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Repeated respiratory tract infections leads to the almost universal development of bronchiectasis. These clinical manifestations are a consequence of poorly functioning motile cilia. However, confirming the diagnosis is quite difficult and is often delayed, so the true incidence of <jats:styled-content style=\"fixed-case\">PCD<\/jats:styled-content> may be significantly higher than current estimates. Nasal nitric oxide has been earmarked as a useful screening tool for identifying patients, but its use is limited in pre\u2010school\u2010aged children. Due to the rarity of <jats:styled-content style=\"fixed-case\">PCD<\/jats:styled-content>, the evidence base for management is somewhat limited, and treatment regimens are extrapolated from other suppurative lung disorders, like cystic fibrosis.<\/jats:p>","DOI":"10.1111\/jpc.12628","type":"journal-article","created":{"date-parts":[[2014,6,18]],"date-time":"2014-06-18T14:04:32Z","timestamp":1403100272000},"page":"952-958","update-policy":"https:\/\/doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":18,"title":["<scp>P<\/scp>rimary ciliary dyskinesia: Overlooked and undertreated in children"],"prefix":"10.1111","volume":"50","author":[{"given":"Patrick","family":"Hosie","sequence":"first","affiliation":[{"name":"Discipline of Paediatrics School of Women's and Children's Health University of New South Wales  New South Wales Australia"},{"name":"Department of Respiratory Medicine The Children's Hospital at Westmead Sydney Medical School  Sydney New South 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