{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2025,5,14]],"date-time":"2025-05-14T02:01:33Z","timestamp":1747188093387,"version":"3.40.5"},"reference-count":35,"publisher":"Wiley","issue":"4","license":[{"start":{"date-parts":[[2024,2,20]],"date-time":"2024-02-20T00:00:00Z","timestamp":1708387200000},"content-version":"vor","delay-in-days":0,"URL":"http:\/\/onlinelibrary.wiley.com\/termsAndConditions#vor"}],"content-domain":{"domain":["onlinelibrary.wiley.com"],"crossmark-restriction":true},"short-container-title":["Special Care in Dentistry"],"published-print":{"date-parts":[[2024,7]]},"abstract":"<jats:title>Abstract<\/jats:title><jats:sec><jats:title>Background<\/jats:title><jats:p>Woolly Hair Syndrome (WHS) is a rare birth condition that affects the structure of hair in non\u2010black people. The pathogenesis is not yet defined. It is postulated that the hair follicle's desmosomes (specifically desmoplaquine, placoglobin and placofilin\u20101, which are cell structural proteins that keep the adhesion among close cells) would be altered in this pathology, leading to fragility in the cellular union. It is subdivided into two large groups: the localized or circumscribed variant and the generalized variant. From birth or first months of life, patients with WHS are clinically characterized by the presence of a portion or entire scalp area of very short frizzy hair, usually of a smaller diameter, brittle and lighter color. The most frequent skin manifestations are pilar keratosis and palmo\u2010plantar keratodermia. The diagnosis is based on the clinical findings, and it is facilitated by trichotoscopic examination. However, a definitive diagnosis of WHS requires genetic testing. Oral agenesis, enamel defects (such as hypomineralization), atypical caries, dental inclusion, and malformed pin\u2010shaped teeth may occur.<\/jats:p><\/jats:sec><jats:sec><jats:title>Objective<\/jats:title><jats:p>To describe an aesthetic alternative of oral rehabilitation using the mock\u2010up technique in a patient with WHS.<\/jats:p><\/jats:sec><jats:sec><jats:title>Clinical case<\/jats:title><jats:p>A 5\u2010year\u2010old female patient diagnosed with WHS from the National Institute of Child Health<\/jats:p><\/jats:sec><jats:sec><jats:title>Nihch<\/jats:title><jats:p>Bre\u00f1a, Lima, who was referred from the Genetic service to the Pediatric Dentistry service in order to screen outbreaks of infection associated with odontogenic origin and dental anomalies. At the ectoscopy, a patient with short capillary length, brittle and curly hair, dry skin, and nail dystrophy was observed. At the intraoral clinical examination, anterior pieces of 52, 51, 61, 62, and enamel hypomineralization were observed in all teeth. The radiographic examination showed agenesis of parts 41, 34, and 45. Integral dental treatment was performed in the operating room under general anesthesia due to the complexity of the case. Pulpectomy in pieces 52, 51, 61, 62, post of composite resin, and rehabilitation with supra\u2010nanow filling resin using the mock\u2010up technique were proposed as alternative treatments.<\/jats:p><\/jats:sec><jats:sec><jats:title>Conclusion<\/jats:title><jats:p>The making of supra\u2010nano filling resin\u2010based crowns using the mock\u2010up technique is an alternative treatment for aesthetic oral rehabilitation in deciduous dentition of patients with WHS. The aesthetic treatment was achieved using supra nano\u2010filling resins. After 12 months of dental treatment, a favorable response was observed, improving the chewing, phonation and aesthetics of the patient.