{"status":"ok","message-type":"work","message-version":"1.0.0","message":{"indexed":{"date-parts":[[2026,6,26]],"date-time":"2026-06-26T05:10:17Z","timestamp":1782450617347,"version":"3.54.5"},"reference-count":23,"publisher":"Frontiers Media SA","issue":"12","license":[{"start":{"date-parts":[[2015,9,1]],"date-time":"2015-09-01T00:00:00Z","timestamp":1441065600000},"content-version":"tdm","delay-in-days":0,"URL":"http:\/\/doi.wiley.com\/10.1002\/tdm_license_1.1"}],"content-domain":{"domain":[],"crossmark-restriction":false},"short-container-title":["Transpl Int"],"published-print":{"date-parts":[[2015,12]]},"DOI":"10.1111\/tri.12677","type":"journal-article","created":{"date-parts":[[2015,8,27]],"date-time":"2015-08-27T09:37:54Z","timestamp":1440668274000},"page":"1447-1450","source":"Crossref","is-referenced-by-count":41,"title":["Reversal of cardiomyopathy in propionic acidemia after liver transplantation: a 10-year follow-up"],"prefix":"10.3389","volume":"28","author":[{"given":"Chiara","family":"Arrizza","sequence":"first","affiliation":[{"name":"Department of Paediatrics; Inselspital; University Hospital Bern; Bern Switzerland"},{"name":"Institute of Clinical Chemistry; Inselspital; University Hospital Bern; Bern Switzerland"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"ORCID":"https:\/\/orcid.org\/0000-0002-4401-2340","authenticated-orcid":false,"given":"Andrea","family":"De Gottardi","sequence":"additional","affiliation":[{"name":"Clinic of Visceral Surgery and Medicine, Hepatology; Inselspital; University Hospital Bern; Bern Switzerland"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Ezio","family":"Foglia","sequence":"additional","affiliation":[{"name":"MD Internal Medicine and Cardiology; Massagno Switzerland"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Matthias","family":"Baumgartner","sequence":"additional","affiliation":[{"name":"Division of Metabolism and Children's Research Center; University Children's Hospital; Zurich Switzerland"},{"name":"radiz - Rare Disease Initiative Zurich; Clinical Research Priority Program for Rare Diseases; University of Zurich; Zurich Switzerland"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Matthias","family":"Gautschi","sequence":"additional","affiliation":[{"name":"Department of Paediatrics; Inselspital; University Hospital Bern; Bern Switzerland"},{"name":"Institute of Clinical Chemistry; Inselspital; University Hospital Bern; Bern Switzerland"}],"role":[{"vocabulary":"crossref","role":"author"}]},{"given":"Jean-Marc","family":"Nuoffer","sequence":"additional","affiliation":[{"name":"Department of Paediatrics; Inselspital; University Hospital Bern; Bern Switzerland"},{"name":"Institute of Clinical Chemistry; Inselspital; University Hospital Bern; Bern Switzerland"}],"role":[{"vocabulary":"crossref","role":"author"}]}],"member":"1965","published-online":{"date-parts":[[2015,9,11]]},"reference":[{"key":"10.1111\/tri.12677-BIB0001|tri12677-cit-0001","doi-asserted-by":"crossref","first-page":"26","DOI":"10.1016\/j.ymgme.2011.08.034","article-title":"Chronic management and health supervision of individuals with propionic acidemia","volume":"105","author":"Sutton","year":"2012","journal-title":"Mol Genet Metab"},{"key":"10.1111\/tri.12677-BIB0002|tri12677-cit-0002","doi-asserted-by":"crossref","first-page":"130","DOI":"10.1186\/s13023-014-0130-8","article-title":"Proposed guidelines for the diagnosis and management of methylmalonic and propionic acidemia","volume":"9","author":"Baumgartner","year":"2014","journal-title":"Orphanet J Rare Dis"},{"key":"10.1111\/tri.12677-BIB0003|tri12677-cit-0003","doi-asserted-by":"crossref","first-page":"441","DOI":"10.1007\/BF01955907","article-title":"Cardiomyopathy in propionic acidaemia","volume":"152","author":"Massoud","year":"1993","journal-title":"Eur