{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,11,8]],"date-time":"2025-11-08T17:56:32Z","timestamp":1762624592805,"version":"3.40.5"},"reference-count":61,"publisher":"Wiley","issue":"6","license":[{"start":{"date-parts":[[2021,3,25]],"date-time":"2021-03-25T00:00:00Z","timestamp":1616630400000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"funder":[{"DOI":"10.13039\/100001819","name":"International Rett Syndrome Foundation","doi-asserted-by":"publisher","id":[{"id":"10.13039\/100001819","id-type":"DOI","asserted-by":"publisher"}]}],"content-domain":{"domain":["onlinelibrary.wiley.com"],"crossmark-restriction":true},"short-container-title":["J intellect Disabil Res"],"published-print":{"date-parts":[[2021,6]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:sec><jats:title>Background<\/jats:title><jats:p>There is a dearth of literature available on the comparative oral health status of those with Rett syndrome (RTT) despite diurnal bruxism being a supportive diagnostic criterion for the disorder. This study was designed to investigate the dental experiences of individuals with RTT in terms of perceived at\u2010home and professional dental care.<\/jats:p><\/jats:sec><jats:sec><jats:title>Methods<\/jats:title><jats:p>Using data in the <jats:italic>InterRett<\/jats:italic> database, provided by English\u2010speaking families of individuals with a confirmed <jats:italic>MECP2<\/jats:italic> genetic mutation, the study investigated relationships between dental problems, oral care, child factors including bruxism and use of gastrostomy, and socioeconomic indicators. The study also explored relationships between dental presentations and socioeconomic, child, and family\u2010related factors.<\/jats:p><\/jats:sec><jats:sec><jats:title>Results<\/jats:title><jats:p>Individuals with RTT exhibiting bruxism were more likely to access dental treatment. Those who had full oral feeding had a higher incidence rate of dental treatment than those with full tube feeding. A conservative (under) estimation of the overall dental caries progression rate revealed that this may be similar to that of the normal population.<\/jats:p><\/jats:sec><jats:sec><jats:title>Conclusions<\/jats:title><jats:p>Drivers for dental treatment in RTT include bruxism as well as dental caries. Those who have full oral feeding experience more dental treatment than those with full tube feeding. A higher maternal education level may confer a protective effect for oral health outcomes in those with RTT. Nevertheless, families generally tended to value the importance of oral health despite reported difficulties in day\u2010to\u2010day mouth care.<\/jats:p><\/jats:sec>","DOI":"10.1111\/jir.12834","type":"journal-article","created":{"date-parts":[[2021,3,25]],"date-time":"2021-03-25T11:49:51Z","timestamp":1616672991000},"page":"561-576","update-policy":"https:\/\/doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":11,"title":["Oral health care and service utilisation in individuals with Rett syndrome: an international cross\u2010sectional study"],"prefix":"10.1111","volume":"65","author":[{"ORCID":"https:\/\/orcid.org\/0000-0001-9737-1294","authenticated-orcid":false,"given":"Y. Y. L.","family":"Lai","sequence":"first","affiliation":[{"name":"School of Dentistry, UQ Oral Health Centre The University of Queensland  Herston Queensland Australia"},{"name":"Child Disability, Telethon Kids Institute University of Western Australia  Perth Western Australia Australia"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-7358-9037","authenticated-orcid":false,"given":"J.","family":"Downs","sequence":"additional","affiliation":[{"name":"Child Disability, Telethon Kids Institute University of Western Australia  Perth Western Australia Australia"},{"name":"School of Physiotherapy and Exercise Science Curtin University  Perth Western Australia Australia"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-5551-8147","authenticated-orcid":false,"given":"S.","family":"Zafar","sequence":"additional","affiliation":[{"name":"School of Dentistry, UQ Oral Health Centre The University of Queensland  Herston Queensland Australia"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-5178-6080","authenticated-orcid":false,"given":"K.","family":"Wong","sequence":"additional","affiliation":[{"name":"Child Disability, Telethon Kids Institute University of Western Australia  Perth Western Australia Australia"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-5874-5687","authenticated-orcid":false,"given":"L.","family":"Walsh","sequence":"additional","affiliation":[{"name":"School of Dentistry, UQ Oral Health Centre The University of Queensland  Herston Queensland Australia"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-6405-5834","authenticated-orcid":false,"given":"H.","family":"Leonard","sequence":"additional","affiliation":[{"name":"Child Disability, Telethon Kids Institute University of Western Australia  Perth Western Australia Australia"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"311","published-online":{"date-parts":[[2021,3,25]]},"reference":[{"key":"e_1_2_10_2_1","doi-asserted-by":"publisher","DOI":"10.1038\/13810"},{"key":"e_1_2_10_3_1","doi-asserted-by":"publisher","DOI":"10.1111\/j.1754-4505.2010.00136.x"},{"key":"e_1_2_10_4_1","first-page":"134","article-title":"Classical Rett syndrome in a Ghanaian child: a case report","volume":"28","author":"Badoe E. 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