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Given that skin findings are often the earliest and most recognizable signs of AOS, dermatologists play an important role in early diagnosis, enabling prompt genetic evaluation and coordinated multidisciplinary care. However, the syndrome's varied inheritance patterns and heterogeneous presentation contribute to a broad range of severity and clinical manifestations, posing challenges in both recognition and management. This review explores the clinical presentation, diagnostic criteria, and management strategies for AOS, with a particular focus on its cutaneous manifestations.<\/jats:p>","DOI":"10.1111\/pde.16042","type":"journal-article","created":{"date-parts":[[2025,8,28]],"date-time":"2025-08-28T11:50:43Z","timestamp":1756381843000},"page":"939-945","update-policy":"https:\/\/doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":2,"title":["Cutaneous Features of Adams\u2010Oliver Syndrome: Diagnosis, Differentiation, and Management"],"prefix":"10.1111","volume":"42","author":[{"ORCID":"https:\/\/orcid.org\/0009-0002-7495-9188","authenticated-orcid":false,"given":"Sabrina","family":"Yang","sequence":"first","affiliation":[{"name":"Faculty of Medicine University of Ottawa  Ottawa Ontario Canada"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0001-7808-3369","authenticated-orcid":false,"given":"Joseph 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