{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,12,6]],"date-time":"2025-12-06T04:38:55Z","timestamp":1764995935659},"reference-count":12,"publisher":"Wiley","issue":"9","license":[{"start":{"date-parts":[[2013,4,11]],"date-time":"2013-04-11T00:00:00Z","timestamp":1365638400000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Cardiovasc electrophysiol"],"published-print":{"date-parts":[[2013,9]]},"abstract":"<jats:title>S\u2010ICD in Danon Disease<\/jats:title><jats:p>Danon disease is a rare X\u2010linked lysosomal disease causing severe hypertrophic cardiomyopathy (<jats:italic>LAMP2<\/jats:italic> cardiomyopathy) and an extremely poor prognosis in males, with several reported cases of sudden cardiac death despite the use of transvenous implantable cardioverter defibrillators (TV\u2010ICD). We describe a case in which a TV\u2010ICD was unable to defibrillate induced ventricular fibrillation (VF), but a wholly subcutaneous system (S\u2010ICD) was successful in terminating induced VF and spontaneous ventricular tachycardia. These findings have relevance to the selection of device therapy in the management of these individuals and a wider group of young patients with severe hypertrophic cardiomyopathy.<\/jats:p>","DOI":"10.1111\/jce.12142","type":"journal-article","created":{"date-parts":[[2013,3,15]],"date-time":"2013-03-15T19:34:17Z","timestamp":1363376057000},"page":"1051-1053","source":"Crossref","is-referenced-by-count":14,"title":["Advantages of a Subcutaneous Implantable Cardioverter\u2010Defibrillator in <i>LAMP2<\/i> Hypertrophic Cardiomyopathy"],"prefix":"10.1111","volume":"24","author":[{"given":"ALY","family":"ZAKI","sequence":"first","affiliation":[{"name":"Manchester Heart Centre\/Institute of Cardiovascular Medicine"},{"name":"Centre for Genetic Medicine, Institute of Human Development University of Manchester, Manchester Academic Health Science Centre  Manchester UK"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"AMIR","family":"ZAIDI","sequence":"additional","affiliation":[{"name":"Manchester Heart Centre\/Institute of Cardiovascular Medicine"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"WILLIAM G.","family":"NEWMAN","sequence":"additional","affiliation":[{"name":"Centre for Genetic Medicine, Institute of Human Development University of Manchester, Manchester Academic Health Science Centre  Manchester UK"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"CLIFFORD J.","family":"GARRATT","sequence":"additional","affiliation":[{"name":"Manchester Heart Centre\/Institute of Cardiovascular Medicine"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"311","published-online":{"date-parts":[[2013,4,11]]},"reference":[{"key":"e_1_2_5_2_1","doi-asserted-by":"publisher","DOI":"10.1212\/WNL.31.1.51"},{"key":"e_1_2_5_3_1","doi-asserted-by":"publisher","DOI":"10.1136\/hrt.2003.029504"},{"key":"e_1_2_5_4_1","doi-asserted-by":"publisher","DOI":"10.1038\/35022604"},{"key":"e_1_2_5_5_1","doi-asserted-by":"publisher","DOI":"10.1097\/GIM.0b013e31820ad795"},{"key":"e_1_2_5_6_1","doi-asserted-by":"publisher","DOI":"10.1001\/jama.2009.371"},{"key":"e_1_2_5_7_1","doi-asserted-by":"publisher","DOI":"10.1046\/j.1540-8167.2004.03649.x"},{"key":"e_1_2_5_8_1","doi-asserted-by":"publisher","DOI":"10.1111\/pace.12039"},{"key":"e_1_2_5_9_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.hrthm.2005.12.023"},{"key":"e_1_2_5_10_1","doi-asserted-by":"publisher","DOI":"10.1056\/NEJMoa0909545"},{"key":"e_1_2_5_11_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.hrthm.2012.06.019"},{"key":"e_1_2_5_12_1","doi-asserted-by":"publisher","DOI":"10.1111\/j.1540-8167.2012.02432.x"},{"key":"e_1_2_5_13_1","doi-asserted-by":"publisher","DOI":"10.1161\/CIRCEP.111.964676"}],"container-title":["Journal of Cardiovascular Electrophysiology"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.wiley.com\/onlinelibrary\/tdm\/v1\/articles\/10.1111%2Fjce.12142","content-type":"unspecified","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.wiley.com\/onlinelibrary\/tdm\/v1\/articles\/10.1111%2Fjce.12142","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/pdf\/10.1111\/jce.12142","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2023,10,2]],"date-time":"2023-10-02T23:04:17Z","timestamp":1696287857000},"score":1,"resource":{"primary":{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/10.1111\/jce.12142"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2013,4,11]]},"references-count":12,"journal-issue":{"issue":"9","published-print":{"date-parts":[[2013,9]]}},"alternative-id":["10.1111\/jce.12142"],"URL":"https:\/\/doi.org\/10.1111\/jce.12142","archive":["Portico"],"relation":{},"ISSN":["1045-3873","1540-8167"],"issn-type":[{"value":"1045-3873","type":"print"},{"value":"1540-8167","type":"electronic"}],"subject":[],"published":{"date-parts":[[2013,4,11]]}}}