<\/jats:p><\/jats:sec>","DOI":"10.1111\/scd.12979","type":"journal-article","created":{"date-parts":[[2024,2,20]],"date-time":"2024-02-20T10:59:16Z","timestamp":1708426756000},"page":"1065-1073","update-policy":"https:\/\/doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":0,"title":["Aesthetic oral rehabilitation of the upper\u2010anterior sector with supra\u2010nano filling resin in a patient with woolly hair syndrome: case report"],"prefix":"10.1111","volume":"44","author":[{"given":"Patricia Nataly","family":"Conto Quispe","sequence":"first","affiliation":[{"name":"Faculty of Dentistry Universidad Nacional Mayor de San Marcos  Lima Peru"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-2585-3013","authenticated-orcid":false,"given":"Akemy Celeste","family":"Tapia Martinez","sequence":"additional","affiliation":[{"name":"Faculty of Dentistry, Universidad Nacional Mayor de San Marcos, Lima Peru and Dentistry Department National Police Hospital of Peru Luis N. Saenz  Lima Peru"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-3687-2180","authenticated-orcid":false,"given":"Henry Jes\u00fas","family":"Vilcapoma Guerra","sequence":"additional","affiliation":[{"name":"Faculty of Dentistry, Universidad Nacional Mayor de San Marcos, Lima, Peru and Dentistry Department Central Hospital of the Peruvian Air Force  Lima Peru"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-8021-0563","authenticated-orcid":false,"given":"Lenny","family":"Lavado Garc\u00eda","sequence":"additional","affiliation":[{"name":"Faculty of Dentistry, Universidad Nacional Mayor de San Marcos, Lima Peru and Dentistry Department, Instituto Nacional de Salud del Ni\u00f1o  Lima Peru"}],"role":[{"role":"author","vocabulary":"crossref"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-2590-6736","authenticated-orcid":false,"given":"Gilmer","family":"Torres Ramos","sequence":"additional","affiliation":[{"name":"Faculty of Dentistry Universidad Nacional Mayor de San Marcos  Lima Peru"}],"role":[{"role":"author","vocabulary":"crossref"}]}],"member":"311","published-online":{"date-parts":[[2024,2,20]]},"reference":[{"key":"e_1_2_7_2_1","first-page":"157","article-title":"Familial woolly hair","volume":"68","author":"Prasad GK","year":"2002","journal-title":"Indian J Dermatol Venereol Leprol"},{"key":"e_1_2_7_3_1","first-page":"450","article-title":"Familial woolly hair disease","volume":"47","author":"Harish R","year":"2010","journal-title":"Indian Pediatr"},{"doi-asserted-by":"publisher","key":"e_1_2_7_4_1","DOI":"10.4067\/S0370-41062013000600010"},{"key":"e_1_2_7_5_1","first-page":"3","article-title":"Diagnosis of woolly hair using trichoscopy. Hindawi case reports in dermatological","author":"Mathur M","year":"2019","journal-title":"Medicine"},{"issue":"2","key":"e_1_2_7_6_1","first-page":"160","article-title":"Woolly hair. Clinical and general aspects","volume":"60","author":"Hutchinson PE","year":"1974","journal-title":"Trans St Johns Hosp Dermatol Soc"},{"doi-asserted-by":"publisher","key":"e_1_2_7_7_1","DOI":"10.1016\/j.jdermsci.2015.03.006"},{"doi-asserted-by":"publisher","key":"e_1_2_7_8_1","DOI":"10.1016\/j.jaad.2005.01.092"},{"doi-asserted-by":"publisher","key":"e_1_2_7_9_1","DOI":"10.5152\/akd.2014.5413"},{"doi-asserted-by":"publisher","key":"e_1_2_7_10_1","DOI":"10.1136\/jmedgenet-2015-103403"},{"doi-asserted-by":"publisher","key":"e_1_2_7_11_1","DOI":"10.4103\/0974-7753.179400"},{"doi-asserted-by":"publisher","key":"e_1_2_7_12_1","DOI":"10.4103\/2229-5178.115524"},{"doi-asserted-by":"publisher","key":"e_1_2_7_13_1","DOI":"10.1046\/j.1365-2133.2001.04303.x"},{"doi-asserted-by":"publisher","key":"e_1_2_7_14_1","DOI":"10.1016\/j.joms.2011.05.024"},{"doi-asserted-by":"publisher","key":"e_1_2_7_15_1","DOI":"10.1007\/s13555-019-0313-2"},{"doi-asserted-by":"publisher","key":"e_1_2_7_16_1","DOI":"10.1016\/j.det.2013.06.007"},{"doi-asserted-by":"publisher","key":"e_1_2_7_17_1","DOI":"10.1111\/j.1468-3083.2012.04526.x"},{"doi-asserted-by":"publisher","key":"e_1_2_7_18_1","DOI":"10.3109\/14764172.2013.764436"},{"issue":"3","key":"e_1_2_7_19_1","first-page":"185","article-title":"Evoluci\u00f3n de las coronas