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After informed consent, clinical and demographic data were obtained by an interviewer\u2010assisted questionnaire. Computerised case notes and laboratory results, linked to each patient's National Health Index (NHI) number, were also reviewed. In the current analysis, ethnic\u2010specific data was obtained on the prevalence of CVID and its sequelae in NZ. One hundred and eight patients with a diagnosis of CVID were enrolled in the NZCS, comprising approximately 70% of patients known to have CVID in NZ. There was a much greater prevalence of bronchiectasis in M\u0101ori (79%) compared to Caucasian CVID patients (38%). M\u0101ori patients with CVID develop symptoms at a younger age and have an increased number of severe infections prior to diagnosis. M\u0101ori CVID patients with bronchiectasis had a higher prevalence of complete IgA deficiency compared to Caucasian CVID patients with bronchiectasis. In contrast to Caucasian patients with CVID, autoimmune and inflammatory sequelae were much less common in M\u0101ori. This study also demonstrated worsening diagnostic delays in patients with CVID in NZ. The Indigenous M\u0101ori of Aotearoa have a much more aggresssive early\u2010onset, infection\u2010only CVID variant compared to Caucasian New Zealanders.<\/jats:p>","DOI":"10.1111\/sji.70068","type":"journal-article","created":{"date-parts":[[2025,11,21]],"date-time":"2025-11-21T06:12:25Z","timestamp":1763705545000},"update-policy":"https:\/\/doi.org\/10.1002\/crossmark_policy","source":"Crossref","is-referenced-by-count":0,"title":["Common Variable Immune Deficiency Disorders (\n                    <scp>CVID<\/scp>\n                    ) in the Indigenous M\u0101ori of Aotearoa (New Zealand) Are Associated With a High Prevalence of Bronchiectasis and Complete\n                    <scp>IgA<\/scp>\n                    Deficiency"],"prefix":"10.1111","volume":"102","author":[{"ORCID":"https:\/\/orcid.org\/0000-0002-3011-8654","authenticated-orcid":false,"given":"Rohan","family":"Ameratunga","sequence":"first","affiliation":[{"name":"Department of Clinical Immunology Auckland City 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