{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,4,23]],"date-time":"2026-04-23T22:19:44Z","timestamp":1776982784770,"version":"3.51.4"},"reference-count":18,"publisher":"Wiley","issue":"3","license":[{"start":{"date-parts":[[2014,4,24]],"date-time":"2014-04-24T00:00:00Z","timestamp":1398297600000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Pediatric Dermatology"],"published-print":{"date-parts":[[2014,5]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:p>We report six new cases of lipofibromatosis, an uncommon pediatric soft tissue neoplasm. This is the only series of patients to be described since the initial case series of 45 patients that characterized this entity in 2000. The purpose of this study was to characterize the presentation of lipofibromatosis to further define the clinical phenotype of this rare entity. Six patients were diagnosed with lipofibromatosis at our institution from 2000 to 2012. Patient age, sex, and ethnicity were recorded, along with tumor site and size, management, and recurrence data. Half of our patients were younger than 2\u00a0years old at presentation and the other half were school age. Boys and girls were affected with equal frequency. In five of six patients, lipofibromatosis presented in its \u201cclassic\u201d form as a mass on the distal extremities. These tumors typically measured 1 to 2\u00a0cm in diameter, in contrast to case reports in the medical literature highlighting the occurrence of lipofibromatosis of greater size and at varied anatomic sites. The tumors in our series were managed using excision, with recurrence noted in 33%. Lipofibromatosis is an uncommon tumor typically found on the distal extremities of infants, although it can appear in various sizes and locations. It should be considered in the differential diagnosis of pediatric soft tissue neoplasms.<\/jats:p>","DOI":"10.1111\/pde.12335","type":"journal-article","created":{"date-parts":[[2014,4,24]],"date-time":"2014-04-24T11:40:50Z","timestamp":1398339650000},"page":"298-304","source":"Crossref","is-referenced-by-count":32,"title":["Lipofibromatosis: An Institutional and Literature Review of an Uncommon Entity"],"prefix":"10.1111","volume":"31","author":[{"given":"Markus D.","family":"Boos","sequence":"first","affiliation":[{"name":"Department of Dermatology Perelman School of Medicine University of Pennsylvania Philadelphia Pennsylvania"},{"name":"Department of Pediatrics Perelman School of Medicine University of Pennsylvania Philadelphia Pennsylvania"},{"name":"Section of Dermatology Children's Hospital of Philadelphia Philadelphia Pennsylvania"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Kudakwashe R.","family":"Chikwava","sequence":"additional","affiliation":[{"name":"Department of Pathology and Laboratory Medicine Children's Hospital of Philadelphia Philadelphia Pennsylvania"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"John P.","family":"Dormans","sequence":"additional","affiliation":[{"name":"Department of Orthopedic Surgery Perelman School of Medicine University of Pennsylvania Philadelphia Pennsylvania"},{"name":"Department of Orthopedic Surgery Children's Hospital of Philadelphia Philadelphia Pennsylvania"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Nancy A.","family":"Chauvin","sequence":"additional","affiliation":[{"name":"Department of Pediatrics Children's Hospital of Philadelphia Philadelphia Pennsylvania"},{"name":"Division of Radiology Children's Hospital of Philadelphia Philadelphia Pennsylvania"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Melinda","family":"Jen","sequence":"additional","affiliation":[{"name":"Department of Dermatology Perelman School of Medicine University of Pennsylvania Philadelphia Pennsylvania"},{"name":"Department of Pediatrics Perelman School of Medicine University of Pennsylvania Philadelphia Pennsylvania"},{"name":"Section of Dermatology Children's Hospital of Philadelphia Philadelphia 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