J Pediatr"},{"key":"10.1111\/tri.12677-BIB0004|tri12677-cit-0004","doi-asserted-by":"crossref","first-page":"286","DOI":"10.1016\/j.ymgme.2005.04.004","article-title":"Clinical, pathological, and biochemical studies in a patient with propionic acidemia and fatal cardiomyopathy","volume":"85","author":"Mardach","year":"2005","journal-title":"Mol Genet Metab"},{"key":"10.1111\/tri.12677-BIB0005|tri12677-cit-0005","doi-asserted-by":"crossref","first-page":"773","DOI":"10.1111\/j.1399-3046.2006.00569.x","article-title":"Evaluation and management of patients with propionic acidemia undergoing liver transplantation: a comprehensive review","volume":"10","author":"Barshes","year":"2006","journal-title":"Pediatr Transplant"},{"key":"10.1111\/tri.12677-BIB0006|tri12677-cit-0006","doi-asserted-by":"crossref","first-page":"128","DOI":"10.1016\/j.jpeds.2009.07.002","article-title":"Cardiomyopathies in propionic aciduria are reversible after liver transplantation","volume":"156","author":"Romano","year":"2010","journal-title":"J Pediatr"},{"key":"10.1111\/tri.12677-BIB0007|tri12677-cit-0007","doi-asserted-by":"crossref","first-page":"866","DOI":"10.1016\/j.jpeds.2010.12.031","article-title":"Left ventricular assist device as bridge to liver transplantation in a patient with propionic acidemia and cardiogenic shock","volume":"158","author":"Ameloot","year":"2011","journal-title":"J Pediatr"},{"key":"10.1111\/tri.12677-BIB0008|tri12677-cit-0008","unstructured":"FAO Energy and protein requirements. Report of a joint FAO\/WHO\/UNU Expert Consultation 1985 724 1 206"},{"key":"10.1111\/tri.12677-BIB0009|tri12677-cit-0009","doi-asserted-by":"crossref","first-page":"969","DOI":"10.1007\/s00246-007-9160-5","article-title":"Cardiac arrest secondary to long QT(C)in a child with propionic acidemia","volume":"29","author":"Jameson","year":"2008","journal-title":"Pediatr Cardiol"},{"key":"10.1111\/tri.12677-BIB0010|tri12677-cit-0010","doi-asserted-by":"crossref","first-page":"635","DOI":"10.1007\/s10545-013-9600-8","article-title":"Current concepts in organic acidurias: understanding intra- and extracerebral disease manifestation","volume":"36","author":"Kolker","year":"2013","journal-title":"J Inherit Metab Dis"},{"key":"10.1111\/tri.12677-BIB0011|tri12677-cit-0011","doi-asserted-by":"crossref","first-page":"91","DOI":"10.1203\/PDR.0b013e3181a7c270","article-title":"Multiple OXPHOS deficiency in the liver, kidney, heart, and skeletal muscle of patients with methylmalonic aciduria and propionic aciduria","volume":"66","author":"Keyzer","year":"2009","journal-title":"Pediatr Res"},{"key":"10.1111\/tri.12677-BIB0012|tri12677-cit-0012","doi-asserted-by":"crossref","first-page":"150","DOI":"10.1016\/j.mito.2014.07.001","article-title":"Successful reversal of propionic acidaemia associated cardiomyopathy: evidence for low myocardial coenzyme Q10 status and secondary mitochondrial dysfunction as an underlying pathophysiological mechanism","volume":"17","author":"Baruteau","year":"2014","journal-title":"Mitochondrion"},{"issue":"Suppl. 1","key":"10.1111\/tri.12677-BIB0013|tri12677-cit-0013","doi-asserted-by":"crossref","first-page":"S97","DOI":"10.1007\/s10545-009-1084-1","article-title":"Unusual presentation of propionic acidaemia as isolated cardiomyopathy","volume":"32","author":"Lee","year":"2009","journal-title":"J Inherit Metab Dis"},{"issue":"Suppl. 