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We present a case of an 18\u2010year\u2010old female with a past medical history of growth failure, immunoglobulin A\u00a0nephropathy, and inflammatory arthritis who presented to a pediatric dermatology clinic with findings of acne, psoriasiform dermatitis, and hidradenitis suppurativa, whose clinical, genetic, and laboratory findings were most consistent with PAMI syndrome. We conducted a literature review to better characterize this rare condition in the context of dermatologic findings. Recognition of the distinctive skin findings seen in PAMI syndrome can help distinguish it from other inflammatory disorders, enabling expedited diagnosis and treatment.<\/jats:p>","DOI":"10.1111\/pde.15669","type":"journal-article","created":{"date-parts":[[2024,7,5]],"date-time":"2024-07-05T15:44:17Z","timestamp":1720194257000},"page":"1179-1182","update-policy":"https:\/\/doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":0,"title":["<scp>PSTPIP1<\/scp>\u2010associated myeloid\u2010related proteinemia inflammatory (PAMI) syndrome: <scp>A<\/scp> case report and review of the literature"],"prefix":"10.1111","volume":"41","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-2862-0805","authenticated-orcid":false,"given":"Megan M.","family":"Tran","sequence":"first","affiliation":[{"name":"Warren Alpert Medical School of Brown University  Providence Rhode Island USA"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Pallavi 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