{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,7,12]],"date-time":"2025-07-12T22:51:46Z","timestamp":1752360706670},"reference-count":10,"publisher":"Wiley","issue":"3","license":[{"start":{"date-parts":[[2014,6,3]],"date-time":"2014-06-03T00:00:00Z","timestamp":1401753600000},"content-version":"vor","delay-in-days":2,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Pediatrics International"],"published-print":{"date-parts":[[2014,6]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:p>Chromosomal abnormalities as well as non\u2010cardiac anomalies have been identified as independent risk factors for surgical morbidity and mortality in <jats:styled-content style=\"fixed-case\">F<\/jats:styled-content>ontan palliation. The combination of malformations consisting of pulmonary hypoplasia, agonadism (sex reversal), omphalocele, and diaphragmatic defect is compatible with pulmonary artery and lung hypoplasia, agonadism, omphalocele, and diaphragmatic defect (<jats:styled-content style=\"fixed-case\">PAGOD<\/jats:styled-content>). Most cases have been associated with cardiac disease, particularly hypoplastic left heart syndrome (<jats:styled-content style=\"fixed-case\">HLHS<\/jats:styled-content>) that is potentially destined for <jats:styled-content style=\"fixed-case\">F<\/jats:styled-content>ontan palliation. Reported herein is the case of a <jats:styled-content style=\"fixed-case\">J<\/jats:styled-content>apanese female infant diagnosed with <jats:styled-content style=\"fixed-case\">PAGOD<\/jats:styled-content> syndrome along with <jats:styled-content style=\"fixed-case\">HLHS<\/jats:styled-content> (mitral atresia and aortic atresia), in whom intractable respiratory failure manifested as bilateral eventration of the diaphragm and presumed right lung hypoplasia. These characteristic pulmonary lesions associated with the syndrome precluded use of the <jats:styled-content style=\"fixed-case\">F<\/jats:styled-content>ontan pathway.<\/jats:p>","DOI":"10.1111\/ped.12280","type":"journal-article","created":{"date-parts":[[2014,6,4]],"date-time":"2014-06-04T03:19:16Z","timestamp":1401851956000},"page":"422-424","source":"Crossref","is-referenced-by-count":5,"title":["Hypoplastic left heart syndrome in <scp>PAGOD<\/scp> syndrome"],"prefix":"10.1111","volume":"56","author":[{"given":"Kazuhiro","family":"Takahashi","sequence":"first","affiliation":[{"name":"Department of Pediatric Cardiology Okinawa Children's Medical Center  Okinawa Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Akira","family":"Miyake","sequence":"additional","affiliation":[{"name":"Department of Pediatric Cardiology Okinawa Children's Medical Center  Okinawa Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Mami","family":"Nakayashiro","sequence":"additional","affiliation":[{"name":"Department of Pediatric Cardiology Okinawa Children's Medical Center  Okinawa Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"311","published-online":{"date-parts":[[2014,6,3]]},"reference":[{"key":"e_1_2_5_2_1","doi-asserted-by":"publisher","DOI":"10.1002\/ajmg.1320410420"},{"key":"e_1_2_5_3_1","doi-asserted-by":"publisher","DOI":"10.1002\/ajmg.10262"},{"key":"e_1_2_5_4_1","doi-asserted-by":"publisher","DOI":"10.1136\/jmg.37.4.315"},{"key":"e_1_2_5_5_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.ijcard.2005.11.068"},{"key":"e_1_2_5_6_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.jtcvs.2005.09.030"},{"key":"e_1_2_5_7_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.athoracsur.2010.02.004"},{"key":"e_1_2_5_8_1","doi-asserted-by":"publisher","DOI":"10.1161\/CIRCULATIONAHA.111.064113"},{"key":"e_1_2_5_9_1","doi-asserted-by":"publisher","DOI":"10.1007\/s00246-009-9479-1"},{"key":"e_1_2_5_10_1","doi-asserted-by":"publisher","DOI":"10.1007\/s100249900056"},{"key":"e_1_2_5_11_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.jtcvs.2008.09.058"}],"container-title":["Pediatrics International"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.wiley.com\/onlinelibrary\/tdm\/v1\/articles\/10.1111%2Fped.12280","content-type":"unspecified","content-version":"vor","intended-application":"text-mining"},{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/pdf\/10.1111\/ped.12280","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2023,9,29]],"date-time":"2023-09-29T20:25:34Z","timestamp":1696019134000},"score":1,"resource":{"primary":{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/10.1111\/ped.12280"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2014,6]]},"references-count":10,"journal-issue":{"issue":"3","published-print":{"date-parts":[[2014,6]]}},"alternative-id":["10.1111\/ped.12280"],"URL":"https:\/\/doi.org\/10.1111\/ped.12280","archive":["Portico"],"relation":{},"ISSN":["1328-8067","1442-200X"],"issn-type":[{"value":"1328-8067","type":"print"},{"value":"1442-200X","type":"electronic"}],"subject":[],"published":{"date-parts":[[2014,6]]}}}