{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,2,21]],"date-time":"2026-02-21T04:27:10Z","timestamp":1771648030742,"version":"3.50.1"},"reference-count":10,"publisher":"Wiley","issue":"5","license":[{"start":{"date-parts":[[2022,1,10]],"date-time":"2022-01-10T00:00:00Z","timestamp":1641772800000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/creativecommons.org\/licenses\/by-nc-nd\/4.0\/"}],"content-domain":{"domain":["onlinelibrary.wiley.com"],"crossmark-restriction":true},"short-container-title":["J of Diabetes Invest"],"published-print":{"date-parts":[[2022,5]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:p>A 34\u2010year\u2010old man visited our Department of Gastroenterology and Metabolism, Nagoya City University Graduate School of Medical Sciences, Nagoya, Japan, because of dry mouth and weight loss. His plasma glucose level was 32.8\u2009mmol\/L and serum levels of ketone bodies were increased, but with metabolic alkalemia. He was also suffering from renal tubular hypomagnesemia and hypokalemia. Abdominal computed tomography showed bilateral renal cysts. These findings were suggestive of maturity\u2010onset diabetes of the young type\u20095. Genetic testing showed heterozygous hepatocyte nuclear factor\u20091 beta gene deletion. In the present case, it seemed reasonable to view hepatocyte nuclear factor\u20091 beta gene deletion as the common cause of maturity\u2010onset diabetes of the young type\u20095\u2010associated diabetic ketoacidosis and tubular malfunction\u2010induced hypokalemic alkalosis. This case exemplifies the importance of hepatocyte nuclear factor\u20091 beta gene abnormality as a potential cause of diabetic ketoacidosis with alkalemia.<\/jats:p>","DOI":"10.1111\/jdi.13737","type":"journal-article","created":{"date-parts":[[2021,12,21]],"date-time":"2021-12-21T06:49:35Z","timestamp":1640069375000},"page":"923-926","update-policy":"https:\/\/doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":4,"title":["Maturity\u2010onset diabetes of the young type\u20095, presenting as diabetic ketoacidosis with alkalemia: A report of a case"],"prefix":"10.1111","volume":"13","author":[{"given":"Akiko","family":"Hayakawa\u2010Iwamoto","sequence":"first","affiliation":[{"name":"Department of Gastroenterology and Metabolism Graduate School of Medical Sciences and Medical School Nagoya City University  Nagoya 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