{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,9,25]],"date-time":"2025-09-25T18:16:02Z","timestamp":1758824162514,"version":"3.41.2"},"reference-count":21,"publisher":"Wiley","issue":"3","license":[{"start":{"date-parts":[[2018,2,19]],"date-time":"2018-02-19T00:00:00Z","timestamp":1518998400000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"funder":[{"DOI":"10.13039\/501100001691","name":"Japan Society for the Promotion of Science","doi-asserted-by":"publisher","award":["JP15K21365"],"award-info":[{"award-number":["JP15K21365"]}],"id":[{"id":"10.13039\/501100001691","id-type":"DOI","asserted-by":"publisher"}]}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Pediatric Transplantation"],"published-print":{"date-parts":[[2018,5]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:p>Children with single ventricle physiology have complete mixing of the pulmonary and systemic circulations, requiring staged procedures to achieve a separation of these circulations, or Fontan circulation. The single ventricle physiology significantly increases the risk of mortality in children undergoing non\u2010cardiac surgery. As liver transplantation for patients with single ventricle physiology is particularly challenging, only a few reports have been published. We herein report a case of successful LDLTx for an 8\u2010month\u2010old pediatric patient with biliary atresia, heterotaxy, and complex heart disease of single ventricle physiology. The cardiac anomalies included total anomalous pulmonary venous return type <jats:styled-content style=\"fixed-case\">II<\/jats:styled-content>b, intermediate atrioventricular septal defect, tricuspid regurgitation grade <jats:styled-content style=\"fixed-case\">III<\/jats:styled-content>, coarctation of aorta, interrupted inferior vena cava, bilateral superior vena cava, and polysplenia syndrome. Following <jats:styled-content style=\"fixed-case\">LDLT<\/jats:styled-content>x, the patient sequentially underwent total cavopulmonary shunt\u00a0+\u00a0Damus\u2010Kaye\u2010Stansel at 3\u00a0years of age and extracardiac total cavopulmonary connection (<jats:styled-content style=\"fixed-case\">EC<\/jats:styled-content>\u2010<jats:styled-content style=\"fixed-case\">TCPC<\/jats:styled-content>) completion at 5\u00a0years of age; 7\u00a0years have now passed since <jats:styled-content style=\"fixed-case\">LDLT<\/jats:styled-content>x (2\u00a0years post\u2013<jats:styled-content style=\"fixed-case\">EC<\/jats:styled-content>\u2010<jats:styled-content style=\"fixed-case\">TCPC<\/jats:styled-content>). We describe the details of the management of <jats:styled-content style=\"fixed-case\">LT<\/jats:styled-content>x in the presence of cardiac anomalies and report the long\u2010term cardiac and liver function, from peri\u2010<jats:styled-content style=\"fixed-case\">LDLT<\/jats:styled-content>x through <jats:styled-content style=\"fixed-case\">EC<\/jats:styled-content>\u2010<jats:styled-content style=\"fixed-case\">TCPC<\/jats:styled-content> completion.<\/jats:p>","DOI":"10.1111\/petr.13118","type":"journal-article","created":{"date-parts":[[2018,2,21]],"date-time":"2018-02-21T18:21:37Z","timestamp":1519237297000},"source":"Crossref","is-referenced-by-count":6,"title":["Successful management of living donor liver transplantation for biliary atresia with single ventricle physiology\u2014from peri\u2010transplant through total cavopulmonary connection: A\u00a0case report"],"prefix":"10.1111","volume":"22","author":[{"ORCID":"https:\/\/orcid.org\/0000-0001-6059-7660","authenticated-orcid":false,"given":"Yohei","family":"Yamada","sequence":"first","affiliation":[{"name":"Department of Pediatric Surgery Keio University School of Medicine  Tokyo Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Ken","family":"Hoshino","sequence":"additional","affiliation":[{"name":"Department of Pediatric Surgery Keio University School of Medicine  Tokyo Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Takayuki","family":"Oyanagi","sequence":"additional","affiliation":[{"name":"Department of Pediatrics Keio University School of Medicine  Tokyo Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Ryohei","family":"Gatayama","sequence":"additional","affiliation":[{"name":"Department of Pediatrics Keio University School of Medicine  Tokyo 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Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Masahiro","family":"Shinoda","sequence":"additional","affiliation":[{"name":"Department of Surgery Keio University School of Medicine  Tokyo Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Kentaro","family":"Matsubara","sequence":"additional","affiliation":[{"name":"Department of Surgery Keio University School of Medicine  Tokyo Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Hideaki","family":"Obara","sequence":"additional","affiliation":[{"name":"Department of Surgery Keio University School of Medicine  Tokyo Japan"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"given":"Ryo","family":"Aeba","sequence":"additional","affiliation":[{"name":"Department of Cardiac Surgery Keio University School of Medicine  Tokyo 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