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K., D'Souza, S. W., Gordon, H., and Scopes, J. W. (1970). Fetal haemoglobin in cord blood as estimated by two different techniques. Journal of Obstetrics and Gynaecology of the British Commonwealth, 77, 238.","journal-title":"Journal of Obstetrics and Gynaecology of the British Commonwealth"},{"key":"ref_2","doi-asserted-by":"crossref","first-page":"868","DOI":"10.1111\/j.1651-2227.1960.tb16097.x","article-title":"Foetal and adult haemoglobin in newborn infants with erythroblastosis foetalis","volume":"49","author":"Brody, S.; Engstrom, L.","year":"1960","unstructured":"Brody, S., and Engstrom, L. (1960). Foetal and adult haemoglobin in newborn infants with erythroblastosis foetalis. Acta Paediatrica, 49, 868.","journal-title":"Acta Paediatrica"},{"key":"ref_3","doi-asserted-by":"crossref","first-page":"850","DOI":"10.1038\/161850a0","article-title":"Foetal haemoglobin and erythroblastosis","volume":"161","author":"Jonxis, J.H.P.","year":"1948","unstructured":"Jonxis, J. H. P. (1948). Foetal haemoglobin and erythroblastosis. Nature (London), 161, 850.","journal-title":"Nature (London)"},{"key":"ref_4","doi-asserted-by":"crossref","first-page":"637","DOI":"10.1007\/BF01481043","article-title":"Demonstration von Fetalem bamoglobin in den Erythrocyten eines Biueausstrichs","volume":"35","author":"Kleihauer, E.; Braun, H.; Betke, K.","year":"1957","unstructured":"Kleihauer, E., Braun, H., and Betke, K. (1957). Demonstration von Fetalem bamoglobin in den Erythrocyten eines Biueausstrichs. Klinische Wochenschrift, 35, 637.","journal-title":"Klinische Wochenschrift"},{"key":"ref_5","doi-asserted-by":"crossref","first-page":"161","DOI":"10.1136\/adc.18.96.161","article-title":"The survival of transfused erythrocytes in haemolytic disease of the newborn","volume":"18","author":"Mollison, P.L.","year":"1943","unstructured":"Mollison, P. L. (1943). The survival of transfused erythrocytes in haemolytic disease of the newborn. Archives of Disease in Childhood, 18, 161. Opp6, T. E., and Fraser, I. D. (1961). Foetal haemoglobin in haemolytic disease of the newborn. Archives of Disease in Childhood. 36, 507.","journal-title":"Archives of Disease in Childhood; Foetal haemoglobin in haemolytic disease of the newborn"},{"key":"ref_6","doi-asserted-by":"crossref","first-page":"1264","DOI":"10.1182\/blood.V4.11.1264.1264","article-title":"Fetal and adult hemaglobins in the blood of infants affected with hemolytic diseases of the newborn","volume":"4","author":"Ponder, E.; Levine, P.","year":"1949","unstructured":"Ponder, E., and Levine, P. (1949). Fetal and adult hemaglobins in the blood of infants affected with hemolytic diseases of the newborn. Blood, 4, 1264.","journal-title":"Blood"},{"key":"ref_7","first-page":"167","article-title":"Fetal and adult hemoglobins in hemolytic disease of the newborn","volume":"87","author":"Schulman, I.; Smith, C.H.","year":"1954","unstructured":"Schulman, I., and Smith, C. H. (1954). Fetal and adult hemoglobins in hemolytic disease of the newborn. American Journal of Diseases of Children, 87, 167.","journal-title":"American Journal of Diseases of Children"},{"key":"ref_8","first-page":"413","article-title":"Studies on abnormal haemoglobins: I. Their demonstration in sickle cell anemia and other hematologic disorders by means of alkali denaturation","volume":"6","author":"Singer, K.; Chernoff, A.I.; Singer, L.","year":"1951","unstructured":"Singer, K., Chernoff, A. I., and Singer, L. (1951). Studies on abnormal haemoglobins: I. Their demonstration in sickle cell anemia and other hematologic disorders by means of alkali denaturation. Blood, 6, 413.","journal-title":"Blood"},{"key":"ref_9","article-title":"Partial Immunodeficiency and Graft-versus-Host Disease If patients with defective