{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2023,11,15]],"date-time":"2023-11-15T08:00:24Z","timestamp":1700035224495},"reference-count":31,"publisher":"Wiley","issue":"5","license":[{"start":{"date-parts":[[2005,9,28]],"date-time":"2005-09-28T00:00:00Z","timestamp":1127865600000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["European J of Haematology"],"published-print":{"date-parts":[[2005,11]]},"abstract":"<jats:p><jats:bold>Abstract:\u2002<\/jats:bold> The Budd\u2010Chiari syndrome (BCS), characterized by the obstruction and occlusion of the suprahepatic veins, is a rare but typical complication occurring in patients with polycythemia vera (PV). We describe three young women who developed BCS as first manifestation of PV, in association with an inherited thrombophilic state and in the absence of concomitant use of oral contraceptives. Our report illustrates the existence of an aggressive form of myeloproliferative disorder, which requires prompt recognition and immediate therapeutic intervention including cytostatic drugs and anticoagulant treatment. Furthermore, we suggest the need of routine screening for thrombophilic state in young women affected by PV.<\/jats:p>","DOI":"10.1111\/j.1600-0609.2005.00522.x","type":"journal-article","created":{"date-parts":[[2005,9,28]],"date-time":"2005-09-28T12:56:53Z","timestamp":1127912213000},"page":"396-400","source":"Crossref","is-referenced-by-count":9,"title":["Budd\u2010Chiari syndrome as the first manifestation of polycythemia vera in young women with inherited thrombophilic state: an aggressive form of myeloproliferative disorder requiring multidisciplinary management"],"prefix":"10.1111","volume":"75","author":[{"given":"Massimo","family":"Breccia","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Salvatore Giacomo","family":"Morano","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Mariella","family":"D'Andrea","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Eleonora","family":"Russo","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Gianna Maria","family":"D'Elia","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Giuliana","family":"Alimena","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"311","published-online":{"date-parts":[[2005,9,28]]},"reference":[{"key":"e_1_2_6_2_2","doi-asserted-by":"publisher","DOI":"10.1016\/1040-8428(94)00164-O"},{"key":"e_1_2_6_3_2","doi-asserted-by":"publisher","DOI":"10.7326\/0003-4819-103-3-329"},{"key":"e_1_2_6_4_2","doi-asserted-by":"publisher","DOI":"10.1136\/bmj.302.6770.192"},{"key":"e_1_2_6_5_2","doi-asserted-by":"publisher","DOI":"10.1016\/S0025-6196(12)62109-0"},{"key":"e_1_2_6_6_2","doi-asserted-by":"publisher","DOI":"10.1097\/00005792-199401000-00003"},{"key":"e_1_2_6_7_2","first-page":"183","volume-title":"Diseases of the liver and biliary system","author":"Sherlock S","year":"1993"},{"key":"e_1_2_6_8_2","first-page":"1091","volume-title":"Diseases of the liver","author":"Reynolds TB.","year":"1993"},{"key":"e_1_2_6_9_2","doi-asserted-by":"publisher","DOI":"10.1093\/oxfordjournals.qjmed.a030135"},{"key":"e_1_2_6_10_2","first-page":"2364","article-title":"Factor V Leiden mutation, prothrombin gene mutation, and deficiencies in coagulation inhibitors associated with Budd\u2010Chiari syndrome and portal vein thrombosis: results of a case\u2010control study","volume":"96","author":"Janssen HL","year":"2000","journal-title":"Blood"},{"key":"e_1_2_6_11_2","first-page":"11","article-title":"Polycythemia