{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,6,4]],"date-time":"2026-06-04T01:54:57Z","timestamp":1780538097550,"version":"3.54.1"},"reference-count":27,"publisher":"Wiley","issue":"8","license":[{"start":{"date-parts":[[2015,1,20]],"date-time":"2015-01-20T00:00:00Z","timestamp":1421712000000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Acad Dermatol Venereol"],"published-print":{"date-parts":[[2015,8]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:sec><jats:title>Background<\/jats:title><jats:p>Primary cutaneous lymphomas (<jats:styled-content style=\"fixed-case\">PCL<\/jats:styled-content>) are a heterogenous group of rare lymphoid neoplasms with incomplete information on global and regional prevalence. The recently introduced lymphoma classifications define distinctive clinicopathological disease entities that should allow for more accurate epidemiological assessment.<\/jats:p><\/jats:sec><jats:sec><jats:title>Objective<\/jats:title><jats:p>The aim of this study was to evaluate the prevalence and clinical spectrum of <jats:styled-content style=\"fixed-case\">PCL<\/jats:styled-content> diagnosed and treated at the Department of Dermatology and Venereology in St. P\u00f6lten, Lower Austria, a dermatology referral centre providing secondary and tertiary care for a population of about 600\u00a0000.<\/jats:p><\/jats:sec><jats:sec><jats:title>Methods<\/jats:title><jats:p>In this retrospective study pathology reports, electronically archived between 2006 and 2013, were screened for the terms lymphoma, mycosis fungoides (<jats:styled-content style=\"fixed-case\">MF<\/jats:styled-content>) and lymphomatoid papulosis (LyP). Patients were diagnosed according to the current <jats:styled-content style=\"fixed-case\">WHO<\/jats:styled-content>\u2010<jats:styled-content style=\"fixed-case\">EORTC<\/jats:styled-content> classification for cutaneous lymphomas and results were compared with data from European, <jats:styled-content style=\"fixed-case\">US<\/jats:styled-content> and Asian centres.<\/jats:p><\/jats:sec><jats:sec><jats:title>Results<\/jats:title><jats:p>Among 86 patients with <jats:styled-content style=\"fixed-case\">PCL<\/jats:styled-content> (age 58.3\u00a0\u00b1\u00a017.35\u00a0years, mean \u00b1 <jats:styled-content style=\"fixed-case\">SD<\/jats:styled-content>; women 38%, <jats:italic>n<\/jats:italic>\u00a0=\u00a033; men 62%, <jats:italic>n<\/jats:italic>\u00a0=\u00a053) 83% (<jats:italic>n<\/jats:italic>\u00a0=\u00a071) were classified as cutaneous T\u2010cell lymphomas (<jats:styled-content style=\"fixed-case\">CTCL<\/jats:styled-content>) and 17% (<jats:italic>n<\/jats:italic>\u00a0=\u00a015) as cutaneous B\u2010cell lymphomas (<jats:styled-content style=\"fixed-case\">CBCL<\/jats:styled-content>). Nine patients with <jats:styled-content style=\"fixed-case\">CTCL<\/jats:styled-content> showed associated haematological disorders and malignomas. Among 47 <jats:styled-content style=\"fixed-case\">MF<\/jats:styled-content> patients following variants were observed: pilotropic <jats:styled-content style=\"fixed-case\">MF<\/jats:styled-content> (<jats:italic>n<\/jats:italic>\u00a0=\u00a02), follicular mucinosis (<jats:italic>n<\/jats:italic>\u00a0=\u00a01), unilesional <jats:styled-content style=\"fixed-case\">MF<\/jats:styled-content> (<jats:italic>n<\/jats:italic>\u00a0=\u00a01), large\u2010cell transformation (<jats:italic>n<\/jats:italic>\u00a0=\u00a03), erythrodermic <jats:styled-content style=\"fixed-case\">MF<\/jats:styled-content> (<jats:italic>n<\/jats:italic>\u00a0=\u00a01), poikilodermatous <jats:styled-content style=\"fixed-case\">MF<\/jats:styled-content> (<jats:italic>n<\/jats:italic>\u00a0=\u00a02) and posttransplant