cellular immunity are transfused with immunologically competent cells (ICC), graft-versus-host disease (GVHD) may result. It has occurred in several children with severe combined immunodeficiency","volume-title":"but only once in a child with partial immunodeficiency-Wiskott-Aldrich disease","author":"(Douglas and Fudenberg,","year":"1968","unstructured":"Partial Immunodeficiency and Graft-versus-Host Disease If patients with defective cellular immunity are transfused with immunologically competent cells (ICC), graft-versus-host disease (GVHD) may result. It has occurred in several children with severe combined immunodeficiency (Hong, Gatti, and Good, 1968), but only once in a child with partial immunodeficiency-Wiskott-Aldrich disease (Douglas and Fudenberg, 1969)."},{"key":"ref_10","article-title":"The morbid anatomical findings were similar to those in severe combined immunodeficiency which is usually fatal in infancy (Berry, 1970); it is interesting that such findings may be compatible with measurable immunological function. Plasma cells in the marrow, and actively phagocytic macrophages in the marrow and skin, seen in our case, are not usual in severe combined immunodeficiency, and are suggestive of GVHD, though they could be related to her partial immunological function. Other features of GVHD (histiocytic infiltration of the reticuloendothelial system and erythrophagocytosis) were absent. Unfortunately, both the donor and the recipient were female, so we were unable to demonstrate chimerism by chromosome studies","unstructured":"The morbid anatomical findings were similar to those in severe combined immunodeficiency which is usually fatal in infancy (Berry, 1970); it is interesting that such findings may be compatible with measurable immunological function. Plasma cells in the marrow, and actively phagocytic macrophages in the marrow and skin, seen in our case, are not usual in severe combined immunodeficiency, and are suggestive of GVHD, though they could be related to her partial immunological function. Other features of GVHD (histiocytic infiltration of the reticuloendothelial system and erythrophagocytosis) were absent. Unfortunately, both the donor and the recipient were female, so we were unable to demonstrate chimerism by chromosome studies."},{"key":"ref_11","article-title":"under whose care the child was studied, and Professor R. M. Hardisty for the haematological data. Requests for reprints","author":"Wolff, H.","year":"1970","unstructured":"H. Wolff, under whose care the child was studied, and Professor R. M. Hardisty for the haematological data. Requests for reprints to J.F.S. This case was presented to the Paediatric Section of the Royal Society of Medicine 27 February 1970.","journal-title":"the Paediatric Section of the Royal Society of Medicine; This case was presented to"},{"key":"ref_12","doi-asserted-by":"crossref","first-page":"388","DOI":"10.1016\/S0140-6736(68)90600-4","article-title":"Hazards and potential benefits of blood-transfusion in immunological deficiency","volume":"2","author":"Hong, R.; Gatti, R.A.; Good, R.A.","year":"1968","unstructured":"Hong, R., Gatti, R. A., and Good, R. A. (1968). Hazards and potential benefits of blood-transfusion in immunological deficiency. Lancet, 2, 388.","journal-title":"Lancet"},{"key":"ref_13","doi-asserted-by":"crossref","first-page":"34","DOI":"10.1203\/00006450-196901000-00005","article-title":"Hereditary thymic dysplasia: a graft-versus-host reaction induced by bone marrow cells with a partial 4-a series histocompatibility","volume":"3","author":"Kretschmer, R.; Jeannet, M.; Mereu, T.R.; Kretschmer, K.; Winn, H.; Rosen, F.S.","year":"1969","unstructured":"Kretschmer, R., Jeannet, M., Mereu, T. R., Kretschmer, K., Winn, H. and Rosen, F. S. (1969). Hereditary thymic dysplasia: a graft-versus-host reaction induced by bone marrow cells with a partial 4-a series histocompatibility. Pediatric Research, 3, 34.","journal-title":"Pediatric Research"},{"key":"ref_14","author":"McCullough, J.; Benson, S.J.; Yunis, E.J.; Quie, P.G.","year":"1969","unstructured":"McCullough, J., Benson, S. J., Yunis, E. J., and Quie, P. G. (1969)."