vera and essential thrombocytemia in young patients","volume":"78","author":"Frezzato M","year":"1993","journal-title":"Haematologica"},{"key":"e_1_2_6_12_2","first-page":"543","article-title":"Is polycythemia vera a serious disease in young adults","volume":"86","author":"Perea G","year":"2001","journal-title":"Haematologica"},{"key":"e_1_2_6_13_2","first-page":"202","article-title":"Indications for cytoreductive therapy in polycythemia vera and essential thrombocythemia","volume":"1","author":"Barbui T","year":"2003","journal-title":"Hematology"},{"key":"e_1_2_6_14_2","doi-asserted-by":"publisher","DOI":"10.1007\/BF01725198"},{"key":"e_1_2_6_15_2","doi-asserted-by":"publisher","DOI":"10.1002\/hep.510310307"},{"key":"e_1_2_6_16_2","doi-asserted-by":"publisher","DOI":"10.1111\/j.1365-2141.1987.00285.x"},{"key":"e_1_2_6_17_2","doi-asserted-by":"publisher","DOI":"10.1055\/s-2007-996117"},{"key":"e_1_2_6_18_2","doi-asserted-by":"publisher","DOI":"10.1016\/S0168-8278(00)80218-4"},{"key":"e_1_2_6_19_2","doi-asserted-by":"publisher","DOI":"10.1182\/blood.V64.1.1.1"},{"key":"e_1_2_6_20_2","doi-asserted-by":"publisher","DOI":"10.1136\/gut.40.6.798"},{"key":"e_1_2_6_21_2","doi-asserted-by":"crossref","first-page":"445","DOI":"10.1055\/s-0037-1615008","article-title":"Budd\u2010Chiari syndrome in a patient heterozygous for the G20210A mutation of the prothrombin gene","volume":"79","author":"Bucciarelli P","year":"1998","journal-title":"Thromb haemost"},{"key":"e_1_2_6_22_2","doi-asserted-by":"publisher","DOI":"10.1002\/lt.500050211"},{"key":"e_1_2_6_23_2","doi-asserted-by":"publisher","DOI":"10.1016\/S0300-2977(00)00046-2"},{"key":"e_1_2_6_24_2","doi-asserted-by":"publisher","DOI":"10.1002\/ajh.10153"},{"key":"e_1_2_6_25_2","doi-asserted-by":"publisher","DOI":"10.1016\/S0140-6736(94)90286-0"},{"key":"e_1_2_6_26_2","doi-asserted-by":"publisher","DOI":"10.1055\/s-2007-996120"},{"key":"e_1_2_6_27_2","doi-asserted-by":"publisher","DOI":"10.1111\/j.1365-2141.2004.05277.x"},{"key":"e_1_2_6_28_2","doi-asserted-by":"publisher","DOI":"10.1182\/asheducation-2000.1.51"},{"key":"e_1_2_6_29_2","doi-asserted-by":"publisher","DOI":"10.1016\/S0037-1963(01)90137-4"},{"key":"e_1_2_6_30_2","doi-asserted-by":"publisher","DOI":"10.1056\/NEJMoa035572"},{"key":"e_1_2_6_31_2","doi-asserted-by":"publisher","DOI":"10.1097\/00000658-200104000-00007"},{"key":"e_1_2_6_32_2","doi-asserted-by":"publisher","DOI":"10.1053\/jhep.2002.30274"}],"container-title":["European Journal of Haematology"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.wiley.com\/onlinelibrary\/tdm\/v1\/articles\/10.1111%2Fj.1600-0609.2005.00522.x","content-type":"unspecified","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/pdf\/10.1111\/j.1600-0609.2005.00522.x","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2023,9,27]],"date-time":"2023-09-27T04:02:52Z","timestamp":1695787372000},"score":1,"resource":{"primary":{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/10.1111\/j.1600-0609.2005.00522.x"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2005,9,28]]},"references-count":31,"journal-issue":{"issue":"5","published-print":{"date-parts":[[2005,11]]}},"alternative-id":["10.1111\/j.1600-0609.2005.00522.x"],"URL":"https:\/\/doi.org\/10.1111\/j.1600-0609.2005.00522.x","archive":["Portico"],"relation":{},"ISSN":["0902-4441","1600-0609"],"issn-type":[{"value":"0902-4441","type":"print"},{"value":"1600-0609","type":"electronic"}],"subject":[],"published":{"date-parts":[[2005,9,28]]}}}