lymphoproliferative disorder (<jats:styled-content style=\"fixed-case\">CD<\/jats:styled-content>8<jats:sup>+<\/jats:sup> <jats:styled-content style=\"fixed-case\">MF<\/jats:styled-content> with gamma\/delta phenotype after renal transplantation) (<jats:italic>n<\/jats:italic>\u00a0=\u00a01). One patient had <jats:styled-content style=\"fixed-case\">MF<\/jats:styled-content> concurrent with lymphomatoid papulosis. The group of <jats:styled-content style=\"fixed-case\">CBCL<\/jats:styled-content> comprised six cases (40%) of <jats:styled-content style=\"fixed-case\">PCMZL<\/jats:styled-content> and <jats:styled-content style=\"fixed-case\">PCFCL<\/jats:styled-content> each, 20% (<jats:italic>n<\/jats:italic>\u00a0=\u00a03) were classified as <jats:styled-content style=\"fixed-case\">PCLBCL<\/jats:styled-content>,<jats:styled-content style=\"fixed-case\"> LT<\/jats:styled-content>.<\/jats:p><\/jats:sec><jats:sec><jats:title>Conclusion<\/jats:title><jats:p>This study for the first time provides data on the distribution of <jats:styled-content style=\"fixed-case\">PCL<\/jats:styled-content> clinicopathologic variants and stages according to the latest classification and staging systems in an Austrian referral centre.<\/jats:p><\/jats:sec>","DOI":"10.1111\/jdv.12907","type":"journal-article","created":{"date-parts":[[2015,1,20]],"date-time":"2015-01-20T07:00:16Z","timestamp":1421737216000},"page":"1517-1523","source":"Crossref","is-referenced-by-count":16,"title":["Frequency of primary cutaneous lymphoma variants in Austria: retrospective data from a dermatology referral centre between 2006 and 2013"],"prefix":"10.1111","volume":"29","author":[{"given":"J.","family":"Eder","sequence":"first","affiliation":[{"name":"Karl Landsteiner Institute of Dermatological Research St. P\u00f6lten Austria"},{"name":"Department of Dermatology and Venereology Karl Landsteiner University of Health Sciences St. P\u00f6lten Austria"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"A.","family":"Kern","sequence":"additional","affiliation":[{"name":"Karl Landsteiner Institute of Dermatological Research St. P\u00f6lten Austria"},{"name":"Department of Dermatology and Venereology Karl Landsteiner University of Health Sciences St. P\u00f6lten Austria"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"J.","family":"Moser","sequence":"additional","affiliation":[{"name":"Karl Landsteiner Institute of Dermatological Research St. P\u00f6lten Austria"},{"name":"Department of Dermatology and Venereology Karl Landsteiner University of Health Sciences St. P\u00f6lten Austria"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"M.","family":"Kitzw\u00f6gerer","sequence":"additional","affiliation":[{"name":"Institute of Clinical Pathology Karl Landsteiner University of Health Sciences St. P\u00f6lten Austria"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"R.","family":"Sedivy","sequence":"additional","affiliation":[{"name":"Institute of Clinical Pathology Karl Landsteiner University of Health Sciences St. P\u00f6lten Austria"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"F.","family":"Trautinger","sequence":"additional","affiliation":[{"name":"Karl Landsteiner Institute of Dermatological Research St. P\u00f6lten Austria"},{"name":"Department of Dermatology and Venereology Karl Landsteiner University of Health Sciences St. P\u00f6lten Austria"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"311","published-online":{"date-parts":[[2015,1,20]]},"reference":[{"key":"e_1_2_5_2_1","doi-asserted-by":"publisher","DOI":"10.1182\/blood-2004-09-3502"},{"key":"e_1_2_5_3_1","doi-asserted-by":"publisher","DOI":"10.1182\/blood-2008-10-184168"},{"key":"e_1_2_5_4_1","first-page":"354","article-title":"EORTC