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The clinical picture can range from severe myotonic reactions (e.g., masseter spasm, opisthotonus) to attacks of weakness and paralysis. Provided here is a short overview of the pathomechanisms behind such wide\u2010ranging phenotypic presentations in these patients, followed by recommendations concerning the management of anesthesia in such populations.<\/jats:p>","DOI":"10.1111\/pan.12217","type":"journal-article","created":{"date-parts":[[2013,6,27]],"date-time":"2013-06-27T09:33:13Z","timestamp":1372325593000},"page":"824-833","source":"Crossref","is-referenced-by-count":31,"title":["Pathophysiologic and anesthetic considerations for patients with myotonia congenita or periodic paralyses"],"prefix":"10.1111","volume":"23","author":[{"given":"Oliver","family":"Bandschapp","sequence":"first","affiliation":[{"name":"Department of Anesthesia, Surgical Intensive Care, Prehospital Emergency Medicine and Pain Therapy University Hospital Basel Basel Switzerland"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Paul A.","family":"Iaizzo","sequence":"additional","affiliation":[{"name":"Departments of Surgery and Integrative Biology &amp; Physiology  The Malignant Hyperthermia Diagnostic Center, University of Minnesota Minneapolis MN USA"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"311","published-online":{"date-parts":[[2013,6,27]]},"reference":[{"key":"e_1_2_9_2_1","doi-asserted-by":"publisher","DOI":"10.1152\/physrev.00015.2007"},{"key":"e_1_2_9_3_1","doi-asserted-by":"publisher","DOI":"10.1213\/ane.0b013e3181a7c8e5"},{"key":"e_1_2_9_4_1","doi-asserted-by":"publisher","DOI":"10.1002\/mus.880130311"},{"key":"e_1_2_9_5_1","doi-asserted-by":"publisher","DOI":"10.1152\/physrev.1985.65.2.310"},{"key":"e_1_2_9_6_1","doi-asserted-by":"publisher","DOI":"10.1113\/jphysiol.1959.sp006278"},{"key":"e_1_2_9_7_1","doi-asserted-by":"publisher","DOI":"10.1046\/j.1365-201X.1996.189000.x"},{"key":"e_1_2_9_8_1","first-page":"1","article-title":"Exercise\u2010induced muscle fatigue: the significance of potassium","volume":"593","author":"Sjogaard G","year":"1990","journal-title":"Acta Physiol Scand Suppl"},{"key":"e_1_2_9_9_1","doi-asserted-by":"publisher","DOI":"10.1046\/j.1365-201X.1996.192000.x"},{"key":"e_1_2_9_10_1","doi-asserted-by":"publisher","DOI":"10.1152\/ajpcell.1991.261.2.C195"},{"key":"e_1_2_9_11_1","doi-asserted-by":"publisher","DOI":"10.1126\/science.1101141"},{"key":"e_1_2_9_12_1","doi-asserted-by":"publisher","DOI":"10.1152\/ajpcell.00279.2011"},{"key":"e_1_2_9_13_1","doi-asserted-by":"publisher","DOI":"10.1074\/jbc.M502890200"},{"key":"e_1_2_9_14_1","doi-asserted-by":"publisher","DOI":"10.1001\/archneur.1994.00540230033009"},{"key":"e_1_2_9_15_1","doi-asserted-by":"publisher","DOI":"10.1002\/mus.880100414"},{"key":"e_1_2_9_16_1","doi-asserted-by":"publisher","DOI":"10.1002\/mus.880100709"},{"key":"e_1_2_9_17_1","doi-asserted-by":"publisher","DOI":"10.1126\/science.2173143"},{"key":"e_1_2_9_18_1","doi-asserted-by":"publisher","DOI":"10.1016\/0092-8674(91)90374-8"},{"key":"e_1_2_9_19_1","doi-asserted-by":"publisher","DOI":"10.1016\/0896-6273(92)90203-P"},{"key":"e_1_2_9_20_1","doi-asserted-by":"publisher","DOI":"10.1152\/physrev.1999.79.4.1317"},{"key":"e_1_2_9_21_1","doi-asserted-by":"publisher","DOI":"10.1016\/S0006-3495(93)81045-2"},{"key":"e_1_2_9_22_1","doi-asserted-by":"publisher","DOI":"10.1097\/WCO.0b013e32833cc97e"},{"key":"e_1_2_9_23_1","doi-asserted-by":"publisher","DOI":"10.1007\/s11910-011-0238-3"},{"key":"e_1_2_9_24_1","doi-asserted-by":"publisher","DOI":"10.1212\/01.wnl.0000342387.65477.46"},{"key":"e_1_2_9_25_1","doi-asserted-by":"publisher","DOI":"10.1212\/WNL.0b013e318219fb57"},{"key":"e_1_2_9_26_1","first-page":"343","article-title":"State of the art in hereditary muscle channelopathies","volume":"29","author":"Jurkat\u2010Rott K","year":"2010","journal-title":"Acta Myol"},{"key":"e_1_2_9_27_1","doi-asserted-by":"publisher","DOI":"10.1002\/humu.10063"},{"key":"e_1_2_9_28_1","doi-asserted-by":"publisher","DOI":"10.1038\/ng0493-305"},{"key":"e_1_2_9_29_1","doi-asserted-by":"publisher","DOI":"10.1126\/science.1379744"},{"key":"e_1_2_9_30_1","doi-asserted-by":"publisher","DOI":"10.1093\/brain\/awp294"},{"key":"e_1_2_9_31_1","doi-asserted-by":"publisher","DOI":"10.1034\/j.1399-6576.2003.00116.x"},{"key":"e_1_2_9_32_1","doi-asserted-by":"publisher","DOI":"10.1016\/S0065-2660(08)01002-X"},{"key":"e_1_2_9_33_1","doi-asserted-by":"crossref","first-page":"1345","DOI":"10.2106\/00004623-197052070-00007","article-title":"Myotonia congenita. 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