{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,5,13]],"date-time":"2026-05-13T05:00:27Z","timestamp":1778648427357,"version":"3.51.4"},"reference-count":13,"publisher":"Wiley","issue":"6","license":[{"start":{"date-parts":[[2013,6,17]],"date-time":"2013-06-17T00:00:00Z","timestamp":1371427200000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Pediatric Transplantation"],"published-print":{"date-parts":[[2013,9]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:p>WAS is a severe X\u2010linked recessive disorder characterized by microthrombocytopenia, eczema, and immunodeficiency. A six\u2010yr\u2010old boy with <jats:styled-content style=\"fixed-case\">WAS<\/jats:styled-content> diagnosed as B\u2010cell <jats:styled-content style=\"fixed-case\">NHL<\/jats:styled-content> (Stage <jats:styled-content style=\"fixed-case\">III<\/jats:styled-content>) localized in the liver who underwent successful <jats:styled-content style=\"fixed-case\">HSCT<\/jats:styled-content> from <jats:styled-content style=\"fixed-case\">HLA<\/jats:styled-content>\u2010one antigen mismatch sibling donor has been presented here. His conditioning regimen included <jats:styled-content style=\"fixed-case\">ATG<\/jats:styled-content>, busulfan, and fludarabine. He received 2.3\u00a0\u00d7\u00a010<jats:sup>6<\/jats:sup>\/kg <jats:styled-content style=\"fixed-case\">CD<\/jats:styled-content> 34(+) stem cells and 11\u00a0\u00d7\u00a010<jats:sup>8<\/jats:sup>\/kg nucleated cells at day 0. Neutrophil engraftment was achieved at day +14 and platelet engraftment at day +20. He has been in CR for more than two\u00a0yr after transplantation. Thus, <jats:styled-content style=\"fixed-case\">HSCT<\/jats:styled-content> is an effective treatment for children with <jats:styled-content style=\"fixed-case\">WAS<\/jats:styled-content> even after development of lymphoma.<\/jats:p>","DOI":"10.1111\/petr.12114","type":"journal-article","created":{"date-parts":[[2013,6,17]],"date-time":"2013-06-17T08:20:28Z","timestamp":1371457228000},"source":"Crossref","is-referenced-by-count":7,"title":["Successful allogeneic hemopoietic stem cell transplantation in a case of Wiskott\u2013Aldrich syndrome and non\u2010Hodgkin lymphoma"],"prefix":"10.1111","volume":"17","author":[{"given":"Betul","family":"Tavil","sequence":"first","affiliation":[{"name":"Department of Pediatric Hematology Ankara Children's Hematology and Oncology Hospital Diskapi Ankara Turkey"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Arzu Yazal","family":"Erdem","sequence":"additional","affiliation":[{"name":"Department of Pediatric Hematology Ankara Children's Hematology and Oncology Hospital Diskapi Ankara Turkey"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Fatih","family":"Azik","sequence":"additional","affiliation":[{"name":"Department of Pediatric Hematology Ankara Children's Hematology and Oncology Hospital Diskapi Ankara Turkey"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Pamir","family":"Isik","sequence":"additional","affiliation":[{"name":"Department of Pediatric Hematology Ankara Children's Hematology and Oncology Hospital Diskapi Ankara Turkey"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Ayse","family":"Metin","sequence":"additional","affiliation":[{"name":"Department of Pediatric Immunology Ankara Children's Hematology and Oncology Hospital Diskapi Ankara Turkey"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Suna","family":"Emir","sequence":"additional","affiliation":[{"name":"Department of Pediatric Oncology Ankara Children's Hematology and Oncology Hospital Diskapi Ankara Turkey"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Duygu","family":"Uckan","sequence":"additional","affiliation":[{"name":"Department of Pediatric Hematology Ankara Children's Hematology and Oncology Hospital Diskapi Ankara Turkey"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Bahattin","family":"Tunc","sequence":"additional","affiliation":[{"name":"Department of Pediatric Hematology Ankara Children's Hematology and Oncology Hospital Diskapi Ankara Turkey"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"311","published-online":{"date-parts":[[2013,6,17]]},"reference":[{"key":"e_1_2_5_2_1","doi-asserted-by":"publisher","DOI":"10.1002\/pbc.23393"},{"key":"e_1_2_5_3_1","doi-asserted-by":"publisher","DOI":"10.1182\/blood-2007-03-076679"},{"key":"e_1_2_5_4_1","doi-asserted-by":"publisher","DOI":"10.1385\/CRIAI:20:1:61"},{"key":"e_1_2_5_5_1","doi-asserted-by":"publisher","DOI":"10.1016\/j.jaci.2006.02.005"},{"key":"e_1_2_5_6_1","doi-asserted-by":"publisher","DOI":"10.3109\/07357908509039813"},{"key":"e_1_2_5_7_1","unstructured":"EBMT\/ESID Guidelines for Haematopoietic Stem Cell Transplantation for Primary Immunodeficiencies. Available at:http:\/\/www.esid.org\/downloads\/bmt_guidelines_2011.pdf. 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