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To avoid such bewilderment, the present review describes the distinguishing clinical and genetic criteria of 20 different capillary malformations, and a specific name is given to all of them. The group of capillary naevi includes\n                    <jats:italic>\n                      naevus flammeus, port\u2010wine naevus of the Proteus type, port\u2010wine naevus of the\n                      <jats:styled-content style=\"fixed-case\">CLOVES<\/jats:styled-content>\n                      type, naevus roseus, rhodoid naevus, cutis marmorata telangiectatica congenita, congenital livedo reticularis, segmental angioma serpiginosum, naevus anaemicus, naevus vascularis mixtus and angiokeratoma circumscriptum\n                    <\/jats:italic>\n                    . Capillary lesions that perhaps represent naevi are the\n                    <jats:italic>mesotropic port\u2010wine patch, Carter\u2010Mirzaa macules, unilateral punctate telangiectasia and unilateral naevoid telangiectasia of the patchy type<\/jats:italic>\n                    . Capillary malformations that do not represent naevi include\n                    <jats:italic>X\u2010linked angiokeratoma corporis diffusum (Fabry disease), autosomal dominant angiokeratoma corporis diffusum, hereditary haemorrhagic telangiectasia, hereditary angioma serpiginosusm<\/jats:italic>\n                    and the\n                    <jats:italic>salmon patch<\/jats:italic>\n                    . In this way, we are able to discriminate between various non\u2010hereditary capillary naevi such as naevus roseus and the hereditary rhodoid naevus and several hereditary traits that do not represent naevi such as angiokeratoma corporis diffusum and hereditary haemorrhagic telangiectasia; between four different types of port\u2010wine stains, three of them being lateralized and one being mesotropic; between cutis marmorata telangiectatica congenita and congenital livedo reticularis; between telangiectatic naevi and the vasoconstrictive naevus anaemicus; and between two different types of angiokeratoma corporis diffusum. Finally, arguments are presented why the salmon patch (\u2018stork bite\u2019, \u2018naevus simplex\u2019) cannot be categorized as a naevus.\n                  <\/jats:p>","DOI":"10.1111\/jdv.13147","type":"journal-article","created":{"date-parts":[[2015,4,10]],"date-time":"2015-04-10T19:32:50Z","timestamp":1428694370000},"page":"2295-2305","source":"Crossref","is-referenced-by-count":61,"title":["Capillary malformations: a classification using specific names for specific skin disorders"],"prefix":"10.1111","volume":"29","author":[{"given":"R.","family":"Happle","sequence":"first","affiliation":[{"name":"Department of Dermatology Freiburg University Medical Center Freiburg Germany"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"311","published-online":{"date-parts":[[2015,4,10]]},"reference":[{"key":"e_1_2_7_2_1","doi-asserted-by":"publisher","DOI":"10.1097\/NRL.0b013e318220c5b6"},{"key":"e_1_2_7_3_1","doi-asserted-by":"publisher","DOI":"10.1002\/9781444345384.ch112"},{"key":"e_1_2_7_4_1","doi-asserted-by":"publisher","DOI":"10.1016\/B978-0-444-52891-9.00037-3"},{"key":"e_1_2_7_5_1","doi-asserted-by":"publisher","DOI":"10.1002\/ajmg.a.35940"},{"key":"e_1_2_7_6_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.jaad.2013.05.030"},{"key":"e_1_2_7_7_1","doi-asserted-by":"publisher","DOI":"10.1002\/humu.22431"},{"key":"e_1_2_7_8_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.jaad.2006.05.069"},{"key":"e_1_2_7_9_1","doi-asserted-by":"publisher","DOI":"10.1007\/s00247-010-1559-0"},{"key":"e_1_2_7_10_1","doi-asserted-by":"publisher","DOI":"10.1002\/ajmg.a.34118"},{"key":"e_1_2_7_11_1","first-page":"2076","volume-title":"Fitzpatrick's Dermatology in General Medicine","author":"Boon LM","year":"2012"},{"key":"e_1_2_7_12_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.jaad.2008.07.035"},{"key":"e_1_2_7_13_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.ejmg.2011.02.007"},{"key":"e_1_2_7_14_1","unstructured":"Online Mendelian Inheritance in Man (OMIM). 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