classification for primary cutaneous lymphomas: a proposal from the Cutaneous Lymphoma Study Group of the European Organization for Research and Treatment of Cancer","volume":"90","author":"Willemze R","year":"1997","journal-title":"Blood"},{"key":"e_1_2_5_5_1","volume-title":"WHO Classification of Tumours of Haematopoietic and Lymphoid Tissues","author":"Swerdlow HS","year":"2008"},{"key":"e_1_2_5_6_1","doi-asserted-by":"publisher","DOI":"10.1182\/blood-2007-03-055749"},{"key":"e_1_2_5_7_1","doi-asserted-by":"publisher","DOI":"10.1182\/blood-2006-10-054601"},{"key":"e_1_2_5_8_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.ejca.2006.01.025"},{"key":"e_1_2_5_9_1","doi-asserted-by":"publisher","DOI":"10.1182\/blood-2008-04-152850"},{"key":"e_1_2_5_10_1","doi-asserted-by":"publisher","DOI":"10.1182\/blood\u20102011\u201005\u2010351346"},{"key":"e_1_2_5_11_1","doi-asserted-by":"publisher","DOI":"10.1111\/j.1365-2133.2007.08239.x"},{"key":"e_1_2_5_12_1","doi-asserted-by":"publisher","DOI":"10.1111\/j.1365-2133.2010.10143.x"},{"key":"e_1_2_5_13_1","doi-asserted-by":"publisher","DOI":"10.1200\/JCO.2005.03.0395"},{"key":"e_1_2_5_14_1","doi-asserted-by":"publisher","DOI":"10.1111\/j.1365-2133.2006.07264.x"},{"key":"e_1_2_5_15_1","doi-asserted-by":"publisher","DOI":"10.1111\/j.1346-8138.2010.01049.x"},{"key":"e_1_2_5_16_1","doi-asserted-by":"publisher","DOI":"10.1111\/j.1365-2230.2012.04461.x"},{"key":"e_1_2_5_17_1","doi-asserted-by":"publisher","DOI":"10.1182\/blood.V99.3.800"},{"key":"e_1_2_5_18_1","doi-asserted-by":"publisher","DOI":"10.1111\/j.1610-0387.2007.06337.x"},{"key":"e_1_2_5_19_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.jaad.2012.02.033"},{"key":"e_1_2_5_20_1","doi-asserted-by":"publisher","DOI":"10.1001\/archderm.139.7.857"},{"key":"e_1_2_5_21_1","doi-asserted-by":"publisher","DOI":"10.1200\/JCO.2006.09.6396"},{"key":"e_1_2_5_22_1","doi-asserted-by":"publisher","DOI":"10.1001\/jamadermatol.2013.5526"},{"key":"e_1_2_5_23_1","doi-asserted-by":"publisher","DOI":"10.1111\/j.1365-2133.2006.07346.x"},{"key":"e_1_2_5_24_1","doi-asserted-by":"publisher","DOI":"10.1007\/s00277-007-0276-8"},{"key":"e_1_2_5_25_1","doi-asserted-by":"publisher","DOI":"10.1001\/archderm.143.1.45"},{"key":"e_1_2_5_26_1","doi-asserted-by":"publisher","DOI":"10.2340\/00015555-1496"},{"key":"e_1_2_5_27_1","doi-asserted-by":"publisher","DOI":"10.1002\/gcc.20513"},{"key":"e_1_2_5_28_1","unstructured":"ZielonkeN.Krebsinzidenz und Krebsmortalit\u00e4t in \u00d6sterreich. Statistik Austria 2014."}],"container-title":["Journal of the European Academy of Dermatology and Venereology"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.wiley.com\/onlinelibrary\/tdm\/v1\/articles\/10.1111%2Fjdv.12907","content-type":"unspecified","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/api.wiley.com\/onlinelibrary\/tdm\/v1\/articles\/10.1111%2Fjdv.12907","content-type":"application\/pdf","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/pdf\/10.1111\/jdv.12907","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2023,9,24]],"date-time":"2023-09-24T11:21:55Z","timestamp":1695554515000},"score":1,"resource":{"primary":{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/10.1111\/jdv.12907"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2015,1,20]]},"references-count":27,"journal-issue":{"issue":"8","published-print":{"date-parts":[[2015,8]]}},"alternative-id":["10.1111\/jdv.12907"],"URL":"https:\/\/doi.org\/10.1111\/jdv.12907","archive":["Portico"],"relation":{},"ISSN":["0926-9959","1468-3083"],"issn-type":[{"value":"0926-9959","type":"print"},{"value":"1468-3083","type":"electronic"}],"subject":[],"published":{"date-parts":[[2015,1,20]]}}}