{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2024,5,13]],"date-time":"2024-05-13T06:29:09Z","timestamp":1715581749394},"reference-count":28,"publisher":"Wiley","issue":"5","license":[{"start":{"date-parts":[[2008,7,8]],"date-time":"2008-07-08T00:00:00Z","timestamp":1215475200000},"content-version":"vor","delay-in-days":68,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Cardiovasc electrophysiol"],"published-print":{"date-parts":[[2008,5]]},"abstract":"<jats:p> <jats:italic>Introduction:<\/jats:italic> Rhythm disturbances in children with structurally normal hearts are usually associated with abnormalities in cardiac ion channels. The phenotypic expression of these abnormalities (\u201cchannelopathies\u201d) includes: long and short QT syndromes, Brugada syndrome, congenital sick sinus syndrome, catecholaminergic polymorphic ventricular tachycardia, L\u00e8negre\u2010Lev disease, and\/or different degrees of cardiac conduction disease.<\/jats:p><jats:p> <jats:italic>Methods:<\/jats:italic> The study group consisted of three male patients with sick sinus syndrome, intraventricular conduction disease, and monomorphic sustained ventricular tachycardia. Clinical data and results of electrocardiography, Holter monitoring, electrophysiology, and echocardiography are described.<\/jats:p><jats:p> <jats:italic>Results:<\/jats:italic> In all patients, the ECG during sinus rhythm showed right bundle branch block and long QT intervals. First\u2010degree AV block was documented in two subjects, and J point elevation in one. A pacemaker was implanted in all cases due to symptomatic bradycardia (sick sinus syndrome). Atrial tachyarryhthmias were observed in two patients. The common characteristic ventricular arrhythmia was a monomorphic sustained ventricular tachycardia, inducible with ventricular stimulation and sensitive to lidocaine. In one patient, radiofrequency catheter ablation was successfully performed. No structural abnormalities were found in echocardiography in the study group.<\/jats:p><jats:p> <jats:italic>Conclusion:<\/jats:italic> Common clinical and ECG features suggest a common pathophysiology in this group of patients with congenital severe electrical disease.<\/jats:p>","DOI":"10.1111\/j.1540-8167.2007.01006.x","type":"journal-article","created":{"date-parts":[[2007,10,27]],"date-time":"2007-10-27T22:05:30Z","timestamp":1193522730000},"page":"550-555","source":"Crossref","is-referenced-by-count":16,"title":["Association of Congenital, Diffuse Electrical Disease in Children with Normal Heart: Sick Sinus Syndrome, Intraventricular Conduction Block, and Monomorphic Ventricular Tachycardia"],"prefix":"10.1111","volume":"19","author":[{"given":"PEDRO","family":"ITURRALDE\u2010TORRES","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"SANTIAGO","family":"NAVA\u2010TOWNSEND","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"JORGE","family":"G\u00d3MEZ\u2010FLORES","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"ARGELIA","family":"MEDEIROS\u2010DOMINGO","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"LUIS","family":"COL\u00cdN\u2010LIZALDE","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"ANTONIO G.","family":"HERMOSILLO","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"DIANA","family":"VICTORIA","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"MANLIO F.","family":"M\u00c1RQUEZ","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"311","published-online":{"date-parts":[[2008,7,8]]},"reference":[{"key":"e_1_2_6_2_2","doi-asserted-by":"publisher","DOI":"10.1038\/12618"},{"key":"e_1_2_6_3_2","doi-asserted-by":"publisher","DOI":"10.1016\/j.tcm.2003.10.001"},{"key":"e_1_2_6_4_2","doi-asserted-by":"publisher","DOI":"10.1016\/j.jelectrocard.2005.06.101"},{"key":"e_1_2_6_5_2","doi-asserted-by":"publisher","DOI":"10.1161\/01.RES.0000115750.12807.7E"},{"key":"e_1_2_6_6_2","doi-asserted-by":"publisher","DOI":"10.1016\/j.jelectrocard.2004.08.002"},{"key":"e_1_2_6_7_2","doi-asserted-by":"publisher","DOI":"10.1016\/0735-1097(92)90253-J"},{"key":"e_1_2_6_8_2","doi-asserted-by":"publisher","DOI":"10.1038\/35059090"},{"key":"e_1_2_6_9_2","doi-asserted-by":"publisher","DOI":"10.1172\/JCI200318062"},{"key":"e_1_2_6_10_2","doi-asserted-by":"publisher","DOI":"10.1172\/JCI0215570"},{"key":"e_1_2_6_11_2","doi-asserted-by":"publisher","DOI":"10.1161\/CIRCULATIONAHA.106.653949"},{"key":"e_1_2_6_12_2","doi-asserted-by":"publisher","DOI":"10.1016\/j.cardiores.2004.07.007"},{"key":"e_1_2_6_13_2","doi-asserted-by":"publisher","DOI":"10.1016\/j.yjmcc.2005.02.024"},{"key":"e_1_2_6_14_2","doi-asserted-by":"publisher","DOI":"10.1016\/j.jacc.2005.08.043"},{"key":"e_1_2_6_15_2","doi-asserted-by":"publisher","DOI":"10.1016\/j.hrthm.2004.07.001"},{"key":"e_1_2_6_16_2","doi-asserted-by":"publisher","DOI":"10.1016\/S0735-1097(02)01962-9"},{"key":"e_1_2_6_17_2","first-page":"371","article-title":"Estudio cl\u00ednico de un nuevo f\u00e1rmaco antiarritmico: Propafenona. 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