{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,10,12]],"date-time":"2025-10-12T19:44:29Z","timestamp":1760298269014},"reference-count":25,"publisher":"Wiley","issue":"5","license":[{"start":{"date-parts":[[2009,4,24]],"date-time":"2009-04-24T00:00:00Z","timestamp":1240531200000},"content-version":"vor","delay-in-days":9855,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Scandinavian Journal of Haematology"],"published-print":{"date-parts":[[1982,5]]},"abstract":"<jats:p>Fanconi's anaemia is reported in 2 siblings. The simultaneous onset of pancytopenia after possible exposure to common external agents suggest that both a frail genotype and environmental factors may be etiologically involved in the disorder. One of the children died after having developed a monoblastic leukaemia. This patient disclosed very striking cytological abnormalities, including a dyserythropoietic pattern and ropalocytosis. The physiopathology of the latter abnormality, which has hitherto not been noticed in Fanconi's anaemia, is uncertain.<\/jats:p>","DOI":"10.1111\/j.1600-0609.1982.tb00549.x","type":"journal-article","created":{"date-parts":[[2010,8,4]],"date-time":"2010-08-04T19:30:07Z","timestamp":1280950207000},"page":"431-440","source":"Crossref","is-referenced-by-count":8,"title":["Fanconi's Anaemia. Simultaneous onset in 2 Siblings and unusual Cytological Findings"],"prefix":"10.1111","volume":"28","author":[{"given":"Monique de","family":"Vroede","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Walter","family":"Feremans","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Emilie de","family":"Maertelaere\u2010Laurent","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Israel","family":"Mandelbaum","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Mich\u00e8le","family":"Toppet","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Esther","family":"Vamos","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Pierre","family":"Fondu","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"311","published-online":{"date-parts":[[2009,4,24]]},"reference":[{"key":"e_1_2_1_2_1","first-page":"403","article-title":"Fanconi's anaemia","volume":"42","author":"Beard M. E. J.","year":"1973","journal-title":"Quart J Med"},{"key":"e_1_2_1_3_1","doi-asserted-by":"publisher","DOI":"10.1016\/S0031-3955(16)32778-X"},{"key":"e_1_2_1_4_1","doi-asserted-by":"publisher","DOI":"10.1056\/NEJM196601062740102"},{"key":"e_1_2_1_5_1","first-page":"413","article-title":"Fanconi's anaemia in infancy","volume":"32","author":"Borgna Pignati C.","year":"1978","journal-title":"Helv Paediat Acta"},{"key":"e_1_2_1_6_1","doi-asserted-by":"publisher","DOI":"10.1093\/ajcp\/63.6.804"},{"key":"e_1_2_1_7_1","first-page":"237","article-title":"Famili\u00e4re infantile perniziosaartige An\u00e4mie (pernizi\u00f6ses Blutbild und Konstitution)","volume":"117","author":"Fanconi G.","year":"1927","journal-title":"J. B. Kinderheilk"},{"key":"e_1_2_1_8_1","doi-asserted-by":"publisher","DOI":"10.1182\/blood.V14.9.1008.1008"},{"key":"e_1_2_1_9_1","doi-asserted-by":"crossref","first-page":"691","DOI":"10.1001\/archinte.1970.00310040115014","article-title":"The significance of haetnatologic abnormalities in patients with tuberculosis","volume":"125","author":"Glasser R. M.","year":"1970","journal-title":"Arch Intern Med"},{"key":"e_1_2_1_10_1","doi-asserted-by":"publisher","DOI":"10.1007\/BF00439778"},{"key":"e_1_2_1_11_1","volume-title":"Haematological cytochemistry","author":"Hayhoe F. G. J.","year":"1980"},{"key":"e_1_2_1_12_1","doi-asserted-by":"publisher","DOI":"10.1111\/j.1600-0609.1978.tb02496.x"},{"key":"e_1_2_1_13_1","first-page":"551","article-title":"L'an\u00e9mie de Fanconi: aspects cytog\u00e9n\u00e9tiques et biochimiques","volume":"15","author":"Jalbert P.","year":"1975","journal-title":"Nouv Rev Fr Hematol"},{"key":"e_1_2_1_14_1","doi-asserted-by":"publisher","DOI":"10.1016\/S0022-3476(76)80751-2"},{"key":"e_1_2_1_15_1","first-page":"713","article-title":"Sur un cas de leuc\u00e9mie aigu\u00eb chez une fillette atteinte d'an\u00e9mie de Fanconi","volume":"14","author":"Levy J. M.","year":"1974","journal-title":"Nouv Rev Fr Hematol"},{"key":"e_1_2_1_16_1","doi-asserted-by":"publisher","DOI":"10.1083\/jcb.9.2.409"},{"key":"e_1_2_1_17_1","doi-asserted-by":"publisher","DOI":"10.1093\/ajcp\/73.3.433"},{"key":"e_1_2_1_18_1","first-page":"1079","article-title":"Relation between cancer and congenital defects: an epidemiologic evaluation","volume":"40","author":"Miller R. W.","year":"1968","journal-title":"J Natl Cancer Inst"},{"key":"e_1_2_1_19_1","first-page":"8","volume-title":"Further observations on a phosphate buffer for osmium solutions","author":"Millonig G.","year":"1962"},{"key":"e_1_2_1_20_1","doi-asserted-by":"publisher","DOI":"10.1002\/1097-0142(197509)36:3<1029::AID-CNCR2820360328>3.0.CO;2-5"},{"key":"e_1_2_1_21_1","doi-asserted-by":"publisher","DOI":"10.1182\/blood.V37.1.96.96"},{"key":"e_1_2_1_22_1","doi-asserted-by":"publisher","DOI":"10.1007\/BF00295817"},{"key":"e_1_2_1_23_1","doi-asserted-by":"publisher","DOI":"10.1111\/j.1399-0004.1979.tb00998.x"},{"key":"e_1_2_1_24_1","first-page":"43","article-title":"Fanconi's anaemia with special references to erythro\u2010kinetic features","volume":"53","author":"Skikne B. S.","year":"1978","journal-title":"5 Afr Med J"},{"key":"e_1_2_1_25_1","doi-asserted-by":"publisher","DOI":"10.1002\/path.1711090102"},{"key":"e_1_2_1_26_1","first-page":"185","volume-title":"Hereditary disorders of erythro\u2010cyte metabolism","author":"Waller H. D.","year":"1968"}],"container-title":["Scandinavian Journal of Haematology"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.wiley.com\/onlinelibrary\/tdm\/v1\/articles\/10.1111%2Fj.1600-0609.1982.tb00549.x","content-type":"unspecified","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/pdf\/10.1111\/j.1600-0609.1982.tb00549.x","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2023,11,8]],"date-time":"2023-11-08T20:45:01Z","timestamp":1699476301000},"score":1,"resource":{"primary":{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/10.1111\/j.1600-0609.1982.tb00549.x"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[1982,5]]},"references-count":25,"journal-issue":{"issue":"5","published-print":{"date-parts":[[1982,5]]}},"alternative-id":["10.1111\/j.1600-0609.1982.tb00549.x"],"URL":"https:\/\/doi.org\/10.1111\/j.1600-0609.1982.tb00549.x","archive":["Portico"],"relation":{},"ISSN":["0036-553X"],"issn-type":[{"value":"0036-553X","type":"print"}],"subject":[],"published":{"date-parts":[[1982,5]]}}}