{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,9,20]],"date-time":"2025-09-20T20:15:16Z","timestamp":1758399316384,"version":"3.37.3"},"reference-count":15,"publisher":"Wiley","issue":"6","license":[{"start":{"date-parts":[[2018,9,14]],"date-time":"2018-09-14T00:00:00Z","timestamp":1536883200000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"funder":[{"name":"Walloon Excellence in Lifesciences and Biotechnology (WELBIO), University of Louvain, Brussels, Belgium"}],"content-domain":{"domain":["onlinelibrary.wiley.com"],"crossmark-restriction":true},"short-container-title":["Pediatric Dermatology"],"published-print":{"date-parts":[[2018,11]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:p>We herein report the case of a 3\u2010year\u2010old girl with atypical congenital right upper limb lymphedema who developed an angiosarcoma. Only a few cases have been reported following congenital form of lymphedema and only 4 in such a young child. We also summarize all cases of angiosarcoma associated with congenital lymphedema reported in the literature.<\/jats:p>","DOI":"10.1111\/pde.13664","type":"journal-article","created":{"date-parts":[[2018,9,14]],"date-time":"2018-09-14T20:49:34Z","timestamp":1536958174000},"update-policy":"https:\/\/doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":7,"title":["Angiosarcoma arising from congenital primary lymphedema"],"prefix":"10.1111","volume":"35","author":[{"given":"Pauline","family":"Janssens","sequence":"first","affiliation":[{"name":"Department of Dermatology Cliniques Universitaires Saint\u2010Luc Brussels Belgium"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0003-1210-6112","authenticated-orcid":false,"given":"Val\u00e9rie","family":"Dekeuleneer","sequence":"additional","affiliation":[{"name":"Department of Dermatology Cliniques Universitaires Saint\u2010Luc Brussels 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