{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,10,17]],"date-time":"2026-10-17T22:06:41Z","timestamp":1792274801129,"version":"4.4.0"},"reference-count":25,"publisher":"Wiley","issue":"2","license":[{"start":{"date-parts":[[2020,5,26]],"date-time":"2020-05-26T00:00:00Z","timestamp":1590451200000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":["onlinelibrary.wiley.com"],"crossmark-restriction":true},"short-container-title":["J Peripheral Nervous Sys"],"published-print":{"date-parts":[[2020,6]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:p>Motor chronic inflammatory demyelinating polyneuropathy (CIDP) is a rare and poorly described subtype of CIDP. We aimed to study their clinical and electrophysiological characteristics and response to treatment. From a prospective database of CIDP patients, we included patients with definite or probable CIDP with motor signs and without sensory signs\/symptoms at diagnosis. Patients were considered to have pure motor CIDP (PM\u2010CIDP) if sensory conductions were normal or to have motor predominant CIDP (MPred\u2010CIDP) if \u22652 sensory nerve action potential amplitudes were abnormal. Among the 700 patients with CIDP, 17 (2%) were included (PM\u2010CIDP n = 7, MPred\u2010CIDP n = 10); 71% were male, median age at onset was 48\u2009years (range: 13\u201076\u2009years), 47% had an associated inflammatory or infectious disease or neoplasia. At the more severe disease stage, 94% of patients had upper and lower limb weakness, with distal and proximal weakness in 4 limbs for 56% of them. Three\u2010quarters (75%) responded to intravenous immunoglobulins (IVIg) and four of five patients to corticosteroids including three of three patients with MPred\u2010CIDP. The most frequent conduction abnormalities were conduction blocks (CB, 82%) and F\u2010wave abnormalities (88%). During follow up, 4 of 10 MPred\u2010CIDP patients developed mild sensory symptoms; none with PM\u2010CIDP did so. Patients with PM\u2010CIDP had poorer outcome (median ONLS: 4; range: 22\u20105) compared to MPred\u2010CIDP (2, range: 0\u20104; <jats:italic>P<\/jats:italic> = .03) at last follow up. This study found a progressive clinical course in the majority of patients with motor CIDP as well as frequent associated diseases, CB, and F\u2010wave abnormalities. Corticosteroids might be considered as a therapeutic option in resistant IVIg patients with MPred\u2010CIDP.<\/jats:p>","DOI":"10.1111\/jns.12380","type":"journal-article","created":{"date-parts":[[2020,5,4]],"date-time":"2020-05-04T12:09:52Z","timestamp":1588594192000},"page":"162-170","update-policy":"https:\/\/doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":27,"title":["Motor chronic inflammatory demyelinating polyneuropathy (<scp>CIDP<\/scp>) in 17 patients: Clinical characteristics, electrophysiological study, and response to treatment"],"prefix":"10.1111","volume":"25","author":[{"ORCID":"https:\/\/orcid.org\/0000-0003-1563-9432","authenticated-orcid":false,"given":"Antoine","family":"Pegat","sequence":"first","affiliation":[{"name":"Service de neurologie C pathologies neuromusculaires, service d'explorations fonctionnelles neurologiques H\u00f4pital Neurologique Pierre Wertheimer, Hospices Civils de Lyon  Bron France"},{"name":"D\u00e9partement 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