como material de restauraci\u00f3n en dentici\u00f3n temporal: revisi\u00f3n de la literatura","volume":"18","author":"Virol\u00e9s M","year":"2010","journal-title":"Odontol pedi\u00e1tr"},{"key":"e_1_2_7_20_1","first-page":"163","article-title":"Restoring primary anterior teeth: updated for","volume":"37","author":"Aggoner WF","year":"2014","journal-title":"Pediatr Dent"},{"issue":"5","key":"e_1_2_7_21_1","first-page":"377","article-title":"Clinical outcomes for primary anterior teeth treated with preveneered stainless steel crowns","volume":"29","author":"MacLean JK","year":"2007","journal-title":"Pediatr Dent"},{"issue":"2","key":"e_1_2_7_22_1","first-page":"1","article-title":"Batu Can Yaman And F\u00fcsun \u00d6zer. Surface roughness and morphology of resin composites polished with two\u2010step polishing systems","volume":"33","author":"Sa Esra","year":"2014","journal-title":"Dent Mater J"},{"doi-asserted-by":"publisher","key":"e_1_2_7_23_1","DOI":"10.4012\/dmj.2015-126"},{"doi-asserted-by":"publisher","key":"e_1_2_7_24_1","DOI":"10.1111\/jerd.12671"},{"doi-asserted-by":"publisher","key":"e_1_2_7_25_1","DOI":"10.1016\/j.dental.2021.01.023"},{"doi-asserted-by":"publisher","key":"e_1_2_7_26_1","DOI":"10.12968\/denu.2013.40.4.297"},{"issue":"5","key":"e_1_2_7_27_1","first-page":"907","article-title":"[Clinical performance of rensin\u2010bonded composite strip crowns in primary incisors]","volume":"52","author":"Chen XX","year":"2020","journal-title":"Beijing Da Xue Xue Bao Yi Xue Ban"},{"doi-asserted-by":"publisher","key":"e_1_2_7_28_1","DOI":"10.15381\/os.v18i2.11520"},{"doi-asserted-by":"publisher","key":"e_1_2_7_29_1","DOI":"10.4067\/S0719-01072018000100009"},{"volume-title":"Alternativas de restauraci\u00f3n en dientes deciduos con tratamiento pulpar. [Tesis de pregrado]","year":"2009","author":"Canales IZ","key":"e_1_2_7_30_1"},{"doi-asserted-by":"publisher","key":"e_1_2_7_31_1","DOI":"10.1111\/jerd.12420"},{"doi-asserted-by":"publisher","key":"e_1_2_7_32_1","DOI":"10.1007\/s00784-016-1968-z"},{"doi-asserted-by":"publisher","key":"e_1_2_7_33_1","DOI":"10.3109\/00016351003752395"},{"issue":"3","key":"e_1_2_7_34_1","first-page":"233","article-title":"Resistencia de uni\u00f3n a micro\u2010 cizallamiento del composite de resina a los dientes afectados por hipomineralizaci\u00f3n molar mediante 2 sistemas adhesivos","volume":"28","author":"William V","year":"2006","journal-title":"Pediatr Dent"},{"doi-asserted-by":"publisher","key":"e_1_2_7_35_1","DOI":"10.17796\/1053-4628-41.5.336"},{"doi-asserted-by":"publisher","key":"e_1_2_7_36_1","DOI":"10.1111\/j.1365-263X.2011.01212.x"}],"container-title":["Special Care in Dentistry"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/pdf\/10.1111\/scd.12979","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2024,10,9]],"date-time":"2024-10-09T03:55:19Z","timestamp":1728446119000},"score":1,"resource":{"primary":{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/10.1111\/scd.12979"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2024,2,20]]},"references-count":35,"journal-issue":{"issue":"4","published-print":{"date-parts":[[2024,7]]}},"alternative-id":["10.1111\/scd.12979"],"URL":"https:\/\/doi.org\/10.1111\/scd.12979","archive":["Portico"],"relation":{},"ISSN":["0275-1879","1754-4505"],"issn-type":[{"type":"print","value":"0275-1879"},{"type":"electronic","value":"1754-4505"}],"subject":[],"published":{"date-parts":[[2024,2,20]]},"assertion":[{"value":"2023-10-24","order":0,"name":"received","label":"Received","group":{"name":"publication_history","label":"Publication History"}},{"value":"2024-02-09","order":2,"name":"accepted","label":"Accepted","group":{"name":"publication_history","label":"Publication History"}},{"value":"2024-02-20","order":3,"name":"published","label":"Published","group":{"name":"publication_history","label":"Publication History"}}]}}