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The immunodeficiency is progressive with normal immune functions at birth, but then, T\u2010cell deficiency with variable B\u2010cell functions usually presents by the age of two\u00a0yr. The only curative treatment for <jats:styled-content style=\"fixed-case\">PNP<\/jats:styled-content> deficiency is hematopoietic stem cell transplantation. Here, we present a 13\u2010yr\u2010old girl with late\u2010onset <jats:styled-content style=\"fixed-case\">PNP<\/jats:styled-content> deficiency. Despite many complications of infections, she was successfully transplanted with a reduced intensity\u2010conditioning regimen from an <jats:styled-content style=\"fixed-case\">HLA<\/jats:styled-content>\u2010identical unrelated donor.<\/jats:p>","DOI":"10.1111\/petr.12413","type":"journal-article","created":{"date-parts":[[2014,12,17]],"date-time":"2014-12-17T06:18:56Z","timestamp":1418797136000},"source":"Crossref","is-referenced-by-count":10,"title":["A successful unrelated peripheral blood stem cell transplantation with reduced intensity\u2010conditioning regimen in a patient with late\u2010onset purine nucleoside phosphorylase deficiency"],"prefix":"10.1111","volume":"19","author":[{"given":"Fatih","family":"Celmeli","sequence":"first","affiliation":[{"name":"Department of Pediatric Allergy\u2010Immunology Antalya Education and Research Hospital Antalya 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