{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,11,1]],"date-time":"2025-11-01T13:39:25Z","timestamp":1762004365649},"reference-count":24,"publisher":"Wiley","issue":"4","license":[{"start":{"date-parts":[[2011,12,1]],"date-time":"2011-12-01T00:00:00Z","timestamp":1322697600000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":["onlinelibrary.wiley.com"],"crossmark-restriction":true},"short-container-title":["Acta Paediatrica"],"published-print":{"date-parts":[[2012,4]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:p><jats:bold>Aim:\u2002<\/jats:bold> The aims of the study were to assess shoulder range of motion (ROM) in patients with mucopolysaccharidosis type II (MPS II) and to correlate joint mobility with patients\u2019 height, age and functional status.<\/jats:p><jats:p><jats:bold>Methods:\u2002<\/jats:bold> Passive ROM and <jats:italic>Z<\/jats:italic>\u2010score of height were followed in 29 patients with MPS II (mean age 11.5\u2003years, range 2\u201329\u2003years) between the years 2005 and 2010. Passive ROM was measured by a goniometer, and height, by a stadiometer. Functional status was assessed by an age\u2010appropriate health assessment questionnaire (HAQ).<\/jats:p><jats:p><jats:bold>Results:\u2002<\/jats:bold> (i) A strong correlation was observed between patients\u2019 age and <jats:italic>Z<\/jats:italic>\u2010score of patients\u2019 height (R\u2003=\u20030.78, p\u2003&lt;\u20030.001). (ii) A medium correlation was observed between <jats:italic>Z<\/jats:italic>\u2010score of patients\u2019 height and passive shoulder flexion and abduction (R\u2003=\u20030.697, p\u2003&lt;\u20030.001 and R\u2003=\u20030.63, p\u2003&lt;\u20030.001, respectively). The progression of restriction was slower in attenuated patients. (iii) Restrictions in shoulder flexion and abduction were already observed before the second year of life. (iv) ROM limitations intensified and became more severe with age. (v) Activities of daily living depended on cognitive impairment of patients with MPS II.<\/jats:p><jats:p><jats:bold>Conclusion:\u2002<\/jats:bold> Range of motion limitations in patients with MPS II correlate with patients\u2019 height, increase with patients\u2019 age and are more pronounced in a severe form of MPS II.<\/jats:p>","DOI":"10.1111\/j.1651-2227.2011.02522.x","type":"journal-article","created":{"date-parts":[[2011,11,12]],"date-time":"2011-11-12T00:24:33Z","timestamp":1321057473000},"update-policy":"http:\/\/dx.doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":18,"title":["Restricted joint range of motion in patients with MPS II: correlation with height, age and functional status"],"prefix":"10.1111","volume":"101","author":[{"given":"Jolanta","family":"Marucha","sequence":"first","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Agnieszka","family":"Jurecka","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Ma\u0142gorzata","family":"Syczewska","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Agnieszka","family":"R\u00f3\u017cd\u017cy\u0144ska\u2010\u015awi\u0105tkowska","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Anna","family":"Tylki\u2010Szyma\u0144ska","sequence":"additional","affiliation":[],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"311","published-online":{"date-parts":[[2011,12]]},"reference":[{"key":"e_1_2_10_2_2","volume-title":"The metabolic and molecular basis of inherited disease","author":"Neufeld EF","year":"2001"},{"key":"e_1_2_10_3_2","doi-asserted-by":"publisher","DOI":"10.1542\/peds.2007-1350"},{"key":"e_1_2_10_4_2","doi-asserted-by":"publisher","DOI":"10.1016\/S0002-9440(10)64961-9"},{"key":"e_1_2_10_5_2","doi-asserted-by":"publisher","DOI":"10.1097\/01.bor.0000147283.40529.13"},{"key":"e_1_2_10_6_2","doi-asserted-by":"publisher","DOI":"10.2353\/ajpath.2008.070564"},{"key":"e_1_2_10_7_2","doi-asserted-by":"publisher","DOI":"10.1203\/01.PDR.0000156510.96253.5A"},{"key":"e_1_2_10_8_2","doi-asserted-by":"publisher","DOI":"10.1073\/pnas.0912937107"},{"key":"e_1_2_10_9_2","doi-asserted-by":"publisher","DOI":"10.1038\/labinvest.3780345"},{"key":"e_1_2_10_10_2","first-page":"10","volume-title":"Klinische Tests an Knochen Gelenken und Muskeln","author":"Buckup K","year":"1995"},{"key":"e_1_2_10_11_2","doi-asserted-by":"publisher","DOI":"10.1016\/S1047-9651(18)30047-0"},{"key":"e_1_2_10_12_2","doi-asserted-by":"publisher","DOI":"10.1016\/0021-9290(87)90027-3"},{"key":"e_1_2_10_13_2","doi-asserted-by":"publisher","DOI":"10.1682\/JRRD.2003.03.0149"},{"key":"e_1_2_10_14_2","first-page":"62","volume-title":"Kinezyterapia","author":"Zembaty A","year":"2002"},{"key":"e_1_2_10_15_2","unstructured":"NoratoDYJ GiovanettiDF.MPS I Registry health assessment questionnaire. 9th International Symposium on Mucopolysaccharidosis and Related Diseases. 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