1","key":"10.1111\/tri.12677-BIB0014|tri12677-cit-0014","first-page":"35","article-title":"Cardiomyopathy as the presenting feature in a 15-year-old boy with propionic acidemia","volume":"30","author":"Rhead","year":"2007","journal-title":"J Inherit Metab Dis"},{"key":"10.1111\/tri.12677-BIB0015|tri12677-cit-0015","doi-asserted-by":"crossref","first-page":"295","DOI":"10.1034\/j.1399-3046.2002.02009.x","article-title":"Long-term survival after liver transplantation in children with metabolic disorders","volume":"6","author":"Kayler","year":"2002","journal-title":"Pediatr Transplant"},{"key":"10.1111\/tri.12677-BIB0016|tri12677-cit-0016","doi-asserted-by":"crossref","first-page":"967951","DOI":"10.1155\/2015\/967951","article-title":"Bypass during liver transplantation: anachronism or revival? Liver transplantation using a combined venovenous\/portal venous bypass-experiences with 163 liver transplants in a newly established liver transplantation program","volume":"2015","author":"Mossdorf","year":"2015","journal-title":"Gastroenterol Res Pract"},{"key":"10.1111\/tri.12677-BIB0017|tri12677-cit-0017","doi-asserted-by":"crossref","first-page":"192","DOI":"10.1016\/j.jpeds.2006.11.043","article-title":"Prolonged QTc intervals and decreased left ventricular contractility in patients with propionic acidemia","volume":"150","author":"Baumgartner","year":"2007","journal-title":"J Pediatr"},{"key":"10.1111\/tri.12677-BIB0018|tri12677-cit-0018","doi-asserted-by":"crossref","first-page":"160","DOI":"10.1007\/s00246-005-1129-7","article-title":"Coincidence of long QT syndrome and propionic acidemia","volume":"27","author":"Kakavand","year":"2006","journal-title":"Pediatr Cardiol"},{"key":"10.1111\/tri.12677-BIB0019|tri12677-cit-0019","doi-asserted-by":"crossref","first-page":"274","DOI":"10.1177\/0883073813508812","article-title":"Acute psychosis in propionic acidemia: 2 case reports","volume":"29","author":"Dejean de la Batie","year":"2014","journal-title":"J Child Neurol"},{"key":"10.1111\/tri.12677-BIB0020|tri12677-cit-0020","doi-asserted-by":"crossref","first-page":"578","DOI":"10.1016\/j.neuroscience.2009.08.028","article-title":"Evidence for catabolic pathway of propionate metabolism in CNS: expression pattern of methylmalonyl-CoA mutase and propionyl-CoA carboxylase alpha-subunit in developing and adult rat brain","volume":"164","author":"Ballhausen","year":"2009","journal-title":"Neuroscience"},{"key":"10.1111\/tri.12677-BIB0021|tri12677-cit-0021","doi-asserted-by":"crossref","first-page":"661","DOI":"10.1002\/lt.22279","article-title":"Liver transplantation for propionic acidemia in children","volume":"17","author":"Vara","year":"2011","journal-title":"Liver Transpl"},{"key":"10.1111\/tri.12677-BIB0022|tri12677-cit-0022","doi-asserted-by":"crossref","first-page":"2200","DOI":"10.1111\/j.1600-6143.2007.01899.x","article-title":"Auxiliary liver transplantation for propionic acidemia: a 10-year follow-up","volume":"7","author":"Rela","year":"2007","journal-title":"Am J Transplant"},{"key":"10.1111\/tri.12677-BIB0023|tri12677-cit-0023","doi-asserted-by":"crossref","first-page":"342","DOI":"10.1097\/TP.0b013e31823b72d6","article-title":"Current status of hepatocyte transplantation","volume":"93","author":"Hughes","year":"2012","journal-title":"Transplantation"}],"container-title":["Transplant International"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/api.wiley.com\/onlinelibrary\/tdm\/v1\/articles\/10.1111%2Ftri.12677","content-type":"unspecified","content-version":"vor","intended-application":"text-mining"},{"URL":"http:\/\/onlinelibrary.wiley.com\/wol1\/doi\/10.1111\/tri.12677\/fullpdf","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2022,1,1]],"date-time":"2022-01-01T18:38:20Z","timestamp":1641062300000},"score":1,"resource":{"primary":{"URL":"https:\/\/onlinelibrary.wiley.com\/doi\/10.1111\/tri.12677"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[2015,9,11]]},"references-count":23,"journal-issue":{"issue":"12","published-print":{"date-parts":[[2015,12]]}},"URL":"https:\/\/doi.org\/10.1111\/tri.12677","archive":["Portico"],"relation":{},"ISSN":["0934-0874"],"issn-type":[{"value":"0934-0874","type":"print"}],"subject":[],"published":{"date-parts":[[2015,9,11]]}}}