},{"key":"ref_15","doi-asserted-by":"crossref","first-page":"730","DOI":"10.1016\/S0022-3476(67)80323-8","article-title":"Thymic dysplasia ('Swiss agammaglobulinemia')","volume":"70","author":"Miller, M.E.","year":"1967","unstructured":"Miller, M. E. (1967). Thymic dysplasia ('Swiss agammaglobulinemia'). Journal of Pediatrics, 70, 730.","journal-title":"Journal of Pediatrics"},{"key":"ref_16","doi-asserted-by":"crossref","first-page":"193","DOI":"10.1136\/jcp.23.3.193","article-title":"Histopathological findings in the combined immunity-deficiency syndrome","volume":"23","author":"Berry, C.L.","year":"1970","unstructured":"Berry, C. L. (1970). Histopathological findings in the combined immunity-deficiency syndrome. Journal of Clinical Pathology, 23, 193.","journal-title":"Journal of Clinical Pathology"},{"key":"ref_17","doi-asserted-by":"crossref","first-page":"172","DOI":"10.1111\/j.1423-0410.1969.tb04731.x","article-title":"Graft versus host reactions in Wiskott-Aldrich syndrome: antemortem diagnosis of human GVH in an munologsc deficiency disease","volume":"16","author":"Douglas, S.D.; Fudenberg, H.H.","year":"1969","unstructured":"Douglas, S. D., and Fudenberg, H. H. (1969). Graft versus host reactions in Wiskott-Aldrich syndrome: antemortem diagnosis of human GVH in an munologsc deficiency disease. Vox Sanguinis, 16, 172.","journal-title":"Vox Sanguinis"},{"key":"ref_18","first-page":"1366","article-title":"Immunological reconstitution of sex-linked lymphopenic immunological deficiency","volume":"2","author":"Gatti, R.A.; Meuwissen, H.J.; Allen, H.D.; Hong, R.; Good, R.A.","year":"1968","unstructured":"Gatti, R. A., Meuwissen, H. J., Allen, H. D., Hong, R., and Good, R. A. (1968). Immunological reconstitution of sex-linked lymphopenic immunological deficiency. Lancet, 2, 1366.","journal-title":"Lancet"},{"key":"ref_19","doi-asserted-by":"crossref","first-page":"953","DOI":"10.1056\/NEJM196510282731803","article-title":"Aplastic anemia, histiocytosis and erythrodermia in immunologically deficient children. Probable human runt disease","volume":"273","author":"Hathaway, W.E.; Githens, J.H.; Blackburn, W.R.; Fulginiti, V.; Kempe, C.H.","year":"1965","unstructured":"Hathaway, W. E., Githens, J. H., Blackburn, W. R., Fulginiti, V., and Kempe, C. H. (1965). Aplastic anemia, histiocytosis and erythrodermia in immunologically deficient children. Probable human runt disease. 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The title was changed by the Editors in the final proof stage, and they apologize for the change in its meaning."}],"container-title":["Archives of Disease in Childhood"],"original-title":[],"language":"en","link":[{"URL":"https:\/\/syndication.highwire.org\/content\/doi\/10.1136\/adc.46.248.571","content-type":"unspecified","content-version":"vor","intended-application":"similarity-checking"}],"deposited":{"date-parts":[[2020,9,26]],"date-time":"2020-09-26T08:55:22Z","timestamp":1601110522000},"score":1,"resource":{"primary":{"URL":"https:\/\/adc.bmj.com\/lookup\/doi\/10.1136\/adc.46.248.571"}},"subtitle":[],"short-title":[],"issued":{"date-parts":[[1971,8,1]]},"references-count":20,"journal-issue":{"issue":"248","published-print":{"date-parts":[[1971,8,1]]}},"URL":"https:\/\/doi.org\/10.1136\/adc.46.248.571","relation":{},"ISSN":["0003-9888","1468-2044"],"issn-type":[{"value":"0003-9888","type":"print"},{"value":"1468-2044","type":"electronic"}],"subject":[],"published":{"date-parts":[[1971,8,1]]}}}