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We investigated whether this diagnosis per se, compared to other chronic liver diseases (OCLD<\/jats:styled-content>), had an influence on patient survival. Data from 421 Scandinavian children, 194 with BA<\/jats:styled-content> and 227 with OCLD<\/jats:styled-content>, listed for LT<\/jats:styled-content> between 1990 and 2010 were analyzed. The intention\u2010to\u2010treat survival and influencing risk factors were studied. Patients with BA<\/jats:styled-content> had higher risk of death after listing than patients with OCLD<\/jats:styled-content>. The youngest (<1\u00a0year) and smallest (<10\u00a0kg) children with the highest bilirubin (>510\u00a0\u03bcmol\/L), highest INR<\/jats:styled-content> (>1.6), and highest PELD<\/jats:styled-content> score (>20) listed during 1990s had the worst outcome. Given the same PELD<\/jats:styled-content> score, patients with BA<\/jats:styled-content> had higher risk of death than patients with OCLD<\/jats:styled-content>. For adolescents, low weight\/BMI<\/jats:styled-content> was the only prognostic marker. Impaired intention\u2010to\u2010treat survival in patients with BA<\/jats:styled-content> was mainly explained by more advanced liver disease in younger ages and higher proportion of young children in the BA<\/jats:styled-content> group rather than diagnosis per se. PELD<\/jats:styled-content> score predicted death, but seemed to underestimate the severity of liver disease in patients with BA<\/jats:styled-content>. Poor nutritional status and severe cholestasis had negative impact on survival, supporting the \u201csickest children first\u201d allocation policy and correction of malnutrition before surgery.<\/jats:p>","DOI":"10.1111\/petr.12851","type":"journal-article","created":{"date-parts":[[2016,12,13]],"date-time":"2016-12-13T08:12:55Z","timestamp":1481616775000},"source":"Crossref","is-referenced-by-count":11,"title":["Impaired intention\u2010to\u2010treat survival after listing for liver transplantation in children with biliary atresia compared to other chronic liver diseases: 20\u00a0years\u2019 experience from the Nordic countries"],"prefix":"10.1111","volume":"21","author":[{"given":"S.","family":"Malenicka","sequence":"first","affiliation":[{"name":"Department of Pediatric Gastroenterology Hepatology and Nutrition Astrid Lindgren Children's Hospital CLINTEC Karolinska Institute Karolinska University Hospital Huddinge Stockholm Sweden"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"B.\u2010G.","family":"Ericzon","sequence":"additional","affiliation":[{"name":"Division of Transplantation Surgery CLINTEC Karolinska Institute Karolinska University Hospital Huddinge Stockholm Sweden"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"M. 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