five males, 16 females) with a male\u00a0:\u00a0female ratio of 0.31\u00a0:\u00a01 were identified from a total of 10\u00a0455 new patients seen in our dermatology clinics over the study period. The occurrence rate of CNBIE in our clinics was 0.2%, or two per 1000 new dermatology cases. Nineteen\u00a0(90%) of 21 CNBIE patients were born with collodion membranes. Eighty\u2010one per cent of our patients had a positive family history of CNBIE. Consanguinity among the parents of our CNBIE patients was significantly high at 95%.<\/jats:p><jats:p><jats:bold>Conclusions\u2002<\/jats:bold> To the best of our knowledge, this preliminary study is the first report of its kind from Saudi Arabia (documenting the clinico\u2010epidemiological features of CNBIE patients in the Eastern Province). The high rate of parental consanguinity among the parents of our Saudi CNBIE patients may account for the high incidence rate of this genodermatosis in eastern Saudi Arabia. In comparison with results of other studies that reported a low occurrence rate of CNBIE among dermatology patients, our results were of a significantly higher rate.<\/jats:p>","DOI":"10.1111\/j.1468-3083.2004.01042.x","type":"journal-article","created":{"date-parts":[[2004,10,11]],"date-time":"2004-10-11T15:40:55Z","timestamp":1097509255000},"page":"659-664","source":"Crossref","is-referenced-by-count":7,"title":["Clinico\u2010epidemiological features of congenital nonbullous ichthyosiform erythroderma in the eastern province of Saudi Arabia"],"prefix":"10.1111","volume":"18","author":[{"given":"OM","family":"Al\u2010Amro Al\u2010Akloby","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"AA","family":"Al\u2010Zayir","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"311","published-online":{"date-parts":[[2004,9,21]]},"reference":[{"key":"e_1_2_6_2_2","first-page":"1416","volume-title":"Textbook of Dermatology","author":"Ebling FJG","year":"1987"},{"key":"e_1_2_6_3_2","doi-asserted-by":"crossref","first-page":"559","DOI":"10.1001\/archderm.1986.01660170089026","article-title":"A mother and two children with nonbullous congenital ichthyosiform erythroderma","volume":"122","author":"Rossman\u2010Ringdahl I","year":"1986","journal-title":"Arch Dermatol"},{"key":"e_1_2_6_4_2","doi-asserted-by":"crossref","first-page":"240","DOI":"10.1001\/archderm.1970.04000090002002","article-title":"Inherited ichthyoses","volume":"102","author":"Schnyder UW","year":"1970","journal-title":"Arch 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